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Items: 1 to 50 of 59

1.

AVXS-101 (Onasemnogene Abeparvovec) for SMA1: Comparative Study with a Prospective Natural History Cohort.

Al-Zaidy SA, Kolb SJ, Lowes L, Alfano LN, Shell R, Church KR, Nagendran S, Sproule DM, Feltner DE, Wells C, Ogrinc F, Menier M, L'Italien J, Arnold WD, Kissel JT, Kaspar BK, Mendell JR.

J Neuromuscul Dis. 2019;6(3):307-317. doi: 10.3233/JND-190403.

PMID:
31381526
2.

Impact of Age and Motor Function in a Phase 1/2A Study of Infants With SMA Type 1 Receiving Single-Dose Gene Replacement Therapy.

Lowes LP, Alfano LN, Arnold WD, Shell R, Prior TW, McColly M, Lehman KJ, Church K, Sproule DM, Nagendran S, Menier M, Feltner DE, Wells C, Kissel JT, Al-Zaidy S, Mendell J.

Pediatr Neurol. 2019 Sep;98:39-45. doi: 10.1016/j.pediatrneurol.2019.05.005. Epub 2019 May 13.

3.

Health outcomes in spinal muscular atrophy type 1 following AVXS-101 gene replacement therapy.

Al-Zaidy S, Pickard AS, Kotha K, Alfano LN, Lowes L, Paul G, Church K, Lehman K, Sproule DM, Dabbous O, Maru B, Berry K, Arnold WD, Kissel JT, Mendell JR, Shell R.

Pediatr Pulmonol. 2019 Feb;54(2):179-185. doi: 10.1002/ppul.24203. Epub 2018 Dec 12.

4.

Respiratory Management of the Patient With Duchenne Muscular Dystrophy.

Sheehan DW, Birnkrant DJ, Benditt JO, Eagle M, Finder JD, Kissel J, Kravitz RM, Sawnani H, Shell R, Sussman MD, Wolfe LF.

Pediatrics. 2018 Oct;142(Suppl 2):S62-S71. doi: 10.1542/peds.2018-0333H.

5.

Recruitment & retention program for the NeuroNEXT SMA Biomarker Study: Super Babies for SMA!

Bartlett A, Kolb SJ, Kingsley A, Swoboda KJ, Reyna SP, Sakonju A, Darras BT, Shell R, Kuntz N, Castro D, Iannaccone ST, Parsons J, Connolly AM, Chiriboga CA, McDonald C, Burnette WB, Werner K, Thangarajh M, Shieh PB, Finanger E, Coffey CS, Yankey JW, Cudkowicz ME, McGovern MM, McNeil DE, Arnold WD, Kissel JT; NeuroNEXT Clinical Trial Network and on behalf of the NN101 SMA Biomarker Investigators.

Contemp Clin Trials Commun. 2018 Jul 20;11:113-119. doi: 10.1016/j.conctc.2018.07.002. eCollection 2018 Sep.

6.

Low-level expression of EPG5 leads to an attenuated Vici syndrome phenotype.

Waldrop MA, Gumienny F, Boue D, de Los Reyes E, Shell R, Weiss RB, Flanigan KM.

Am J Med Genet A. 2018 May;176(5):1207-1211. doi: 10.1002/ajmg.a.38676.

PMID:
29681093
7.

Natural history of infantile-onset spinal muscular atrophy.

Kolb SJ, Coffey CS, Yankey JW, Krosschell K, Arnold WD, Rutkove SB, Swoboda KJ, Reyna SP, Sakonju A, Darras BT, Shell R, Kuntz N, Castro D, Parsons J, Connolly AM, Chiriboga CA, McDonald C, Burnette WB, Werner K, Thangarajh M, Shieh PB, Finanger E, Cudkowicz ME, McGovern MM, McNeil DE, Finkel R, Iannaccone ST, Kaye E, Kingsley A, Renusch SR, McGovern VL, Wang X, Zaworski PG, Prior TW, Burghes AHM, Bartlett A, Kissel JT; NeuroNEXT Clinical Trial Network on behalf of the NN101 SMA Biomarker Investigators.

Ann Neurol. 2017 Dec;82(6):883-891. doi: 10.1002/ana.25101. Epub 2017 Dec 8.

8.

Single-Dose Gene-Replacement Therapy for Spinal Muscular Atrophy.

Mendell JR, Al-Zaidy S, Shell R, Arnold WD, Rodino-Klapac LR, Prior TW, Lowes L, Alfano L, Berry K, Church K, Kissel JT, Nagendran S, L'Italien J, Sproule DM, Wells C, Cardenas JA, Heitzer MD, Kaspar A, Corcoran S, Braun L, Likhite S, Miranda C, Meyer K, Foust KD, Burghes AHM, Kaspar BK.

N Engl J Med. 2017 Nov 2;377(18):1713-1722. doi: 10.1056/NEJMoa1706198.

9.

Cysteamine-mediated clearance of antibiotic-resistant pathogens in human cystic fibrosis macrophages.

Shrestha CL, Assani KD, Rinehardt H, Albastroiu F, Zhang S, Shell R, Amer AO, Schlesinger LS, Kopp BT.

PLoS One. 2017 Oct 5;12(10):e0186169. doi: 10.1371/journal.pone.0186169. eCollection 2017.

10.

Clinicopathologic Conference: A Newborn With Hypotonia, Cleft Palate, Micrognathia, and Bilateral Club Feet.

Waldrop MA, Boue DR, Sites E, Flanigan KM, Shell R.

Pediatr Neurol. 2017 Sep;74:11-14. doi: 10.1016/j.pediatrneurol.2017.01.026. Epub 2017 Feb 4. No abstract available.

11.

Pretransplant Panel Reactive Antibodies and Lung Transplant Outcomes in Children.

Hayes D Jr, Kopp BT, Sheikh SI, Shell RD, Paul GR, McConnell PI, Tobias JD, Tumin D.

Thorac Cardiovasc Surg. 2017 Jan;65(1):36-42. doi: 10.1055/s-0036-1588058. Epub 2016 Sep 5.

PMID:
27595243
12.

Nonbacterial thrombotic endocarditis: A rare manifestation of gynecologic cancer.

Orfanelli T, Sultanik E, Shell R, Gibbon D.

Gynecol Oncol Rep. 2016 May 31;17:72-4. doi: 10.1016/j.gore.2016.05.010. eCollection 2016 Aug.

13.

Baseline results of the NeuroNEXT spinal muscular atrophy infant biomarker study.

Kolb SJ, Coffey CS, Yankey JW, Krosschell K, Arnold WD, Rutkove SB, Swoboda KJ, Reyna SP, Sakonju A, Darras BT, Shell R, Kuntz N, Castro D, Iannaccone ST, Parsons J, Connolly AM, Chiriboga CA, McDonald C, Burnette WB, Werner K, Thangarajh M, Shieh PB, Finanger E, Cudkowicz ME, McGovern MM, McNeil DE, Finkel R, Kaye E, Kingsley A, Renusch SR, McGovern VL, Wang X, Zaworski PG, Prior TW, Burghes AH, Bartlett A, Kissel JT; NeuroNEXT Clinical Trial Network and on behalf of the NN101 SMA Biomarker Investigators.

Ann Clin Transl Neurol. 2016 Jan 21;3(2):132-45. doi: 10.1002/acn3.283. eCollection 2016 Feb.

14.

Does emotional intelligence predict breaking bad news skills in pediatric interns? A pilot study.

Reed S, Kassis K, Nagel R, Verbeck N, Mahan JD, Shell R.

Med Educ Online. 2015 Aug 17;20:24245. doi: 10.3402/meo.v20.24245. eCollection 2015.

15.

Breaking bad news is a teachable skill in pediatric residents: A feasibility study of an educational intervention.

Reed S, Kassis K, Nagel R, Verbeck N, Mahan JD, Shell R.

Patient Educ Couns. 2015 Jun;98(6):748-52. doi: 10.1016/j.pec.2015.02.015. Epub 2015 Feb 23.

PMID:
25775928
16.

Applying adult learning practices in medical education.

Reed S, Shell R, Kassis K, Tartaglia K, Wallihan R, Smith K, Hurtubise L, Martin B, Ledford C, Bradbury S, Bernstein HH, Mahan JD.

Curr Probl Pediatr Adolesc Health Care. 2014 Jul;44(6):170-81. doi: 10.1016/j.cppeds.2014.01.008. Review.

PMID:
24981666
17.

Decreased right ventricular function in healthy pediatric cystic fibrosis patients versus non-cystic fibrosis patients.

Ozcelik N, Shell R, Holtzlander M, Cua C.

Pediatr Cardiol. 2013 Jan;34(1):159-64. doi: 10.1007/s00246-012-0407-4. Epub 2012 Jun 10.

PMID:
22684194
18.

Master data management: getting your house in order.

Seiler KP, Bodycombe NE, Hawkins T, Shell R, Lemon A, de Souza A, Clemons PA.

Comb Chem High Throughput Screen. 2011 Nov;14(9):749-56.

PMID:
21631416
19.

Application of artificial neural network models in occupational safety and health utilizing ordinal variables.

Moayed FA, Shell RL.

Ann Occup Hyg. 2011 Mar;55(2):132-42. doi: 10.1093/annhyg/meq079. Epub 2010 Dec 27.

PMID:
21187370
20.

Developing the function of 'Magnitude-of-Effect' (MoE) for artificial neural networks to demonstrate the causal effect of exposure variables on outcome variable.

Moayed FA, Shell RL.

Ann Occup Hyg. 2011 Mar;55(2):143-51. doi: 10.1093/annhyg/meq080. Epub 2010 Dec 14.

PMID:
21156728
21.

Randomized trial of biofilm testing to select antibiotics for cystic fibrosis airway infection.

Moskowitz SM, Emerson JC, McNamara S, Shell RD, Orenstein DM, Rosenbluth D, Katz MF, Ahrens R, Hornick D, Joseph PM, Gibson RL, Aitken ML, Benton WW, Burns JL.

Pediatr Pulmonol. 2011 Feb;46(2):184-92. doi: 10.1002/ppul.21350. Epub 2010 Oct 20.

22.

Pediatric bronchoalveolar lavage: practical considerations and future prospects.

Shell R, Nicol K.

Pediatr Dev Pathol. 2010 Jul-Aug;13(4):255-64. doi: 10.2350/09-01-0591-PB.1. Review.

PMID:
19824821
23.

Integrated solution to purification challenges in the manufacture of a soluble recombinant protein in E. coli.

Caparon MH, Rust KJ, Hunter AK, McLaughlin JK, Thomas KE, Herberg JT, Shell RE, Lanter PB, Bishop BF, Dufield RL, Wang X, Ho SV.

Biotechnol Bioeng. 2010 Feb 1;105(2):239-49. doi: 10.1002/bit.22542.

PMID:
19777583
24.

Separation of product associating E. coli host cell proteins OppA and DppA from recombinant apolipoprotein A-I(Milano) in an industrial HIC unit operation.

Hunter AK, Wang X, Suda EJ, Herberg JT, Shell RE, Thomas KE, Dufield RL, Gustafson ME, Mozier NM, Ho SV.

Biotechnol Prog. 2009 Mar-Apr;25(2):446-53. doi: 10.1002/btpr.106.

PMID:
19291803
25.

Neonatal cyanosis due to a novel fetal hemoglobin: Hb F-Circleville [Ggamma63(E7)His-->Leu, CAT>CTT].

Dainer E, Shell R, Miller R, Atkin JF, Pastore M, Kutlar A, Zhuang L, Holley L, Davis DH, Kutlar F.

Hemoglobin. 2008;32(6):596-600. doi: 10.1080/03630260802507915.

PMID:
19065339
26.

Separation of recombinant apolipoprotein A-I(Milano) modified forms and aggregates in an industrial ion-exchange chromatography unit operation.

Hunter AK, Suda EJ, Herberg JT, Thomas KE, Shell RE, Gustafson ME, Ho SV.

J Chromatogr A. 2008 Sep 12;1204(1):42-7. doi: 10.1016/j.chroma.2008.07.059. Epub 2008 Jul 26.

PMID:
18701112
27.

Evaluation of refolding conditions for a human recombinant fusion cytokine protein, promegapoietin-1a.

Boyle DM, Johnson GV, Heeren RA, Shell RE, Banerjee A, Gustafson ME.

Biotechnol Appl Biochem. 2008 Jan;49(Pt 1):73-83.

PMID:
17608622
28.

Theory of planned behaviour predictors of intention to use condoms among Xhosa adolescents in South Africa.

Jemmott JB 3rd, Heeren GA, Ngwane Z, Hewitt N, Jemmott LS, Shell R, O'leary A.

AIDS Care. 2007 May;19(5):677-84.

PMID:
17505930
29.

Impact of denaturation with urea on recombinant apolipoprotein A-IMilano ion-exchange adsorption: equilibrium uptake behavior and protein mass transfer kinetics.

Hunter AK, Suda EJ, Das TK, Shell RE, Herberg JT, Ramasubramanyan N, Gustafson ME, Ho SV.

Biotechnol J. 2007 Jan;2(1):110-20.

PMID:
17136731
30.

Perceived barriers to teaching for critical thinking by BSN nursing faculty.

Shell R.

Nurs Health Care Perspect. 2001 Nov-Dec;22(6):286-91.

PMID:
16370252
31.

Molecular characterization of adeno-associated viruses infecting children.

Chen CL, Jensen RL, Schnepp BC, Connell MJ, Shell R, Sferra TJ, Bartlett JS, Clark KR, Johnson PR.

J Virol. 2005 Dec;79(23):14781-92.

32.

Towards a model of safety climate measurement.

Alhemood AM, Genaidy AM, Shell R, Gunn M, Shoaf C.

Int J Occup Saf Ergon. 2004;10(4):303-18. Review.

PMID:
15598356
33.

Barriers to cancer screening by rural Appalachian primary care providers.

Shell R, Tudiver F.

J Rural Health. 2004 Fall;20(4):368-73.

PMID:
15551854
34.

Teaching and evaluating critical thinking with concept maps.

King M, Shell R.

Nurse Educ. 2002 Sep-Oct;27(5):214-6. No abstract available.

PMID:
12355046
35.

Serum and lower respiratory tract drug concentrations after tobramycin inhalation in young children with cystic fibrosis.

Rosenfeld M, Gibson R, McNamara S, Emerson J, McCoyd KS, Shell R, Borowitz D, Konstan MW, Retsch-Bogart G, Wilmott RW, Burns JL, Vicini P, Montgomery AB, Ramsey B.

J Pediatr. 2001 Oct;139(4):572-7.

PMID:
11598606
36.

Chronic aspiration without gastroesophageal reflux as a cause of chronic respiratory symptoms in neurologically normal infants.

Sheikh S, Allen E, Shell R, Hruschak J, Iram D, Castile R, McCoy K.

Chest. 2001 Oct;120(4):1190-5.

PMID:
11591559
37.

Antidepressant prescribing practices of nurse practitioners.

Shell RC.

Nurse Pract. 2001 Jul;26(7 Pt 1):42-7.

PMID:
11494935
38.

Impact of added rest breaks on the productivity and well being of workers.

Dababneh AJ, Swanson N, Shell RL.

Ergonomics. 2001 Feb 10;44(2):164-74.

PMID:
11209875
39.

Compression of the trachea by the innominate artery in a 2-month-old child.

Shell R, Allen E, Mutabagani K, Long F, Davis JT, McCoy K, Castile R.

Pediatr Pulmonol. 2001 Jan;31(1):80-5.

PMID:
11180679
40.

A phase I study of adenovirus-mediated transfer of the human cystic fibrosis transmembrane conductance regulator gene to a lung segment of individuals with cystic fibrosis.

Zuckerman JB, Robinson CB, McCoy KS, Shell R, Sferra TJ, Chirmule N, Magosin SA, Propert KJ, Brown-Parr EC, Hughes JV, Tazelaar J, Baker C, Goldman MJ, Wilson JM.

Hum Gene Ther. 1999 Dec 10;10(18):2973-85.

PMID:
10609658
41.

Antidepressant prescribing practices of nurse practitioners.

Shell RC, Smith PL, Moody NB.

Clin Excell Nurse Pract. 1998 Sep;2(5):273-8.

PMID:
10455575
42.

The Marianas population decline: 17th century estimates.

Shell RJ.

J Pac Hist. 1999;34(3):291-306. No abstract available.

PMID:
21991635
43.

Children's reactions to the receipt of direct and indirect help.

Shell RM, Eisenberg N.

Child Dev. 1996 Aug;67(4):1391-405.

PMID:
8890490
44.

Use of visual perception in estimating static postural stresses: magnitudes and sources of errors.

Baluyut R, Genaidy AM, Davis LS, Shell RL, Simmons RL.

Ergonomics. 1995 Sep;38(9):1841-50.

PMID:
7671861
45.

Noncompliance in adolescent oral contraceptive users.

Shell R.

Nurse Pract. 1995 Aug;20(8):7, 10. No abstract available.

PMID:
9019693
46.
47.

Ergonomic risk assessment: preliminary guidelines for analysis of repetition, force and posture.

Genaidy AM, al-Shedi AA, Shell RL.

J Hum Ergol (Tokyo). 1993 Jun;22(1):45-55. Review.

PMID:
8064150
48.
49.

Interpreting children's reports of concern about parental drinking: indicators of risk status?

Shell RM, Groppenbacher N, Roosa MW, Gensheimer LK.

Am J Community Psychol. 1992 Aug;20(4):463-89.

PMID:
1481785
50.

A developmental model of recipients' reactions to aid.

Shell RM, Eisenberg N.

Psychol Bull. 1992 May;111(3):413-33. Review.

PMID:
1594719

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