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Items: 1 to 20 of 64

1.

A Comparison between Two Pathophysiologically Different yet Microbiologically Similar Lung Diseases: Cystic Fibrosis and Chronic Obstructive Pulmonary Disease.

Fenker DE, McDaniel CT, Panmanee W, Panos RJ, Sorscher EJ, Sabusap C, Clancy JP, Hassett DJ.

Int J Respir Pulm Med. 2018;5(2). pii: 098. doi: 10.23937/2378-3516/1410098. Epub 2018 Nov 29.

2.

Antisense oligonucleotide eluforsen improves CFTR function in F508del cystic fibrosis.

Sermet-Gaudelus I, Clancy JP, Nichols DP, Nick JA, De Boeck K, Solomon GM, Mall MA, Bolognese J, Bouisset F, den Hollander W, Paquette-Lamontagne N, Tomkinson N, Henig N, Elborn JS, Rowe SM.

J Cyst Fibros. 2018 Nov 19. pii: S1569-1993(18)30914-7. doi: 10.1016/j.jcf.2018.10.015. [Epub ahead of print]

3.

Rapid therapeutic advances in CFTR modulator science.

Clancy JP.

Pediatr Pulmonol. 2018 Nov;53(S3):S4-S11. doi: 10.1002/ppul.24157.

PMID:
30289627
4.

Brushed nasal epithelial cells are a surrogate for bronchial epithelial CFTR studies.

Brewington JJ, Filbrandt ET, LaRosa FJ 3rd, Moncivaiz JD, Ostmann AJ, Strecker LM, Clancy JP.

JCI Insight. 2018 Jul 12;3(13). pii: 99385. doi: 10.1172/jci.insight.99385. [Epub ahead of print]

5.

CFTR modulator theratyping: Current status, gaps and future directions.

Clancy JP, Cotton CU, Donaldson SH, Solomon GM, VanDevanter DR, Boyle MP, Gentzsch M, Nick JA, Illek B, Wallenburg JC, Sorscher EJ, Amaral MD, Beekman JM, Naren AP, Bridges RJ, Thomas PJ, Cutting G, Rowe S, Durmowicz AG, Mense M, Boeck KD, Skach W, Penland C, Joseloff E, Bihler H, Mahoney J, Borowitz D, Tuggle KL.

J Cyst Fibros. 2018 Jun 19. pii: S1569-1993(18)30585-X. doi: 10.1016/j.jcf.2018.05.004. [Epub ahead of print] Review.

6.

Subacute TGFβ expression drives inflammation, goblet cell hyperplasia, and pulmonary function abnormalities in mice with effects dependent on CFTR function.

Kramer EL, Hardie WD, Madala SK, Davidson C, Clancy JP.

Am J Physiol Lung Cell Mol Physiol. 2018 Sep 1;315(3):L456-L465. doi: 10.1152/ajplung.00530.2017. Epub 2018 Jun 7.

PMID:
29877096
7.

Generation of Human Nasal Epithelial Cell Spheroids for Individualized Cystic Fibrosis Transmembrane Conductance Regulator Study.

Brewington JJ, Filbrandt ET, LaRosa FJ 3rd, Moncivaiz JD, Ostmann AJ, Strecker LM, Clancy JP.

J Vis Exp. 2018 Apr 11;(134). doi: 10.3791/57492.

PMID:
29708545
8.

Effects of an Antioxidant-enriched Multivitamin in Cystic Fibrosis. A Randomized, Controlled, Multicenter Clinical Trial.

Sagel SD, Khan U, Jain R, Graff G, Daines CL, Dunitz JM, Borowitz D, Orenstein DM, Abdulhamid I, Noe J, Clancy JP, Slovis B, Rock MJ, McCoy KS, Strausbaugh S, Livingston FR, Papas KA, Shaffer ML.

Am J Respir Crit Care Med. 2018 Sep 1;198(5):639-647. doi: 10.1164/rccm.201801-0105OC.

PMID:
29688760
9.

Early Detection of Rapid Cystic Fibrosis Disease Progression Tailored to Point of Care: A Proof-of-Principle Study.

Szczesniak R, Brokamp C, Su W, McPhail GL, Pestian J, Clancy JP.

Health Innov Point Care Conf. 2017 Nov;2017:204-207. doi: 10.1109/HIC.2017.8227620. Epub 2017 Dec 21.

10.

Joint hierarchical Gaussian process model with application to personalized prediction in medical monitoring.

Duan LL, Wang X, Clancy JP, Szczesniak RD.

Stat (Int Stat Inst). 2018;7(1). pii: e178. doi: 10.1002/sta4.178. Epub 2018 Mar 4.

11.

Personalised CFTR pharmacotherapeutic response testing and therapy of cystic fibrosis.

McCarthy C, Brewington JJ, Harkness B, Clancy JP, Trapnell BC.

Eur Respir J. 2018 Jun 7;51(6). pii: 1702457. doi: 10.1183/13993003.02457-2017. Print 2018 Jun. No abstract available.

PMID:
29563174
12.

Chronic β2AR stimulation limits CFTR activation in human airway epithelia.

Brewington JJ, Backstrom J, Feldman A, Kramer EL, Moncivaiz JD, Ostmann AJ, Zhu X, Lu LJ, Clancy JP.

JCI Insight. 2018 Feb 22;3(4). pii: 93029. doi: 10.1172/jci.insight.93029. [Epub ahead of print]

13.

Assessment of pulmonary structure-function relationships in young children and adolescents with cystic fibrosis by multivolume proton-MRI and CT.

Pennati F, Roach DJ, Clancy JP, Brody AS, Fleck RJ, Aliverti A, Woods JC.

J Magn Reson Imaging. 2018 Aug;48(2):531-542. doi: 10.1002/jmri.25978. Epub 2018 Feb 19.

PMID:
29457316
14.

An update on new and emerging therapies for cystic fibrosis.

Hudock KM, Clancy JP.

Expert Opin Emerg Drugs. 2017 Dec;22(4):331-346. doi: 10.1080/14728214.2017.1418324. Epub 2017 Dec 22. Review.

PMID:
29264936
15.

MicroRNA-145, Cystic Fibrosis Transmembrane Conductance Regulator, and Transforming Growth Factor-β. An (Un)tangled Regulatory Web.

Kramer EL, Clancy JP.

Am J Respir Crit Care Med. 2018 Mar 1;197(5):551-552. doi: 10.1164/rccm.201711-2297ED. No abstract available.

PMID:
29253345
16.

Flexible semiparametric joint modeling: an application to estimate individual lung function decline and risk of pulmonary exacerbations in cystic fibrosis.

Li D, Keogh R, Clancy JP, Szczesniak RD.

Emerg Themes Epidemiol. 2017 Nov 14;14:13. doi: 10.1186/s12982-017-0067-1. eCollection 2017.

17.

TGFβ as a therapeutic target in cystic fibrosis.

Kramer EL, Clancy JP.

Expert Opin Ther Targets. 2018 Feb;22(2):177-189. doi: 10.1080/14728222.2018.1406922. Epub 2017 Dec 13. Review.

PMID:
29168406
18.

Airway microbiota across age and disease spectrum in cystic fibrosis.

Zemanick ET, Wagner BD, Robertson CE, Ahrens RC, Chmiel JF, Clancy JP, Gibson RL, Harris WT, Kurland G, Laguna TA, McColley SA, McCoy K, Retsch-Bogart G, Sobush KT, Zeitlin PL, Stevens MJ, Accurso FJ, Sagel SD, Harris JK.

Eur Respir J. 2017 Nov 16;50(5). pii: 1700832. doi: 10.1183/13993003.00832-2017. Print 2017 Nov.

19.

Guanylate cyclase 2C agonism corrects CFTR mutants.

Arora K, Huang Y, Mun K, Yarlagadda S, Sundaram N, Kessler MM, Hannig G, Kurtz CB, Silos-Santiago I, Helmrath M, Palermo JJ, Clancy JP, Steinbrecher KA, Naren AP.

JCI Insight. 2017 Oct 5;2(19). pii: 93686. doi: 10.1172/jci.insight.93686. [Epub ahead of print]

20.

Take it to the Bank.

Clancy JP, Joseloff E.

J Cyst Fibros. 2017 Sep;16(5):532-533. doi: 10.1016/j.jcf.2017.08.005. No abstract available.

PMID:
28865769

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