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Items: 1 to 20 of 116

1.

Peroxisomal multifunctional protein-2 deficiency causes neuroinflammation and degeneration of Purkinje cells independent of very long chain fatty acid accumulation.

Verheijden S, Bottelbergs A, Krysko O, Krysko DV, Beckers L, De Munter S, Van Veldhoven PP, Wyns S, Kulik W, Nave KA, Ramer MS, Carmeliet P, Kassmann CM, Baes M.

Neurobiol Dis. 2013 Oct;58:258-69. doi: 10.1016/j.nbd.2013.06.006. Epub 2013 Jun 15.

PMID:
23777740
2.

Central nervous system pathology in MFP2 deficiency: insights from general and conditional knockout mouse models.

Verheijden S, Beckers L, De Munter S, Van Veldhoven PP, Baes M.

Biochimie. 2014 Mar;98:119-26. doi: 10.1016/j.biochi.2013.08.009. Epub 2013 Aug 19. Review.

PMID:
23969159
3.

Specific suppression of microgliosis cannot circumvent the severe neuropathology in peroxisomal β-oxidation-deficient mice.

Beckers L, Stroobants S, Verheijden S, West B, D'Hooge R, Baes M.

Mol Cell Neurosci. 2017 Apr;80:123-133. doi: 10.1016/j.mcn.2017.03.004. Epub 2017 Mar 7.

PMID:
28286294
4.

Autonomous Purkinje cell axonal dystrophy causes ataxia in peroxisomal multifunctional protein-2 deficiency.

De Munter S, Bamps D, Malheiro AR, Kumar Baboota R, Brites P, Baes M.

Brain Pathol. 2018 Jan 17. doi: 10.1111/bpa.12586. [Epub ahead of print]

PMID:
29341299
5.

Identification of a chronic non-neurodegenerative microglia activation state in a mouse model of peroxisomal β-oxidation deficiency.

Verheijden S, Beckers L, Casazza A, Butovsky O, Mazzone M, Baes M.

Glia. 2015 Sep;63(9):1606-20. doi: 10.1002/glia.22831. Epub 2015 Apr 2.

PMID:
25846981
6.
7.

Peroxisome deficiency but not the defect in ether lipid synthesis causes activation of the innate immune system and axonal loss in the central nervous system.

Bottelbergs A, Verheijden S, Van Veldhoven PP, Just W, Devos R, Baes M.

J Neuroinflammation. 2012 Mar 29;9:61. doi: 10.1186/1742-2094-9-61.

8.

Early-onset Purkinje cell dysfunction underlies cerebellar ataxia in peroxisomal multifunctional protein-2 deficiency.

De Munter S, Verheijden S, Vanderstuyft E, Malheiro AR, Brites P, Gall D, Schiffmann SN, Baes M.

Neurobiol Dis. 2016 Oct;94:157-68. doi: 10.1016/j.nbd.2016.06.012. Epub 2016 Jun 25.

PMID:
27353294
9.

The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal beta-oxidation.

Baes M, Gressens P, Huyghe S, De NK, Qi C, Jia Y, Mannaerts GP, Evrard P, Van VP, Declercq PE, Reddy JK.

J Neuropathol Exp Neurol. 2002 Apr;61(4):368-74.

PMID:
11939592
10.

Peroxisomal lignoceroyl-CoA ligase deficiency in childhood adrenoleukodystrophy and adrenomyeloneuropathy.

Lazo O, Contreras M, Hashmi M, Stanley W, Irazu C, Singh I.

Proc Natl Acad Sci U S A. 1988 Oct;85(20):7647-51.

11.

Elongation of very long-chain fatty acids is enhanced in X-linked adrenoleukodystrophy.

Kemp S, Valianpour F, Denis S, Ofman R, Sanders RJ, Mooyer P, Barth PG, Wanders RJ.

Mol Genet Metab. 2005 Feb;84(2):144-51. Erratum in: Mol Genet Metab. 2008 Mar;93(3):350.

PMID:
15670720
12.

Combined deficiency of peroxisomal beta-oxidation and ether lipid synthesis in mice causes only minor cortical neuronal migration defects but severe hypotonia.

Krysko O, Bottelbergs A, Van Veldhoven P, Baes M.

Mol Genet Metab. 2010 May;100(1):71-6. doi: 10.1016/j.ymgme.2010.02.003. Epub 2010 Feb 12.

PMID:
20202875
13.

Differential glial activation during the degeneration of Purkinje cells and mitral cells in the PCD mutant mice.

Baltanás FC, Berciano MT, Valero J, Gómez C, Díaz D, Alonso JR, Lafarga M, Weruaga E.

Glia. 2013 Feb;61(2):254-72. doi: 10.1002/glia.22431. Epub 2012 Oct 9.

PMID:
23047288
16.

Neuroinflammation in white matter tracts of Cnp1 mutant mice amplified by a minor brain injury.

Wieser GL, Gerwig UC, Adamcio B, Barrette B, Nave KA, Ehrenreich H, Goebbels S.

Glia. 2013 Jun;61(6):869-80. doi: 10.1002/glia.22480. Epub 2013 Mar 9.

PMID:
23483656
17.
18.

Peroxisomal multifunctional protein 2 is essential for lipid homeostasis in Sertoli cells and male fertility in mice.

Huyghe S, Schmalbruch H, De Gendt K, Verhoeven G, Guillou F, Van Veldhoven PP, Baes M.

Endocrinology. 2006 May;147(5):2228-36. Epub 2006 Feb 16.

PMID:
16484321
19.

Altered constitutive expression of fatty acid-metabolizing enzymes in mice lacking the peroxisome proliferator-activated receptor alpha (PPARalpha).

Aoyama T, Peters JM, Iritani N, Nakajima T, Furihata K, Hashimoto T, Gonzalez FJ.

J Biol Chem. 1998 Mar 6;273(10):5678-84.

20.

Early oxidative damage underlying neurodegeneration in X-adrenoleukodystrophy.

Fourcade S, López-Erauskin J, Galino J, Duval C, Naudi A, Jove M, Kemp S, Villarroya F, Ferrer I, Pamplona R, Portero-Otin M, Pujol A.

Hum Mol Genet. 2008 Jun 15;17(12):1762-73. doi: 10.1093/hmg/ddn085. Epub 2008 Mar 14.

PMID:
18344354

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