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Items: 1 to 20 of 106

1.

Folding of CFTR is predominantly cotranslational.

Kleizen B, van Vlijmen T, de Jonge HR, Braakman I.

Mol Cell. 2005 Oct 28;20(2):277-87.

3.

Correctors promote folding of the CFTR in the endoplasmic reticulum.

Loo TW, Bartlett MC, Clarke DM.

Biochem J. 2008 Jul 1;413(1):29-36. doi: 10.1042/BJ20071690.

PMID:
18361776
5.

Therapeutic approaches to repair defects in deltaF508 CFTR folding and cellular targeting.

Powell K, Zeitlin PL.

Adv Drug Deliv Rev. 2002 Dec 5;54(11):1395-408. Review.

PMID:
12458151
6.

Derlin-1 promotes the efficient degradation of the cystic fibrosis transmembrane conductance regulator (CFTR) and CFTR folding mutants.

Sun F, Zhang R, Gong X, Geng X, Drain PF, Frizzell RA.

J Biol Chem. 2006 Dec 1;281(48):36856-63. Epub 2006 Sep 5.

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The DeltaF508 cystic fibrosis mutation impairs domain-domain interactions and arrests post-translational folding of CFTR.

Du K, Sharma M, Lukacs GL.

Nat Struct Mol Biol. 2005 Jan;12(1):17-25. Epub 2004 Dec 26.

PMID:
15619635
10.

CFTR: new members join the fold.

Skach WR.

Cell. 2006 Nov 17;127(4):673-5.

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Cotranslational ubiquitination of cystic fibrosis transmembrane conductance regulator in vitro.

Sato S, Ward CL, Kopito RR.

J Biol Chem. 1998 Mar 27;273(13):7189-92.

14.

Cystic fibrosis transmembrane conductance regulator as a model substrate to study endoplasmic reticulum protein quality control in mammalian cells.

Younger JM, Fan CY, Chen L, Rosser MF, Patterson C, Cyr DM.

Methods Mol Biol. 2005;301:293-303.

PMID:
15917641
15.

Destabilization of the transmembrane domain induces misfolding in a phenotypic mutant of cystic fibrosis transmembrane conductance regulator.

Choi MY, Partridge AW, Daniels C, Du K, Lukacs GL, Deber CM.

J Biol Chem. 2005 Feb 11;280(6):4968-74. Epub 2004 Nov 10.

16.

Domain interdependence in the biosynthetic assembly of CFTR.

Cui L, Aleksandrov L, Chang XB, Hou YX, He L, Hegedus T, Gentzsch M, Aleksandrov A, Balch WE, Riordan JR.

J Mol Biol. 2007 Jan 26;365(4):981-94. Epub 2006 Nov 10.

PMID:
17113596
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Characterization of the trafficking pathway of cystic fibrosis transmembrane conductance regulator in baby hamster kidney cells.

Okiyoneda T, Harada K, Yamahira K, Wada I, Hashimoto Y, Ueno K, Suico MA, Shuto T, Kai H.

J Pharmacol Sci. 2004 Aug;95(4):471-5. Epub 2004 Jul 31.

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