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Items: 1 to 20 of 112

1.

Canavan disease, a rare early-onset human spongiform leukodystrophy: insights into its genesis and possible clinical interventions.

Baslow MH, Guilfoyle DN.

Biochimie. 2013 Apr;95(4):946-56. doi: 10.1016/j.biochi.2012.10.023. Epub 2012 Nov 11.

PMID:
23151389
2.

Are astrocytes the missing link between lack of brain aspartoacylase activity and the spongiform leukodystrophy in Canavan disease?

Baslow MH, Guilfoyle DN.

Neurochem Res. 2009 Sep;34(9):1523-34. doi: 10.1007/s11064-009-9958-z. Epub 2009 Mar 25.

PMID:
19319678
4.

N-Acetylaspartate Synthase Deficiency Corrects the Myelin Phenotype in a Canavan Disease Mouse Model But Does Not Affect Survival Time.

Maier H, Wang-Eckhardt L, Hartmann D, Gieselmann V, Eckhardt M.

J Neurosci. 2015 Oct 28;35(43):14501-16. doi: 10.1523/JNEUROSCI.1056-15.2015.

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Restoration of aspartoacylase activity in CNS neurons does not ameliorate motor deficits and demyelination in a model of Canavan disease.

Klugmann M, Leichtlein CB, Symes CW, Serikawa T, Young D, During MJ.

Mol Ther. 2005 May;11(5):745-53.

7.

Suppressing N-Acetyl-l-Aspartate Synthesis Prevents Loss of Neurons in a Murine Model of Canavan Leukodystrophy.

Sohn J, Bannerman P, Guo F, Burns T, Miers L, Croteau C, Singhal NK, McDonough JA, Pleasure D.

J Neurosci. 2017 Jan 11;37(2):413-421. doi: 10.1523/JNEUROSCI.2013-16.2016.

8.

Canavan disease: a white matter disorder.

Kumar S, Mattan NS, de Vellis J.

Ment Retard Dev Disabil Res Rev. 2006;12(2):157-65. Review.

PMID:
16807907
9.

The effects of lithium chloride and other substances on levels of brain N-acetyl-L-aspartic acid in Canavan disease-like rats.

Baslow MH, Kitada K, Suckow RF, Hungund BL, Serikawa T.

Neurochem Res. 2002 May;27(5):403-6.

PMID:
12064356
10.

Canavan disease and the role of N-acetylaspartate in myelin synthesis.

Namboodiri AM, Peethambaran A, Mathew R, Sambhu PA, Hershfield J, Moffett JR, Madhavarao CN.

Mol Cell Endocrinol. 2006 Jun 27;252(1-2):216-23. Epub 2006 May 2. Review.

PMID:
16647192
11.

N-Acetylaspartate in the CNS: from neurodiagnostics to neurobiology.

Moffett JR, Ross B, Arun P, Madhavarao CN, Namboodiri AM.

Prog Neurobiol. 2007 Feb;81(2):89-131. Epub 2007 Jan 5. Review.

12.

N-acetylaspartate in the vertebrate brain: metabolism and function.

Baslow MH.

Neurochem Res. 2003 Jun;28(6):941-53. Review.

PMID:
12718449
13.
14.

Canavan disease: a monogenic trait with complex genomic interaction.

Surendran S, Michals-Matalon K, Quast MJ, Tyring SK, Wei J, Ezell EL, Matalon R.

Mol Genet Metab. 2003 Sep-Oct;80(1-2):74-80. Review. Erratum in: Mol Genet Metab. 2006 Mar;87(3):279.

PMID:
14567959
15.
16.

Expression of aspartoacylase activity in cultured rat macroglial cells is limited to oligodendrocytes.

Baslow MH, Suckow RF, Sapirstein V, Hungund BL.

J Mol Neurosci. 1999 Aug-Oct;13(1-2):47-53.

PMID:
10691291
18.

Ablating N-acetylaspartate prevents leukodystrophy in a Canavan disease model.

Guo F, Bannerman P, Mills Ko E, Miers L, Xu J, Burns T, Li S, Freeman E, McDonough JA, Pleasure D.

Ann Neurol. 2015 May;77(5):884-8. doi: 10.1002/ana.24392. Epub 2015 Mar 27.

PMID:
25712859
19.
20.

Atypical MRI findings in Canavan disease: a patient with a mild course.

Yalcinkaya C, Benbir G, Salomons GS, Karaarslan E, Rolland MO, Jakobs C, van der Knaap MS.

Neuropediatrics. 2005 Oct;36(5):336-9.

PMID:
16217711

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