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Items: 1 to 20 of 67

1.

Abnormal differentiation of Sandhoff disease model mouse-derived multipotent stem cells toward a neural lineage.

Ogawa Y, Kaizu K, Yanagi Y, Takada S, Sakuraba H, Oishi K.

PLoS One. 2017 Jun 2;12(6):e0178978. doi: 10.1371/journal.pone.0178978. eCollection 2017.

2.

FcRγ-dependent immune activation initiates astrogliosis during the asymptomatic phase of Sandhoff disease model mice.

Ogawa Y, Sano T, Irisa M, Kodama T, Saito T, Furusawa E, Kaizu K, Yanagi Y, Tsukimura T, Togawa T, Yamanaka S, Itoh K, Sakuraba H, Oishi K.

Sci Rep. 2017 Jan 13;7:40518. doi: 10.1038/srep40518.

3.

AAV-mediated gene delivery attenuates neuroinflammation in feline Sandhoff disease.

Bradbury AM, Peterson TA, Gross AL, Wells SZ, McCurdy VJ, Wolfe KG, Dennis JC, Brunson BL, Gray-Edwards H, Randle AN, Johnson AK, Morrison EE, Cox NR, Baker HJ, Sena-Esteves M, Martin DR.

Neuroscience. 2017 Jan 6;340:117-125. doi: 10.1016/j.neuroscience.2016.10.047. Epub 2016 Oct 26.

PMID:
27793778
4.

Suppression of the motor deficit in a mucolipidosis type IV mouse model by bone marrow transplantation.

Walker MT, Montell C.

Hum Mol Genet. 2016 Jul 1;25(13):2752-2761. Epub 2016 Jun 7.

PMID:
27270598
5.

Induction of the type I interferon response in neurological forms of Gaucher disease.

Vitner EB, Farfel-Becker T, Ferreira NS, Leshkowitz D, Sharma P, Lang KS, Futerman AH.

J Neuroinflammation. 2016 May 12;13(1):104. doi: 10.1186/s12974-016-0570-2.

6.

Lipid-laden cells differentially distributed in the aging brain are functionally active and correspond to distinct phenotypes.

Shimabukuro MK, Langhi LG, Cordeiro I, Brito JM, Batista CM, Mattson MP, Mello Coelho Vd.

Sci Rep. 2016 Mar 31;6:23795. doi: 10.1038/srep23795.

7.

Immune-Mediated Inflammation May Contribute to the Pathogenesis of Cardiovascular Disease in Mucopolysaccharidosis Type I.

Khalid O, Vera MU, Gordts PL, Ellinwood NM, Schwartz PH, Dickson PI, Esko JD, Wang RY.

PLoS One. 2016 Mar 17;11(3):e0150850. doi: 10.1371/journal.pone.0150850. eCollection 2016.

8.

TSPO in a murine model of Sandhoff disease: presymptomatic marker of neurodegeneration and disease pathophysiology.

Loth MK, Choi J, McGlothan JL, Pletnikov MV, Pomper MG, Guilarte TR.

Neurobiol Dis. 2016 Jan;85:174-86. doi: 10.1016/j.nbd.2015.11.001. Epub 2015 Nov 3.

9.
10.

Anti-inflammatory Therapy With Simvastatin Improves Neuroinflammation and CNS Function in a Mouse Model of Metachromatic Leukodystrophy.

Stein A, Stroobants S, Gieselmann V, D'Hooge R, Matzner U.

Mol Ther. 2015 Jul;23(7):1160-8. doi: 10.1038/mt.2015.69. Epub 2015 Apr 21.

11.

Ex vivo gene therapy using patient iPSC-derived NSCs reverses pathology in the brain of a homologous mouse model.

Griffin TA, Anderson HC, Wolfe JH.

Stem Cell Reports. 2015 May 12;4(5):835-46. doi: 10.1016/j.stemcr.2015.02.022. Epub 2015 Apr 9.

12.

Neuroinflammation, mitochondrial defects and neurodegeneration in mucopolysaccharidosis III type C mouse model.

Martins C, Hůlková H, Dridi L, Dormoy-Raclet V, Grigoryeva L, Choi Y, Langford-Smith A, Wilkinson FL, Ohmi K, DiCristo G, Hamel E, Ausseil J, Cheillan D, Moreau A, Svobodová E, Hájková Z, Tesařová M, Hansíková H, Bigger BW, Hrebícek M, Pshezhetsky AV.

Brain. 2015 Feb;138(Pt 2):336-55. doi: 10.1093/brain/awu355. Epub 2015 Jan 6. Erratum in: Brain. 2015 Jul;138(Pt 7):e366.

13.

Mesenchymal stem cells as cellular vectors for pediatric neurological disorders.

Phinney DG, Isakova IA.

Brain Res. 2014 Jul 21;1573:92-107. doi: 10.1016/j.brainres.2014.05.029. Epub 2014 May 22. Review.

14.

Pathology and Neurotoxicity in Dogs after Repeat Dose Exposure to a Serotonin 5-HT1B Inhibitor.

Chang JC, Ciaccio P, Schroeder P, Wright L, Westwood R, Berg AL.

J Toxicol Pathol. 2014 Apr;27(1):31-42. doi: 10.1293/tox.2013-0033. Epub 2014 Apr 30.

15.

Severe neurodegeneration with impaired autophagy mechanism triggered by ostm1 deficiency.

Héraud C, Griffiths A, Pandruvada SN, Kilimann MW, Pata M, Vacher J.

J Biol Chem. 2014 May 16;289(20):13912-25. doi: 10.1074/jbc.M113.537233. Epub 2014 Apr 9.

16.

High-resolution magnetic resonance microscopy and diffusion tensor imaging to assess brain structural abnormalities in the murine mucopolysaccharidosis VII model.

Kumar M, Nasrallah IM, Kim S, Ittyerah R, Pickup S, Li J, Parente MK, Wolfe JH, Poptani H.

J Neuropathol Exp Neurol. 2014 Jan;73(1):39-49. doi: 10.1097/NEN.0000000000000023.

17.

Metallothioneins as dynamic markers for brain disease in lysosomal disorders.

Cesani M, Cavalca E, Macco R, Leoncini G, Terreni MR, Lorioli L, Furlan R, Comi G, Doglioni C, Zacchetti D, Sessa M, Scherzer CR, Biffi A.

Ann Neurol. 2014 Jan;75(1):127-37. doi: 10.1002/ana.24053.

18.

Reversibility of neuropathology in Tay-Sachs-related diseases.

Cachón-González MB, Wang SZ, Ziegler R, Cheng SH, Cox TM.

Hum Mol Genet. 2014 Feb 1;23(3):730-48. doi: 10.1093/hmg/ddt459. Epub 2013 Sep 20.

19.

Considerations for the treatment of infantile neuronal ceroid lipofuscinosis (infantile Batten disease).

Sands MS.

J Child Neurol. 2013 Sep;28(9):1151-8. doi: 10.1177/0883073813495960.

20.

Rotenone directly induces BV2 cell activation via the p38 MAPK pathway.

Gao F, Chen D, Hu Q, Wang G.

PLoS One. 2013 Aug 20;8(8):e72046. doi: 10.1371/journal.pone.0072046. eCollection 2013.

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