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Items: 1 to 20 of 138

1.

An activated immune and inflammatory response targets the pancreas of newborn pigs with cystic fibrosis.

Abu-El-Haija M, Sinkora M, Meyerholz DK, Welsh MJ, McCray PB Jr, Butler J, Uc A.

Pancreatology. 2011;11(5):506-15. doi: 10.1159/000332582. Epub 2011 Nov 1.

2.

Pancreatic damage in fetal and newborn cystic fibrosis pigs involves the activation of inflammatory and remodeling pathways.

Abu-El-Haija M, Ramachandran S, Meyerholz DK, Abu-El-Haija M, Griffin M, Giriyappa RL, Stoltz DA, Welsh MJ, McCray PB Jr, Uc A.

Am J Pathol. 2012 Aug;181(2):499-507. doi: 10.1016/j.ajpath.2012.04.024. Epub 2012 Jun 8.

3.

Optimal complement-mediated phagocytosis of Pseudomonas aeruginosa by monocytes is cystic fibrosis transmembrane conductance regulator-dependent.

Van de Weert-van Leeuwen PB, Van Meegen MA, Speirs JJ, Pals DJ, Rooijakkers SH, Van der Ent CK, Terheggen-Lagro SW, Arets HG, Beekman JM.

Am J Respir Cell Mol Biol. 2013 Sep;49(3):463-70. doi: 10.1165/rcmb.2012-0502OC.

PMID:
23617438
4.

Intestinal CFTR expression alleviates meconium ileus in cystic fibrosis pigs.

Stoltz DA, Rokhlina T, Ernst SE, Pezzulo AA, Ostedgaard LS, Karp PH, Samuel MS, Reznikov LR, Rector MV, Gansemer ND, Bouzek DC, Abou Alaiwa MH, Hoegger MJ, Ludwig PS, Taft PJ, Wallen TJ, Wohlford-Lenane C, McMenimen JD, Chen JH, Bogan KL, Adam RJ, Hornick EE, Nelson GA 4th, Hoffman EA, Chang EH, Zabner J, McCray PB Jr, Prather RS, Meyerholz DK, Welsh MJ.

J Clin Invest. 2013 Jun;123(6):2685-93. doi: 10.1172/JCI68867. Epub 2013 May 8.

5.

Functional activation of the cystic fibrosis trafficking mutant delta F508-CFTR by overexpression.

Cheng SH, Fang SL, Zabner J, Marshall J, Piraino S, Schiavi SC, Jefferson DM, Welsh MJ, Smith AE.

Am J Physiol. 1995 Apr;268(4 Pt 1):L615-24.

PMID:
7733303
6.

Loss of cftr function leads to pancreatic destruction in larval zebrafish.

Navis A, Bagnat M.

Dev Biol. 2015 Mar 15;399(2):237-48. doi: 10.1016/j.ydbio.2014.12.034. Epub 2015 Jan 13.

7.

Sequential targeting of CFTR by BAC vectors generates a novel pig model of cystic fibrosis.

Klymiuk N, Mundhenk L, Kraehe K, Wuensch A, Plog S, Emrich D, Langenmayer MC, Stehr M, Holzinger A, Kröner C, Richter A, Kessler B, Kurome M, Eddicks M, Nagashima H, Heinritzi K, Gruber AD, Wolf E.

J Mol Med (Berl). 2012 May;90(5):597-608. doi: 10.1007/s00109-011-0839-y. Epub 2011 Dec 15.

PMID:
22170306
8.

A novel natural product compound enhances cAMP-regulated chloride conductance of cells expressing CFTR[delta]F508.

deCarvalho AC, Ndi CP, Tsopmo A, Tane P, Ayafor J, Connolly JD, Teem JL.

Mol Med. 2002 Feb;8(2):75-87.

9.

Cystic fibrosis and the innate immune system: therapeutic implications.

Conese M.

Endocr Metab Immune Disord Drug Targets. 2011 Mar;11(1):8-22.

PMID:
21348822
10.

Current concepts of immune dysregulation in cystic fibrosis.

Rieber N, Hector A, Carevic M, Hartl D.

Int J Biochem Cell Biol. 2014 Jul;52:108-12. doi: 10.1016/j.biocel.2014.01.017. Epub 2014 Feb 2. Review.

PMID:
24495876
11.

Disruption of the CFTR gene produces a model of cystic fibrosis in newborn pigs.

Rogers CS, Stoltz DA, Meyerholz DK, Ostedgaard LS, Rokhlina T, Taft PJ, Rogan MP, Pezzulo AA, Karp PH, Itani OA, Kabel AC, Wohlford-Lenane CL, Davis GJ, Hanfland RA, Smith TL, Samuel M, Wax D, Murphy CN, Rieke A, Whitworth K, Uc A, Starner TD, Brogden KA, Shilyansky J, McCray PB Jr, Zabner J, Prather RS, Welsh MJ.

Science. 2008 Sep 26;321(5897):1837-41. doi: 10.1126/science.1163600.

12.

Cystic fibrosis with three mutations in the cystic fibrosis transmembrane conductance regulator gene.

Dörk T, Wulbrand U, Richter T, Neumann T, Wolfes H, Wulf B, Maass G, Tümmler B.

Hum Genet. 1991 Aug;87(4):441-6.

PMID:
1715308
13.

Reduced IL-10 secretion by CD4+ T lymphocytes expressing mutant cystic fibrosis transmembrane conductance regulator (CFTR).

Moss RB, Bocian RC, Hsu YP, Dong YJ, Kemna M, Wei T, Gardner P.

Clin Exp Immunol. 1996 Nov;106(2):374-88.

15.

Cystic fibrosis transmembrane conductance regulator does not affect neutrophil migration across cystic fibrosis airway epithelial monolayers.

Pizurki L, Morris MA, Chanson M, Solomon M, Pavirani A, Bouchardy I, Suter S.

Am J Pathol. 2000 Apr;156(4):1407-16. Erratum in: Am J Pathol 2000 Oct;157(4):1413.

16.

Ontogeny of T lymphocytes and intestinal morphological characteristics in neonatal pigs at different ages in the postnatal period.

Brown DC, Maxwell CV, Erf GF, Davis ME, Singh S, Johnson ZB.

J Anim Sci. 2006 Mar;84(3):567-78.

PMID:
16478948
17.

Expression of delta F508 cystic fibrosis transmembrane conductance regulator protein and related chloride transport properties in the gallbladder epithelium from cystic fibrosis patients.

Dray-Charier N, Paul A, Scoazec JY, Veissière D, Mergey M, Capeau J, Soubrane O, Housset C.

Hepatology. 1999 Jun;29(6):1624-34.

PMID:
10347100
18.

Peripheral decrease and pulmonary homing of CD4+CD45RO+ helper memory T cells in cystic fibrosis.

Häusler M, Schweizer K, Biesterfel S, Opladen T, Heimann G.

Respir Med. 2002 Feb;96(2):87-94.

PMID:
11860174
19.

Innate and Adaptive Immunity in Cystic Fibrosis.

Bruscia EM, Bonfield TL.

Clin Chest Med. 2016 Mar;37(1):17-29. doi: 10.1016/j.ccm.2015.11.010. Epub 2015 Dec 28. Review.

PMID:
26857765
20.

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