Format
Sort by
Items per page

Send to

Choose Destination

Links from PubMed

Items: 1 to 20 of 166

1.

White matter injury induced by perinatal exposure to glutaric acid.

Olivera-Bravo S, Isasi E, Fernández A, Rosillo JC, Jiménez M, Casanova G, Sarlabós MN, Barbeito L.

Neurotox Res. 2014 May;25(4):381-91. doi: 10.1007/s12640-013-9445-9. Epub 2013 Dec 3.

PMID:
24297153
2.

Neonatal astrocyte damage is sufficient to trigger progressive striatal degeneration in a rat model of glutaric acidemia-I.

Olivera-Bravo S, Fernández A, Sarlabós MN, Rosillo JC, Casanova G, Jiménez M, Barbeito L.

PLoS One. 2011;6(6):e20831. doi: 10.1371/journal.pone.0020831. Epub 2011 Jun 15.

3.

Disturbance of the glutamatergic system by glutaric acid in striatum and cerebral cortex of glutaryl-CoA dehydrogenase-deficient knockout mice: possible implications for the neuropathology of glutaric acidemia type I.

Busanello EN, Fernandes CG, Martell RV, Lobato VG, Goodman S, Woontner M, de Souza DO, Wajner M.

J Neurol Sci. 2014 Nov 15;346(1-2):260-7. doi: 10.1016/j.jns.2014.09.003. Epub 2014 Sep 16.

PMID:
25241940
4.

Chondroitin sulfate proteoglycans impede myelination by oligodendrocytes after perinatal white matter injury.

Deng YP, Sun Y, Hu L, Li ZH, Xu QM, Pei YL, Huang ZH, Yang ZG, Chen C.

Exp Neurol. 2015 Jul;269:213-23. doi: 10.1016/j.expneurol.2015.03.026. Epub 2015 Apr 8.

PMID:
25862289
5.

Caspase-3 mediates apoptosis of striatal cells in GA I rat model.

Tian F, Fu X, Gao J, Zhang C, Ning Q, Luo X.

J Huazhong Univ Sci Technolog Med Sci. 2012 Feb;32(1):107-12. doi: 10.1007/s11596-012-0019-5. Epub 2012 Jan 27.

PMID:
22282255
6.

Induction of S100B secretion in C6 astroglial cells by the major metabolites accumulating in glutaric acidemia type I.

Quincozes-Santos A, Rosa RB, Leipnitz G, de Souza DF, Seminotti B, Wajner M, Gonçalves CA.

Metab Brain Dis. 2010 Jun;25(2):191-8. doi: 10.1007/s11011-010-9203-0. Epub 2010 May 1.

PMID:
20437086
7.

Glutaric acid and its metabolites cause apoptosis in immature oligodendrocytes: a novel mechanism of white matter degeneration in glutaryl-CoA dehydrogenase deficiency.

Gerstner B, Gratopp A, Marcinkowski M, Sifringer M, Obladen M, Bührer C.

Pediatr Res. 2005 Jun;57(6):771-6. Epub 2005 Mar 17.

PMID:
15774829
8.

Striatal neuronal death mediated by astrocytes from the Gcdh-/- mouse model of glutaric acidemia type I.

Olivera-Bravo S, Ribeiro CA, Isasi E, Trías E, Leipnitz G, Díaz-Amarilla P, Woontner M, Beck C, Goodman SI, Souza D, Wajner M, Barbeito L.

Hum Mol Genet. 2015 Aug 15;24(16):4504-15. doi: 10.1093/hmg/ddv175. Epub 2015 May 12.

PMID:
25968119
10.

Preliminary attempts to establish a rat model of striatal injury in glutaric acidaemia type I.

Funk CB, Prasad AN, Del Bigio MR.

J Inherit Metab Dis. 2004;27(6):819-24.

PMID:
15505387
11.

m-Trifluoromethyl diphenyl diselenide attenuates glutaric acid-induced seizures and oxidative stress in rat pups: involvement of the γ-aminobutyric acidergic system.

Magni DV, Brüning CA, Gai BM, Quines CB, Rosa SG, Fighera MR, Nogueira CW.

J Neurosci Res. 2012 Sep;90(9):1723-31. doi: 10.1002/jnr.23070. Epub 2012 Apr 26.

PMID:
22535575
12.

Biochemical, pathologic and behavioral analysis of a mouse model of glutaric acidemia type I.

Koeller DM, Woontner M, Crnic LS, Kleinschmidt-DeMasters B, Stephens J, Hunt EL, Goodman SI.

Hum Mol Genet. 2002 Feb 15;11(4):347-57.

PMID:
11854167
13.

Ammonium accumulation and cell death in a rat 3D brain cell model of glutaric aciduria type I.

Jafari P, Braissant O, Zavadakova P, Henry H, Bonafé L, Ballhausen D.

PLoS One. 2013;8(1):e53735. doi: 10.1371/journal.pone.0053735. Epub 2013 Jan 10.

14.

Quercetin improves hypoxia-ischemia induced cognitive deficits via promoting remyelination in neonatal rat.

Qu X, Qi D, Dong F, Wang B, Guo R, Luo M, Yao R.

Brain Res. 2014 Mar 17;1553:31-40. doi: 10.1016/j.brainres.2014.01.035. Epub 2014 Jan 28.

PMID:
24480472
15.
17.

Chondroitin sulfate proteoglycans inhibit oligodendrocyte myelination through PTPσ.

Pendleton JC, Shamblott MJ, Gary DS, Belegu V, Hurtado A, Malone ML, McDonald JW.

Exp Neurol. 2013 Sep;247:113-21. doi: 10.1016/j.expneurol.2013.04.003. Epub 2013 Apr 12.

PMID:
23588220
18.

A role of astrocytes in mediating postnatal neurodegeneration in Glutaric acidemia-type 1.

Olivera-Bravo S, Barbeito L.

FEBS Lett. 2015 Nov 14;589(22):3492-7. doi: 10.1016/j.febslet.2015.09.010. Epub 2015 Sep 26. Review.

19.

Striatal degeneration and spongy myelinopathy in glutaric acidemia.

Soffer D, Amir N, Elpeleg ON, Gomori JM, Shalev RS, Gottschalk-Sabag S.

J Neurol Sci. 1992 Feb;107(2):199-204. Review.

PMID:
1564518
20.

Animal models for glutaryl-CoA dehydrogenase deficiency.

Koeller DM, Sauer S, Wajner M, de Mello CF, Goodman SI, Woontner M, Mühlhausen C, Okun JG, Kölker S.

J Inherit Metab Dis. 2004;27(6):813-8.

PMID:
15505386

Supplemental Content

Support Center