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Items: 1 to 20 of 122

1.

Stem cells from wildtype and Friedreich's ataxia mice present similar neuroprotective properties in dorsal root ganglia cells.

Jones J, Estirado A, Redondo C, Martinez S.

PLoS One. 2013 May 9;8(5):e62807. doi: 10.1371/journal.pone.0062807.

2.

Mesenchymal stem cells improve motor functions and decrease neurodegeneration in ataxic mice.

Jones J, Estirado A, Redondo C, Pacheco-Torres J, Sirerol-Piquer MS, Garcia-Verdugo JM, Martinez S.

Mol Ther. 2015 Jan;23(1):130-8. doi: 10.1038/mt.2014.143.

3.

Human adipose stem cell-conditioned medium increases survival of Friedreich's ataxia cells submitted to oxidative stress.

Jones J, Estirado A, Redondo C, Bueno C, Martínez S.

Stem Cells Dev. 2012 Oct 10;21(15):2817-26. doi: 10.1089/scd.2012.0029.

PMID:
22548386
4.

Frataxin deficiency leads to defects in expression of antioxidants and Nrf2 expression in dorsal root ganglia of the Friedreich's ataxia YG8R mouse model.

Shan Y, Schoenfeld RA, Hayashi G, Napoli E, Akiyama T, Iodi Carstens M, Carstens EE, Pook MA, Cortopassi GA.

Antioxid Redox Signal. 2013 Nov 1;19(13):1481-93. doi: 10.1089/ars.2012.4537.

5.

Human mesenchymal stem cells increase anti-oxidant defences in cells derived from patients with Friedreich's ataxia.

Dey R, Kemp K, Gray E, Rice C, Scolding N, Wilkins A.

Cerebellum. 2012 Dec;11(4):861-71. doi: 10.1007/s12311-012-0406-2.

PMID:
22826109
6.

Interferon gamma upregulates frataxin and corrects the functional deficits in a Friedreich ataxia model.

Tomassini B, Arcuri G, Fortuni S, Sandi C, Ezzatizadeh V, Casali C, Condò I, Malisan F, Al-Mahdawi S, Pook M, Testi R.

Hum Mol Genet. 2012 Jul 1;21(13):2855-61. doi: 10.1093/hmg/dds110.

7.

Intrathecal delivery of frataxin mRNA encapsulated in lipid nanoparticles to dorsal root ganglia as a potential therapeutic for Friedreich's ataxia.

Nabhan JF, Wood KM, Rao VP, Morin J, Bhamidipaty S, LaBranche TP, Gooch RL, Bozal F, Bulawa CE, Guild BC.

Sci Rep. 2016 Feb 17;6:20019. doi: 10.1038/srep20019.

8.

Progressive GAA expansions in dorsal root ganglia of Friedreich's ataxia patients.

De Biase I, Rasmussen A, Endres D, Al-Mahdawi S, Monticelli A, Cocozza S, Pook M, Bidichandani SI.

Ann Neurol. 2007 Jan;61(1):55-60.

PMID:
17262846
9.

Mesenchymal stem cells restore frataxin expression and increase hydrogen peroxide scavenging enzymes in Friedreich ataxia fibroblasts.

Kemp K, Mallam E, Hares K, Witherick J, Scolding N, Wilkins A.

PLoS One. 2011;6(10):e26098. doi: 10.1371/journal.pone.0026098.

10.

Neurotrophic function of conditioned medium from human amniotic epithelial cells.

Uchida S, Inanaga Y, Kobayashi M, Hurukawa S, Araie M, Sakuragawa N.

J Neurosci Res. 2000 Nov 15;62(4):585-90.

PMID:
11070502
11.

Stimulating the neurotrophic and angiogenic properties of human adipose-derived stem cells enhances nerve repair.

Kingham PJ, Kolar MK, Novikova LN, Novikov LN, Wiberg M.

Stem Cells Dev. 2014 Apr 1;23(7):741-54. doi: 10.1089/scd.2013.0396.

PMID:
24124760
12.

Neurodegeneration in Friedreich's ataxia: from defective frataxin to oxidative stress.

Gomes CM, Santos R.

Oxid Med Cell Longev. 2013;2013:487534. doi: 10.1155/2013/487534. Review.

13.

Friedreich's ataxia.

Alper G, Narayanan V.

Pediatr Neurol. 2003 May;28(5):335-41. Review.

PMID:
12878293
14.

Frataxin knockdown in human astrocytes triggers cell death and the release of factors that cause neuronal toxicity.

Loría F, Díaz-Nido J.

Neurobiol Dis. 2015 Apr;76:1-12. doi: 10.1016/j.nbd.2014.12.017.

PMID:
25554687
15.

Neurogenesis in postnatal mouse dorsal root ganglia.

Namaka MP, Sawchuk M, MacDonald SC, Jordan LM, Hochman S.

Exp Neurol. 2001 Nov;172(1):60-9.

PMID:
11681840
16.

Novel aberrant genetic and epigenetic events in Friedreich's ataxia.

Quesada MP, Jones J, Rodríguez-Lozano FJ, Moraleda JM, Martinez S.

Exp Cell Res. 2015 Jul 1;335(1):51-61. doi: 10.1016/j.yexcr.2015.04.013.

PMID:
25929520
17.

Frataxin deficiency increases cyclooxygenase 2 and prostaglandins in cell and animal models of Friedreich's ataxia.

Hayashi G, Shen Y, Pedersen TL, Newman JW, Pook M, Cortopassi G.

Hum Mol Genet. 2014 Dec 20;23(25):6838-47. doi: 10.1093/hmg/ddu407.

18.

Functional recovery in a Friedreich's ataxia mouse model by frataxin gene transfer using an HSV-1 amplicon vector.

Lim F, Palomo GM, Mauritz C, Giménez-Cassina A, Illana B, Wandosell F, Díaz-Nido J.

Mol Ther. 2007 Jun;15(6):1072-8.

19.

Glutathione-dependent redox status of frataxin-deficient cells in a yeast model of Friedreich's ataxia.

Auchère F, Santos R, Planamente S, Lesuisse E, Camadro JM.

Hum Mol Genet. 2008 Sep 15;17(18):2790-802. doi: 10.1093/hmg/ddn178.

PMID:
18562474
20.

Mitochondrial pathophysiology in Friedreich's ataxia.

González-Cabo P, Palau F.

J Neurochem. 2013 Aug;126 Suppl 1:53-64. doi: 10.1111/jnc.12303. Review.

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