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Items: 1 to 20 of 103

1.

Inhibition of apoptosis blocks human motor neuron cell death in a stem cell model of spinal muscular atrophy.

Sareen D, Ebert AD, Heins BM, McGivern JV, Ornelas L, Svendsen CN.

PLoS One. 2012;7(6):e39113. doi: 10.1371/journal.pone.0039113. Epub 2012 Jun 19.

2.

Established Stem Cell Model of Spinal Muscular Atrophy Is Applicable in the Evaluation of the Efficacy of Thyrotropin-Releasing Hormone Analog.

Ohuchi K, Funato M, Kato Z, Seki J, Kawase C, Tamai Y, Ono Y, Nagahara Y, Noda Y, Kameyama T, Ando S, Tsuruma K, Shimazawa M, Hara H, Kaneko H.

Stem Cells Transl Med. 2016 Feb;5(2):152-63. doi: 10.5966/sctm.2015-0059. Epub 2015 Dec 18.

3.

Modeling the early phenotype at the neuromuscular junction of spinal muscular atrophy using patient-derived iPSCs.

Yoshida M, Kitaoka S, Egawa N, Yamane M, Ikeda R, Tsukita K, Amano N, Watanabe A, Morimoto M, Takahashi J, Hosoi H, Nakahata T, Inoue H, Saito MK.

Stem Cell Reports. 2015 Apr 14;4(4):561-8. doi: 10.1016/j.stemcr.2015.02.010. Epub 2015 Mar 19.

4.

SMN deficiency does not induce oxidative stress in SMA iPSC-derived astrocytes or motor neurons.

Patitucci TN, Ebert AD.

Hum Mol Genet. 2016 Feb 1;25(3):514-23. doi: 10.1093/hmg/ddv489. Epub 2015 Dec 7.

PMID:
26643950
5.

Spinal muscular atrophy patient-derived motor neurons exhibit hyperexcitability.

Liu H, Lu J, Chen H, Du Z, Li XJ, Zhang SC.

Sci Rep. 2015 Jul 20;5:12189. doi: 10.1038/srep12189.

6.

Proteomic assessment of a cell model of spinal muscular atrophy.

Wu CY, Whye D, Glazewski L, Choe L, Kerr D, Lee KH, Mason RW, Wang W.

BMC Neurosci. 2011 Mar 8;12:25. doi: 10.1186/1471-2202-12-25.

7.

Pluripotent stem cell-based models of spinal muscular atrophy.

Frattini E, Ruggieri M, Salani S, Faravelli I, Zanetta C, Nizzardo M, Simone C, Magri F, Corti S.

Mol Cell Neurosci. 2015 Jan;64:44-50. doi: 10.1016/j.mcn.2014.12.005. Epub 2014 Dec 12. Review.

PMID:
25511182
8.

Spinal muscular atrophy phenotype is ameliorated in human motor neurons by SMN increase via different novel RNA therapeutic approaches.

Nizzardo M, Simone C, Dametti S, Salani S, Ulzi G, Pagliarani S, Rizzo F, Frattini E, Pagani F, Bresolin N, Comi G, Corti S.

Sci Rep. 2015 Jun 30;5:11746. doi: 10.1038/srep11746.

9.

Survival motor neuron protein regulates apoptosis in an in vitro model of spinal muscular atrophy.

Parker GC, Li X, Anguelov RA, Toth G, Cristescu A, Acsadi G.

Neurotox Res. 2008 Jan;13(1):39-48.

PMID:
18367439
10.

Survival motor neuron protein in motor neurons determines synaptic integrity in spinal muscular atrophy.

Martinez TL, Kong L, Wang X, Osborne MA, Crowder ME, Van Meerbeke JP, Xu X, Davis C, Wooley J, Goldhamer DJ, Lutz CM, Rich MM, Sumner CJ.

J Neurosci. 2012 Jun 20;32(25):8703-15. doi: 10.1523/JNEUROSCI.0204-12.2012.

11.

SMA Human iPSC-Derived Motor Neurons Show Perturbed Differentiation and Reduced miR-335-5p Expression.

Murdocca M, Ciafrè SA, Spitalieri P, Talarico RV, Sanchez M, Novelli G, Sangiuolo F.

Int J Mol Sci. 2016 Jul 30;17(8). pii: E1231. doi: 10.3390/ijms17081231.

12.

Skeletal muscle DNA damage precedes spinal motor neuron DNA damage in a mouse model of Spinal Muscular Atrophy (SMA).

Fayzullina S, Martin LJ.

PLoS One. 2014 Mar 25;9(3):e93329. doi: 10.1371/journal.pone.0093329. eCollection 2014.

13.

Sensory neurons do not induce motor neuron loss in a human stem cell model of spinal muscular atrophy.

Schwab AJ, Ebert AD.

PLoS One. 2014 Jul 23;9(7):e103112. doi: 10.1371/journal.pone.0103112. eCollection 2014.

14.

Induced pluripotent stem cells from a spinal muscular atrophy patient.

Ebert AD, Yu J, Rose FF Jr, Mattis VB, Lorson CL, Thomson JA, Svendsen CN.

Nature. 2009 Jan 15;457(7227):277-80. doi: 10.1038/nature07677. Epub 2008 Dec 21.

15.

Modeling the phenotype of spinal muscular atrophy by the direct conversion of human fibroblasts to motor neurons.

Zhang QJ, Li JJ, Lin X, Lu YQ, Guo XX, Dong EL, Zhao M, He J, Wang N, Chen WJ.

Oncotarget. 2017 Feb 14;8(7):10945-10953. doi: 10.18632/oncotarget.14641.

16.

Decay in survival motor neuron and plastin 3 levels during differentiation of iPSC-derived human motor neurons.

Boza-Morán MG, Martínez-Hernández R, Bernal S, Wanisch K, Also-Rallo E, Le Heron A, Alías L, Denis C, Girard M, Yee JK, Tizzano EF, Yáñez-Muñoz RJ.

Sci Rep. 2015 Jun 26;5:11696. doi: 10.1038/srep11696.

17.

Restoring Bcl-x(L) levels benefits a mouse model of spinal muscular atrophy.

Tsai LK, Tsai MS, Ting CH, Wang SH, Li H.

Neurobiol Dis. 2008 Sep;31(3):361-7. doi: 10.1016/j.nbd.2008.05.014. Epub 2008 Jun 3.

PMID:
18590823
18.

Increased susceptibility of spinal muscular atrophy fibroblasts to camptothecin-induced cell death.

Wang W, Dimatteo D, Funanage VL, Scavina M.

Mol Genet Metab. 2005 May;85(1):38-45. Epub 2005 Feb 16.

PMID:
15862279
19.

Triptolide increases transcript and protein levels of survival motor neurons in human SMA fibroblasts and improves survival in SMA-like mice.

Hsu YY, Jong YJ, Tsai HH, Tseng YT, An LM, Lo YC.

Br J Pharmacol. 2012 Jun;166(3):1114-26. doi: 10.1111/j.1476-5381.2012.01829.x.

20.

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