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Items: 1 to 20 of 175

1.

Cl transport in complemented CF bronchial epithelial cells correlates with CFTR mRNA expression levels.

Illek B, Maurisse R, Wahler L, Kunzelmann K, Fischer H, Gruenert DC.

Cell Physiol Biochem. 2008;22(1-4):57-68. doi: 10.1159/000149783. Epub 2008 Jul 25.

2.

Cystic fibrosis transmembrane conductance regulator-mRNA delivery: a novel alternative for cystic fibrosis gene therapy.

Bangel-Ruland N, Tomczak K, Fernández Fernández E, Leier G, Leciejewski B, Rudolph C, Rosenecker J, Weber WM.

J Gene Med. 2013 Nov-Dec;15(11-12):414-26. doi: 10.1002/jgm.2748.

PMID:
24123772
3.
4.

DeltaF508 CFTR processing correction and activity in polarized airway and non-airway cell monolayers.

Rowe SM, Pyle LC, Jurkevante A, Varga K, Collawn J, Sloane PA, Woodworth B, Mazur M, Fulton J, Fan L, Li Y, Fortenberry J, Sorscher EJ, Clancy JP.

Pulm Pharmacol Ther. 2010 Aug;23(4):268-78. doi: 10.1016/j.pupt.2010.02.001. Epub 2010 Mar 10.

5.

Episomal expression of wild-type CFTR corrects cAMP-dependent chloride transport in respiratory epithelial cells.

Lei DC, Kunzelmann K, Koslowsky T, Yezzi MJ, Escobar LC, Xu Z, Ellison AR, Rommens JM, Tsui L-C, Tykocinski M, Gruenert DC.

Gene Ther. 1996 May;3(5):427-36.

PMID:
9156804
7.

Sensitivity of chloride efflux vs. transepithelial measurements in mixed CF and normal airway epithelial cell populations.

Illek B, Lei D, Fischer H, Gruenert DC.

Cell Physiol Biochem. 2010;26(6):983-90. doi: 10.1159/000324011. Epub 2011 Jan 4.

8.

Paracellular transport through healthy and cystic fibrosis bronchial epithelial cell lines--do we have a proper model?

Molenda N, Urbanova K, Weiser N, Kusche-Vihrog K, Günzel D, Schillers H.

PLoS One. 2014 Jun 19;9(6):e100621. doi: 10.1371/journal.pone.0100621. eCollection 2014.

9.

Pharmacological modulation of ion transport across wild-type and DeltaF508 CFTR-expressing human bronchial epithelia.

Devor DC, Bridges RJ, Pilewski JM.

Am J Physiol Cell Physiol. 2000 Aug;279(2):C461-79.

10.

The effect of ambroxol on chloride transport, CFTR and ENaC in cystic fibrosis airway epithelial cells.

Varelogianni G, Hussain R, Strid H, Oliynyk I, Roomans GM, Johannesson M.

Cell Biol Int. 2013 Nov;37(11):1149-56. doi: 10.1002/cbin.10146. Epub 2013 Jul 23.

PMID:
23765701
11.

Na+/H+ exchanger regulatory factor isoform 1 overexpression modulates cystic fibrosis transmembrane conductance regulator (CFTR) expression and activity in human airway 16HBE14o- cells and rescues DeltaF508 CFTR functional expression in cystic fibrosis cells.

Guerra L, Fanelli T, Favia M, Riccardi SM, Busco G, Cardone RA, Carrabino S, Weinman EJ, Reshkin SJ, Conese M, Casavola V.

J Biol Chem. 2005 Dec 9;280(49):40925-33. Epub 2005 Oct 3.

12.
13.

Tgf-β1 inhibits Cftr biogenesis and prevents functional rescue of ΔF508-Cftr in primary differentiated human bronchial epithelial cells.

Snodgrass SM, Cihil KM, Cornuet PK, Myerburg MM, Swiatecka-Urban A.

PLoS One. 2013 May 9;8(5):e63167. doi: 10.1371/journal.pone.0063167. Print 2013.

14.

A domain mimic increases DeltaF508 CFTR trafficking and restores cAMP-stimulated anion secretion in cystic fibrosis epithelia.

Clarke LL, Gawenis LR, Hwang TC, Walker NM, Gruis DB, Price EM.

Am J Physiol Cell Physiol. 2004 Jul;287(1):C192-9. Epub 2004 Mar 17.

17.

Gene transfer of CFTR to airway epithelia: low levels of expression are sufficient to correct Cl- transport and overexpression can generate basolateral CFTR.

Farmen SL, Karp PH, Ng P, Palmer DJ, Koehler DR, Hu J, Beaudet AL, Zabner J, Welsh MJ.

Am J Physiol Lung Cell Mol Physiol. 2005 Dec;289(6):L1123-30. Epub 2005 Aug 5.

18.

Bioelectric properties of chloride channels in human, pig, ferret, and mouse airway epithelia.

Liu X, Luo M, Zhang L, Ding W, Yan Z, Engelhardt JF.

Am J Respir Cell Mol Biol. 2007 Mar;36(3):313-23. Epub 2006 Sep 28.

19.

Partial correction of endogenous DeltaF508 CFTR in human cystic fibrosis airway epithelia by spliceosome-mediated RNA trans-splicing.

Liu X, Jiang Q, Mansfield SG, Puttaraju M, Zhang Y, Zhou W, Cohn JA, Garcia-Blanco MA, Mitchell LG, Engelhardt JF.

Nat Biotechnol. 2002 Jan;20(1):47-52.

PMID:
11753361
20.

Lack of correlation between CFTR expression, CFTR Cl- currents, amiloride-sensitive Na+ conductance, and cystic fibrosis phenotype.

Beck S, Kühr J, Schütz VV, Seydewitz HH, Brandis M, Greger R, Kunzelmann K.

Pediatr Pulmonol. 1999 Apr;27(4):251-9.

PMID:
10230924

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