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Items: 1 to 50 of 322

1.

Anti-inflammatories and mucociliary clearance therapies in the age of CFTR modulators.

Perrem L, Ratjen F.

Pediatr Pulmonol. 2019 Nov;54 Suppl 3:S46-S55. doi: 10.1002/ppul.24364. Review.

PMID:
31715088
2.

Antimicrobial resistance in cystic fibrosis: A Delphi approach to defining best practices.

Zemanick E, Burgel PR, Taccetti G, Holmes A, Ratjen F, Byrnes CA, Waters VJ, Bell SC, VanDevanter DR, Stuart Elborn J, Flume PA; Antimicrobial Resistance International Working Group in Cystic Fibrosis.

J Cyst Fibros. 2019 Oct 31. pii: S1569-1993(19)30919-1. doi: 10.1016/j.jcf.2019.10.006. [Epub ahead of print]

PMID:
31680041
3.

Immunoreactive trypsinogen levels in newborn screened infants with an inconclusive diagnosis of cystic fibrosis.

Ooi CY, Sutherland R, Castellani C, Keenan K, Boland M, Reisman J, Bjornson C, Chilvers MA, van Wylick R, Kent S, Price A, Mateos-Corral D, Hughes D, Solomon M, Zuberbuhler P, Brusky J, Durie PR, Ratjen F, Gonska T.

BMC Pediatr. 2019 Oct 22;19(1):369. doi: 10.1186/s12887-019-1756-4.

4.

Long-term effect of CFTR modulator therapy on airway nitric oxide.

Grasemann H, Klingel M, Avolio J, Prentice C, Gonska T, Tullis E, Ratjen F.

Eur Respir J. 2019 Oct 10. pii: 1901113. doi: 10.1183/13993003.01113-2019. [Epub ahead of print] No abstract available.

PMID:
31601715
5.

The future of cystic fibrosis care: a global perspective.

Bell SC, Mall MA, Gutierrez H, Macek M, Madge S, Davies JC, Burgel PR, Tullis E, Castaños C, Castellani C, Byrnes CA, Cathcart F, Chotirmall SH, Cosgriff R, Eichler I, Fajac I, Goss CH, Drevinek P, Farrell PM, Gravelle AM, Havermans T, Mayer-Hamblett N, Kashirskaya N, Kerem E, Mathew JL, McKone EF, Naehrlich L, Nasr SZ, Oates GR, O'Neill C, Pypops U, Raraigh KS, Rowe SM, Southern KW, Sivam S, Stephenson AL, Zampoli M, Ratjen F.

Lancet Respir Med. 2019 Sep 27. pii: S2213-2600(19)30337-6. doi: 10.1016/S2213-2600(19)30337-6. [Epub ahead of print] Review. Erratum in: Lancet Respir Med. 2019 Oct 25;:.

PMID:
31570318
6.

Effect of changes in tidal volume on multiple breath washout outcomes.

Ratjen F, Jensen R, Klingel M, McDonald R, Moore C, Benseler N, Wilson D, Stanojevic S.

PLoS One. 2019 Jul 3;14(7):e0219309. doi: 10.1371/journal.pone.0219309. eCollection 2019.

7.

Proteomic Profiling to Identify Blood Biomarkers Predictive of Response to Azithromycin in Children and Adolescents With Cystic Fibrosis.

Dong K, Singh A, Ng RT, Sin DD, Tebbutt SJ, Ratjen F, Quon BS.

Chest. 2019 Oct;156(4):667-673. doi: 10.1016/j.chest.2019.05.017. Epub 2019 Jun 12.

PMID:
31201785
8.

Inhaled hypertonic saline in preschool children with cystic fibrosis (SHIP): a multicentre, randomised, double-blind, placebo-controlled trial.

Ratjen F, Davis SD, Stanojevic S, Kronmal RA, Hinckley Stukovsky KD, Jorgensen N, Rosenfeld M; SHIP Study Group.

Lancet Respir Med. 2019 Sep;7(9):802-809. doi: 10.1016/S2213-2600(19)30187-0. Epub 2019 Jun 6.

PMID:
31178421
9.

Blood biomarkers to predict short-term pulmonary exacerbation risk in children and adolescents with CF: A pilot study.

Singh A, He M, Chen V, Hollander Z, Tebbutt SJ, Ng RT, McManus BM, Sin DD, Ratjen F, Quon BS.

J Cyst Fibros. 2019 Jun 5. pii: S1569-1993(19)30774-X. doi: 10.1016/j.jcf.2019.05.020. [Epub ahead of print]

PMID:
31176669
10.

Incidence and risk factors of paediatric cystic fibrosis-related diabetes.

Perrem L, Stanojevic S, Solomon M, Carpenter S, Ratjen F.

J Cyst Fibros. 2019 May 6. pii: S1569-1993(19)30074-8. doi: 10.1016/j.jcf.2019.04.015. [Epub ahead of print]

PMID:
31072797
11.

Lavage lipidomics signatures in children with cystic fibrosis and protracted bacterial bronchitis.

Seidl E, Kiermeier H, Liebisch G, Ballmann M, Hesse S, Paul-Buck K, Ratjen F, Rietschel E, Griese M.

J Cyst Fibros. 2019 Apr 24. pii: S1569-1993(18)30860-9. doi: 10.1016/j.jcf.2019.04.012. [Epub ahead of print]

PMID:
31029606
12.

A two-center analysis of hyperpolarized 129Xe lung MRI in stable pediatric cystic fibrosis: Potential as a biomarker for multi-site trials.

Couch MJ, Thomen R, Kanhere N, Hu R, Ratjen F, Woods J, Santyr G.

J Cyst Fibros. 2019 Sep;18(5):728-733. doi: 10.1016/j.jcf.2019.03.005. Epub 2019 Mar 25.

13.

Oral Azithromycin and Response to Pulmonary Exacerbations Treated with Intravenous Tobramycin in Children with Cystic Fibrosis.

Klingel M, Stanojevic S, Tullis E, Ratjen F, Waters V.

Ann Am Thorac Soc. 2019 Jul;16(7):861-867. doi: 10.1513/AnnalsATS.201811-774OC.

PMID:
30874447
14.

Growth of Pulmonary Arteriovenous Malformations in Pediatric Patients with Hereditary Hemorrhagic Telangiectasia.

Ratjen A, Au J, Carpenter S, John P, Ratjen F.

J Pediatr. 2019 May;208:279-281. doi: 10.1016/j.jpeds.2018.12.069. Epub 2019 Mar 8.

PMID:
30853205
15.

Hyperpolarised 129Xe magnetic resonance imaging to monitor treatment response in children with cystic fibrosis.

Rayment JH, Couch MJ, McDonald N, Kanhere N, Manson D, Santyr G, Ratjen F.

Eur Respir J. 2019 May 2;53(5). pii: 1802188. doi: 10.1183/13993003.02188-2018. Print 2019 May.

PMID:
30819815
16.

Does the multiple-breath washout test need to be measured before spirometry?

Au JWY, McDonald R, Stanojevic S, Ratjen F.

ERJ Open Res. 2019 Feb 4;5(1). pii: 00230-2018. doi: 10.1183/23120541.00230-2018. eCollection 2019 Feb.

17.

Lung clearance index is elevated in young children with symptom-controlled asthma.

Racette C, Lu Z, Kowalik K, Cheng O, Bendiak G, Amin R, Dubeau A, Jensen R, Balkovec S, Gustafsson P, Ratjen F, Subbarao P.

Health Sci Rep. 2018 Jun 19;1(8):e58. doi: 10.1002/hsr2.58. eCollection 2018 Aug.

18.

A theory for polymicrogyria and brain arteriovenous malformations in HHT.

Klostranec JM, Chen L, Mathur S, McDonald J, Faughnan ME, Ratjen F, Krings T.

Neurology. 2019 Jan 1;92(1):34-42. doi: 10.1212/WNL.0000000000006686.

PMID:
30584075
19.

Letting It All Out: Neutrophils in Early Cystic Fibrosis Airway Inflammation.

Perrem L, Ratjen F.

Am J Respir Crit Care Med. 2019 Apr 1;199(7):816-817. doi: 10.1164/rccm.201810-1951ED. No abstract available.

20.

Cardiopulmonary Exercise Testing Provides Additional Prognostic Information in Cystic Fibrosis.

Hebestreit H, Hulzebos EHJ, Schneiderman JE, Karila C, Boas SR, Kriemler S, Dwyer T, Sahlberg M, Urquhart DS, Lands LC, Ratjen F, Takken T, Varanistkaya L, Rücker V, Hebestreit A, Usemann J, Radtke T; Prognostic Value of CPET in CF Study Group.

Am J Respir Crit Care Med. 2019 Apr 15;199(8):987-995. doi: 10.1164/rccm.201806-1110OC.

PMID:
30321487
21.

The lung clearance index as a monitoring tool in cystic fibrosis: ready for the clinic?

Perrem L, Rayment JH, Ratjen F.

Curr Opin Pulm Med. 2018 Nov;24(6):579-585. doi: 10.1097/MCP.0000000000000515. Review.

PMID:
30095491
22.

Hyperpolarized Gas Magnetic Resonance Imaging of Pediatric Cystic Fibrosis Lung Disease.

Santyr G, Kanhere N, Morgado F, Rayment JH, Ratjen F, Couch MJ.

Acad Radiol. 2019 Mar;26(3):344-354. doi: 10.1016/j.acra.2018.04.024. Epub 2018 Aug 5.

PMID:
30087066
23.

Epidemiology of Clonal Pseudomonas aeruginosa Infection in a Canadian Cystic Fibrosis Population.

Middleton MA, Layeghifard M, Klingel M, Stanojevic S, Yau YCW, Zlosnik JEA, Coriati A, Ratjen FA, Tullis ED, Stephenson A, Wilcox P, Freitag A, Chilvers M, McKinney M, Lavoie A, Wang PW, Guttman DS, Waters VJ.

Ann Am Thorac Soc. 2018 Jul;15(7):827-836. doi: 10.1513/AnnalsATS.201801-007OC.

PMID:
29911888
24.

Ventilation inhomogeneity in infants with recurrent wheezing.

Lu Z, Foong RE, Kowalik K, Moraes TJ, Boyce A, Dubeau A, Balkovec S, Gustafsson PM, Becker AB, Mandhane PJ, Turvey SE, Lou W, Ratjen F, Sears M, Subbarao P.

Thorax. 2018 Oct;73(10):936-941. doi: 10.1136/thoraxjnl-2017-211351. Epub 2018 Jun 15.

PMID:
29907664
25.

Reference equations for the interpretation of forced expiratory and plethysmographic measurements in infants.

Lu Z, Foong RE, Kowalik K, Moraes TJ, Dubeau A, Lefebvre D, Davis SD, Balkovec S, Becker A, Mandhane P, Turvey SE, Lou W, Sears MR, Ratjen F, Subbarao P.

Pediatr Pulmonol. 2018 Jul;53(7):907-916. doi: 10.1002/ppul.24063. Epub 2018 May 23.

PMID:
29790670
26.

Eradication of early P. aeruginosa infection in children <7 years of age with cystic fibrosis: The early study.

Ratjen F, Moeller A, McKinney ML, Asherova I, Alon N, Maykut R, Angyalosi G; EARLY study group.

J Cyst Fibros. 2019 Jan;18(1):78-85. doi: 10.1016/j.jcf.2018.04.002. Epub 2018 Apr 21.

PMID:
29685813
27.

The CF Canada-Sick Kids Program in individual CF therapy: A resource for the advancement of personalized medicine in CF.

Eckford PDW, McCormack J, Munsie L, He G, Stanojevic S, Pereira SL, Ho K, Avolio J, Bartlett C, Yang JY, Wong AP, Wellhauser L, Huan LJ, Jiang JX, Ouyang H, Du K, Klingel M, Kyriakopoulou L, Gonska T, Moraes TJ, Strug LJ, Rossant J, Ratjen F, Bear CE.

J Cyst Fibros. 2019 Jan;18(1):35-43. doi: 10.1016/j.jcf.2018.03.013. Epub 2018 Oct 10.

28.

Changes in Lung Clearance Index in Preschool-aged Patients with Cystic Fibrosis Treated with Ivacaftor (GOAL): A Clinical Trial.

Ratjen F, Klingel M, Black P, Powers MR, Grasemann H, Solomon M, Sagel SD, Donaldson SH, Rowe SM, Rosenfeld M.

Am J Respir Crit Care Med. 2018 Aug 15;198(4):526-528. doi: 10.1164/rccm.201802-0243LE. No abstract available.

29.

Early detection using qPCR of Pseudomonas aeruginosa infection in children with cystic fibrosis undergoing eradication treatment.

Blanchard AC, Rooney AM, Yau Y, Zhang Y, Stapleton PJ, Horton E, Klingel M, Stanojevic S, Ratjen F, Coburn B, Waters V.

J Cyst Fibros. 2018 Nov;17(6):723-728. doi: 10.1016/j.jcf.2018.02.008. Epub 2018 Mar 7.

PMID:
29525410
30.

ECFS best practice guidelines: the 2018 revision.

Castellani C, Duff AJA, Bell SC, Heijerman HGM, Munck A, Ratjen F, Sermet-Gaudelus I, Southern KW, Barben J, Flume PA, Hodková P, Kashirskaya N, Kirszenbaum MN, Madge S, Oxley H, Plant B, Schwarzenberg SJ, Smyth AR, Taccetti G, Wagner TOF, Wolfe SP, Drevinek P.

J Cyst Fibros. 2018 Mar;17(2):153-178. doi: 10.1016/j.jcf.2018.02.006. Epub 2018 Mar 3. Review.

31.

Preschool Multiple-Breath Washout Testing. An Official American Thoracic Society Technical Statement.

Robinson PD, Latzin P, Ramsey KA, Stanojevic S, Aurora P, Davis SD, Gappa M, Hall GL, Horsley A, Jensen R, Lum S, Milla C, Nielsen KG, Pittman JE, Rosenfeld M, Singer F, Subbarao P, Gustafsson PM, Ratjen F; ATS Assembly on Pediatrics.

Am J Respir Crit Care Med. 2018 Mar 1;197(5):e1-e19. doi: 10.1164/rccm.201801-0074ST.

PMID:
29493315
32.

Comparison of facemask and mouthpiece interfaces for multiple breath washout measurements.

Robinson PD, Lum S, Moore C, Hardaker KM, Benseler N, Aurora P, Cooper P, Fitzgerald D, Jensen R, McDonald R, Selvadurai H, Ratjen F, Stanojevic S.

J Cyst Fibros. 2018 Jul;17(4):511-517. doi: 10.1016/j.jcf.2018.01.003. Epub 2018 Mar 2.

PMID:
29483003
33.

Lung clearance index to monitor treatment response in pulmonary exacerbations in preschool children with cystic fibrosis.

Rayment JH, Stanojevic S, Davis SD, Retsch-Bogart G, Ratjen F.

Thorax. 2018 May;73(5):451-458. doi: 10.1136/thoraxjnl-2017-210979. Epub 2018 Feb 15.

PMID:
29449440
34.

The effects of 100% oxygen on breathing pattern are not limited to young children.

Moore C, Horton E, Benseler N, Jensen R, Ratjen F.

Eur Respir J. 2018 Jan 4;51(1). pii: 1702055. doi: 10.1183/13993003.02055-2017. Print 2018 Jan. No abstract available.

35.

Echocardiography Grading for Pulmonary Arteriovenous Malformation Screening in Children with Hereditary Hemorrhagic Telangiectasia.

Fernandopulle N, Mertens L, Klingel M, Manson D, Ratjen F.

J Pediatr. 2018 Apr;195:288-291.e1. doi: 10.1016/j.jpeds.2017.11.047. Epub 2017 Dec 20.

PMID:
29274888
36.

CFTR Genotype and Maximal Exercise Capacity in Cystic Fibrosis: A Cross-sectional Study.

Radtke T, Hebestreit H, Gallati S, Schneiderman JE, Braun J, Stevens D, Hulzebos EH, Takken T, Boas SR, Urquhart DS, Lands LC, Tejero S, Sovtic A, Dwyer T, Petrovic M, Harris RA, Karila C, Savi D, Usemann J, Mei-Zahav M, Hatziagorou E, Ratjen F, Kriemler S; CFTR-Exercise study group.

Ann Am Thorac Soc. 2018 Feb;15(2):209-216. doi: 10.1513/AnnalsATS.201707-570OC. Epub 2017 Nov 15.

37.

Elucidating progression of early cystic fibrosis lung disease.

Ramsey K, Ratjen F, Latzin P.

Eur Respir J. 2017 Nov 9;50(5). pii: 1701916. doi: 10.1183/13993003.01916-2017. Print 2017 Nov. No abstract available.

38.

False-Positive Newborn Screening for Cystic Fibrosis and Health Care Use.

Hayeems RZ, Miller FA, Vermeulen M, Potter BK, Chakraborty P, Davies C, Carroll JC, Ratjen F, Guttmann A.

Pediatrics. 2017 Nov;140(5). pii: e20170604. doi: 10.1542/peds.2017-0604. Epub 2017 Oct 12.

39.

Correcting for tissue nitrogen excretion in multiple breath washout measurements.

Kane M, Rayment JH, Jensen R, McDonald R, Stanojevic S, Ratjen F.

PLoS One. 2017 Oct 11;12(10):e0185553. doi: 10.1371/journal.pone.0185553. eCollection 2017.

40.

Inter-test reproducibility of the lung clearance index measured by multiple breath washout.

Oude Engberink E, Ratjen F, Davis SD, Retsch-Bogart G, Amin R, Stanojevic S.

Eur Respir J. 2017 Oct 5;50(4). pii: 1700433. doi: 10.1183/13993003.00433-2017. Print 2017 Oct.

41.

Standard versus biofilm antimicrobial susceptibility testing to guide antibiotic therapy in cystic fibrosis.

Waters V, Ratjen F.

Cochrane Database Syst Rev. 2017 Oct 5;10:CD009528. doi: 10.1002/14651858.CD009528.pub4. Review.

42.

Another Brick in the Wall: Lung Clearance Index and Lower Airways Pathology in Preschool Cystic Fibrosis.

Rayment JH, Ratjen F.

Ann Am Thorac Soc. 2017 Sep;14(9):1389-1390. doi: 10.1513/AnnalsATS.201706-432ED. No abstract available.

PMID:
28862497
43.

Changes in magnetic resonance imaging scores and ventilation inhomogeneity in children with cystic fibrosis pulmonary exacerbations.

Grasemann H, Ciet P, Amin R, McDonald N, Klingel M, Tiddens HAWM, Ratjen F, Grosse-Wortmann L.

Eur Respir J. 2017 Aug 24;50(2). pii: 1700244. doi: 10.1183/13993003.00244-2017. Print 2017 Aug. No abstract available.

44.

Reply to Verbanck and Vanderhelst: The Respective Roles of Lung Clearance Index and Magnetic Resonance Imaging in the Clinical Management of Patients with Cystic Fibrosis.

Kanhere N, Couch MJ, Rayment JH, Ratjen F, Santyr G; all authors.

Am J Respir Crit Care Med. 2018 Feb 1;197(3):411-412. doi: 10.1164/rccm.201707-1392LE. No abstract available.

PMID:
28800249
45.

Chronic Hypoxemia in a 2-Year-Old Boy.

Rayment JH, Ahmareen O, John PR, Ratjen F.

Ann Am Thorac Soc. 2017 Aug;14(8):1348-1352. doi: 10.1513/AnnalsATS.201701-069CC. No abstract available.

PMID:
28763268
46.

Orkambi® and amplifier co-therapy improves function from a rare CFTR mutation in gene-edited cells and patient tissue.

Molinski SV, Ahmadi S, Ip W, Ouyang H, Villella A, Miller JP, Lee PS, Kulleperuma K, Du K, Di Paola M, Eckford PD, Laselva O, Huan LJ, Wellhauser L, Li E, Ray PN, Pomès R, Moraes TJ, Gonska T, Ratjen F, Bear CE.

EMBO Mol Med. 2017 Sep;9(9):1224-1243. doi: 10.15252/emmm.201607137.

47.

Phenotypic profiling of CFTR modulators in patient-derived respiratory epithelia.

Ahmadi S, Bozoky Z, Di Paola M, Xia S, Li C, Wong AP, Wellhauser L, Molinski SV, Ip W, Ouyang H, Avolio J, Forman-Kay JD, Ratjen F, Hirota JA, Rommens J, Rossant J, Gonska T, Moraes TJ, Bear CE.

NPJ Genom Med. 2017 Apr 14;2:12. doi: 10.1038/s41525-017-0015-6.

48.

Intrapleural Dornase and Tissue Plasminogen Activator in pediatric empyema (DTPA): a study protocol for a randomized controlled trial.

Livingston MH, Mahant S, Ratjen F, Connolly BL, Thorpe K, Mamdani M, Maclusky I, Laberge S, Giglia L, Walton JM, Yang CL, Roberts A, Shawyer AC, Brindle M, Parsons SJ, Stoian CA, Cohen E.

Trials. 2017 Jun 24;18(1):293. doi: 10.1186/s13063-017-2026-0.

49.

Combination antimicrobial susceptibility testing for acute exacerbations in chronic infection of Pseudomonas aeruginosa in cystic fibrosis.

Waters V, Ratjen F.

Cochrane Database Syst Rev. 2017 Jun 19;6:CD006961. doi: 10.1002/14651858.CD006961.pub4. Review.

50.

Efficacy and safety of lumacaftor and ivacaftor in patients aged 6-11 years with cystic fibrosis homozygous for F508del-CFTR: a randomised, placebo-controlled phase 3 trial.

Ratjen F, Hug C, Marigowda G, Tian S, Huang X, Stanojevic S, Milla CE, Robinson PD, Waltz D, Davies JC; VX14-809-109 investigator group.

Lancet Respir Med. 2017 Jul;5(7):557-567. doi: 10.1016/S2213-2600(17)30215-1. Epub 2017 Jun 9. Erratum in: Lancet Respir Med. 2017 Aug;5(8):e28.

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