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Items: 1 to 20 of 112

1.

Effect of CCS on the accumulation of FALS SOD1 mutant-containing aggregates and on mitochondrial translocation of SOD1 mutants: implication of a free radical hypothesis.

Kim HK, Chung YW, Chock PB, Yim MB.

Arch Biochem Biophys. 2011 May 15;509(2):177-85. doi: 10.1016/j.abb.2011.02.014. Epub 2011 Feb 24.

2.

Stabilization of mutant Cu/Zn superoxide dismutase (SOD1) protein by coexpressed wild SOD1 protein accelerates the disease progression in familial amyotrophic lateral sclerosis mice.

Fukada K, Nagano S, Satoh M, Tohyama C, Nakanishi T, Shimizu A, Yanagihara T, Sakoda S.

Eur J Neurosci. 2001 Dec;14(12):2032-6.

PMID:
11860498
4.

Histological evidence of protein aggregation in mutant SOD1 transgenic mice and in amyotrophic lateral sclerosis neural tissues.

Watanabe M, Dykes-Hoberg M, Culotta VC, Price DL, Wong PC, Rothstein JD.

Neurobiol Dis. 2001 Dec;8(6):933-41.

PMID:
11741389
6.

Different regulation of wild-type and mutant Cu,Zn superoxide dismutase localization in mammalian mitochondria.

Kawamata H, Manfredi G.

Hum Mol Genet. 2008 Nov 1;17(21):3303-17. doi: 10.1093/hmg/ddn226. Epub 2008 Aug 13.

7.

Overexpression of CCS in G93A-SOD1 mice leads to accelerated neurological deficits with severe mitochondrial pathology.

Son M, Puttaparthi K, Kawamata H, Rajendran B, Boyer PJ, Manfredi G, Elliott JL.

Proc Natl Acad Sci U S A. 2007 Apr 3;104(14):6072-7. Epub 2007 Mar 26.

8.

Biological effects of CCS in the absence of SOD1 enzyme activation: implications for disease in a mouse model for ALS.

Proescher JB, Son M, Elliott JL, Culotta VC.

Hum Mol Genet. 2008 Jun 15;17(12):1728-37. doi: 10.1093/hmg/ddn063. Epub 2008 Mar 12.

9.

The copper chaperone CCS directly interacts with copper/zinc superoxide dismutase.

Casareno RL, Waggoner D, Gitlin JD.

J Biol Chem. 1998 Sep 11;273(37):23625-8.

10.

Complete loss of post-translational modifications triggers fibrillar aggregation of SOD1 in the familial form of amyotrophic lateral sclerosis.

Furukawa Y, Kaneko K, Yamanaka K, O'Halloran TV, Nukina N.

J Biol Chem. 2008 Aug 29;283(35):24167-76. doi: 10.1074/jbc.M802083200. Epub 2008 Jun 13.

11.
12.

Mutant SOD1 causes motor neuron disease independent of copper chaperone-mediated copper loading.

Subramaniam JR, Lyons WE, Liu J, Bartnikas TB, Rothstein J, Price DL, Cleveland DW, Gitlin JD, Wong PC.

Nat Neurosci. 2002 Apr;5(4):301-7.

PMID:
11889469
13.

Palmitoylation of superoxide dismutase 1 (SOD1) is increased for familial amyotrophic lateral sclerosis-linked SOD1 mutants.

Antinone SE, Ghadge GD, Lam TT, Wang L, Roos RP, Green WN.

J Biol Chem. 2013 Jul 26;288(30):21606-17. doi: 10.1074/jbc.M113.487231. Epub 2013 Jun 12.

14.

In-cell NMR reveals potential precursor of toxic species from SOD1 fALS mutants.

Luchinat E, Barbieri L, Rubino JT, Kozyreva T, Cantini F, Banci L.

Nat Commun. 2014 Nov 27;5:5502. doi: 10.1038/ncomms6502.

PMID:
25429517
16.
17.

Isolated cytochrome c oxidase deficiency in G93A SOD1 mice overexpressing CCS protein.

Son M, Leary SC, Romain N, Pierrel F, Winge DR, Haller RG, Elliott JL.

J Biol Chem. 2008 May 2;283(18):12267-75. doi: 10.1074/jbc.M708523200. Epub 2008 Mar 11.

18.

Oxidative stress causes abnormal accumulation of familial amyotrophic lateral sclerosis-related mutant SOD1 in transgenic Caenorhabditis elegans.

Oeda T, Shimohama S, Kitagawa N, Kohno R, Imura T, Shibasaki H, Ishii N.

Hum Mol Genet. 2001 Sep 15;10(19):2013-23.

PMID:
11590119
19.

Instability of superoxide dismutase 1 of Drosophila in mutants deficient for its cognate copper chaperone.

Kirby K, Jensen LT, Binnington J, Hilliker AJ, Ulloa J, Culotta VC, Phillips JP.

J Biol Chem. 2008 Dec 19;283(51):35393-401. doi: 10.1074/jbc.M807131200. Epub 2008 Oct 23.

20.

Import, maturation, and function of SOD1 and its copper chaperone CCS in the mitochondrial intermembrane space.

Kawamata H, Manfredi G.

Antioxid Redox Signal. 2010 Nov 1;13(9):1375-84. doi: 10.1089/ars.2010.3212. Review.

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