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Items: 38


A novel missense mutation in a leucine-rich repeat of GPIbα in a Bernard-Soulier variant reduces shear-dependent adherence on von Willebrand factor.

Proulle V, Strassel C, Perrault C, Baas MJ, Moog S, Mangin P, Nurden P, Nurden A, Adam F, Bryckaert M, Kauskot A, Li R, Lanza F.

Br J Haematol. 2019 Jul 1. doi: 10.1111/bjh.16068. [Epub ahead of print] No abstract available.


FVIII dosages in persons with haemophilia A treated with extended half-life products: From local biology to optimized patient management.

Perrier-Cornet A, Philippe A, Lambert T, d'Oiron R, Rafowicz A, Lavenu-Bombled C, Combe S, Gillibert A, Proulle V.

Haemophilia. 2019 Jun 17. doi: 10.1111/hae.13801. [Epub ahead of print] No abstract available.


Relevance of platelet desialylation and thrombocytopenia in type 2B von Willebrand disease: preclinical and clinical evidence.

Dupont A, Soukaseum C, Cheptou M, Adam F, Nipoti T, Lourenco-Rodrigues MD, Legendre P, Proulle V, Rauch A, Kawecki C, Bryckaert M, Rosa JP, Paris C, Ternisien C, Boisseau P, Goudemand J, Borgel D, Lasne D, Maurice P, Lenting PJ, Denis CV, Susen S, Kauskot A.

Haematologica. 2019 Feb 28. pii: haematol.2018.206250. doi: 10.3324/haematol.2018.206250. [Epub ahead of print]


Factor VIII assays in treated hemophilia A patients.

Lasne D, Pouplard C, Nougier C, Eschwege V, Le Cam Duchez V, Proulle V, Smahi M, Harzallah I, Voisin S, Toulon P, Sobas F, Galinat H, Flaujac C, Ternisien C, Jeanpierre E; groupe d'études de la biologie des maladies hémorragiques du Groupe français d'études de l'hémostase et la thrombose.

Ann Biol Clin (Paris). 2019 Feb 1;77(1):53-65. doi: 10.1684/abc.2019.1413. Review.


Factor IX assays in treated hemophilia B patients.

Pouplard C, Jeanpierre E, Lasne D, Le Cam Duchez V, Eschwege V, Flaujac C, Galinat H, Harzallah I, Proulle V, Smahi M, Sobas F, Ternisien C, Toulon P, Voisin S, Nougier C; groupe d’études de la biologie des maladies hémorragiques du Groupe français d’études de l’hémostase et la thrombose.

Ann Biol Clin (Paris). 2019 Feb 1;77(1):41-52. doi: 10.1684/abc.2019.1414. Review.


Clinical and biological features in PIEZO1-hereditary xerocytosis and Gardos channelopathy: a retrospective series of 126 patients.

Picard V, Guitton C, Thuret I, Rose C, Bendelac L, Ghazal K, Aguilar-Martinez P, Badens C, Barro C, Bénéteau C, Berger C, Cathébras P, Deconinck E, Delaunay J, Durand JM, Firah N, Galactéros F, Godeau B, Jaïs X, de Jaureguiberry JP, Le Stradic C, Lifermann F, Maffre R, Morin G, Perrin J, Proulle V, Ruivard M, Toutain F, Lahary A, Garçon L.

Haematologica. 2019 Aug;104(8):1554-1564. doi: 10.3324/haematol.2018.205328. Epub 2019 Jan 17.


A factor VIII-nanobody fusion protein forming an ultrastable complex with VWF: effect on clearance and antibody formation.

Muczynski V, Casari C, Moreau F, Aymé G, Kawecki C, Legendre P, Proulle V, Christophe OD, Denis CV, Lenting PJ.

Blood. 2018 Sep 13;132(11):1193-1197. doi: 10.1182/blood-2018-01-829523. Epub 2018 Jul 31.


Macrophage scavenger receptor SR-AI contributes to the clearance of von Willebrand factor.

Wohner N, Muczynski V, Mohamadi A, Legendre P, Proulle V, Aymé G, Christophe OD, Lenting PJ, Denis CV, Casari C.

Haematologica. 2018 Apr;103(4):728-737. doi: 10.3324/haematol.2017.175216. Epub 2018 Jan 11.


A Novel Single-Domain Antibody Against von Willebrand Factor A1 Domain Resolves Leukocyte Recruitment and Vascular Leakage During Inflammation-Brief Report.

Aymé G, Adam F, Legendre P, Bazaa A, Proulle V, Denis CV, Christophe OD, Lenting PJ.

Arterioscler Thromb Vasc Biol. 2017 Sep;37(9):1736-1740. doi: 10.1161/ATVBAHA.117.309319. Epub 2017 Jun 22.


Red blood cell Gardos channel (KCNN4): the essential determinant of erythrocyte dehydration in hereditary xerocytosis.

Rapetti-Mauss R, Picard V, Guitton C, Ghazal K, Proulle V, Badens C, Soriani O, Garçon L, Guizouarn H.

Haematologica. 2017 Oct;102(10):e415-e418. doi: 10.3324/haematol.2017.171389. Epub 2017 Jun 15. No abstract available.


Soluble Siglec-5 associates to PSGL-1 and displays anti-inflammatory activity.

Pepin M, Mezouar S, Pegon J, Muczynski V, Adam F, Bianchini EP, Bazaa A, Proulle V, Rupin A, Paysant J, Panicot-Dubois L, Christophe OD, Dubois C, Lenting PJ, Denis CV.

Sci Rep. 2016 Nov 28;6:37953. doi: 10.1038/srep37953.


LDL receptor-related protein 1 contributes to the clearance of the activated factor VII-antithrombin complex.

Fazavana JG, Muczynski V, Proulle V, Wohner N, Christophe OD, Lenting PJ, Denis CV.

J Thromb Haemost. 2016 Dec;14(12):2458-2470. doi: 10.1111/jth.13502. Epub 2016 Oct 25.


LIM kinase/cofilin dysregulation promotes macrothrombocytopenia in severe von Willebrand disease-type 2B.

Kauskot A, Poirault-Chassac S, Adam F, Muczynski V, Aymé G, Casari C, Bordet JC, Soukaseum C, Rothschild C, Proulle V, Pietrzyk-Nivau A, Berrou E, Christophe OD, Rosa JP, Lenting PJ, Bryckaert M, Denis CV, Baruch D.

JCI Insight. 2016 Oct 6;1(16):e88643. doi: 10.1172/jci.insight.88643.


A specific plasminogen activator inhibitor-1 antagonist derived from inactivated urokinase.

Gong L, Proulle V, Fang C, Hong Z, Lin Z, Liu M, Xue G, Yuan C, Lin L, Furie B, Flaumenhaft R, Andreasen P, Furie B, Huang M.

J Cell Mol Med. 2016 Oct;20(10):1851-60. doi: 10.1111/jcmm.12875. Epub 2016 May 20.


Risk factors for thrombosis in an african population.

Fall AO, Proulle V, Sall A, Mbaye A, Ba PS, Diao M, Seck M, Gadji M, Gning SB, Diop S, Dièye TN, Faye BF, Thiam D, Dreyfus M.

Clin Med Insights Blood Disord. 2014 Apr 10;7:1-6. doi: 10.4137/CMBD.S13401. eCollection 2014.


Underestimation of unfractionated heparin therapy assessment due to platelet activation when using partial-draw (pediatric) citrate collection tubes.

Desconclois C, Eschwège V, Proulle V, Boutekedjiret T, Dreyfus M, Toulon P.

Thromb Res. 2014 Nov;134(5):1117-22. doi: 10.1016/j.thromres.2014.08.012. Epub 2014 Aug 27.


Spectrum of the mutations in Bernard-Soulier syndrome.

Savoia A, Kunishima S, De Rocco D, Zieger B, Rand ML, Pujol-Moix N, Caliskan U, Tokgoz H, Pecci A, Noris P, Srivastava A, Ward C, Morel-Kopp MC, Alessi MC, Bellucci S, Beurrier P, de Maistre E, Favier R, Hézard N, Hurtaud-Roux MF, Latger-Cannard V, Lavenu-Bombled C, Proulle V, Meunier S, Négrier C, Nurden A, Randrianaivo H, Fabris F, Platokouki H, Rosenberg N, HadjKacem B, Heller PG, Karimi M, Balduini CL, Pastore A, Lanza F.

Hum Mutat. 2014 Sep;35(9):1033-45. doi: 10.1002/humu.22607. Epub 2014 Jul 15. Review.


Platelets are required for enhanced activation of the endothelium and fibrinogen in a mouse thrombosis model of APS.

Proulle V, Furie RA, Merrill-Skoloff G, Furie BC, Furie B.

Blood. 2014 Jul 24;124(4):611-22. doi: 10.1182/blood-2014-02-554980. Epub 2014 May 13.


Multiplate whole blood impedance aggregometry: a new tool for von Willebrand disease.

Valarche V, Desconclois C, Boutekedjiret T, Dreyfus M, Proulle V.

J Thromb Haemost. 2011 Aug;9(8):1645-7. doi: 10.1111/j.1538-7836.2011.04400.x. No abstract available.


β₂-Glycoprotein-1 autoantibodies from patients with antiphospholipid syndrome are sufficient to potentiate arterial thrombus formation in a mouse model.

Arad A, Proulle V, Furie RA, Furie BC, Furie B.

Blood. 2011 Mar 24;117(12):3453-9. doi: 10.1182/blood-2010-08-300715. Epub 2011 Jan 18.


Heparin-induced thrombocytopenia: successful biological and clinical management with lepirudin despite severe renal impairment.

Desconclois C, Ract C, Boutekedjiret T, Alhenc-Gelas M, Duranteau J, Dreyfus M, Proulle V.

Thromb Haemost. 2011 Mar;105(3):568-9. doi: 10.1160/TH10-07-0495. Epub 2011 Jan 12. No abstract available.


Increased levels of circulating microparticles in primary Sjögren's syndrome, systemic lupus erythematosus and rheumatoid arthritis and relation with disease activity.

Sellam J, Proulle V, Jüngel A, Ittah M, Miceli Richard C, Gottenberg JE, Toti F, Benessiano J, Gay S, Freyssinet JM, Mariette X.

Arthritis Res Ther. 2009;11(5):R156. doi: 10.1186/ar2833. Epub 2009 Oct 15.


Thromboxane synthase mutations in an increased bone density disorder (Ghosal syndrome).

Geneviève D, Proulle V, Isidor B, Bellais S, Serre V, Djouadi F, Picard C, Vignon-Savoye C, Bader-Meunier B, Blanche S, de Vernejoul MC, Legeai-Mallet L, Fischer AM, Le Merrer M, Dreyfus M, Gaussem P, Munnich A, Cormier-Daire V.

Nat Genet. 2008 Mar;40(3):284-6. doi: 10.1038/ng.2007.66. Epub 2008 Feb 10.


Detection of 95 novel mutations in coagulation factor VIII gene F8 responsible for hemophilia A: results from a single institution.

Guillet B, Lambert T, d'Oiron R, Proulle V, Plantier JL, Rafowicz A, Peynet J, Costa JM, Bendelac L, Laurian Y, Lavergne JM.

Hum Mutat. 2006 Jul;27(7):676-85.


Circulating microparticles are elevated in haemophiliacs and non-haemophilic individuals aged <18 years.

Proulle V, Hugel B, Guillet B, Grunebaum L, Lambert T, Freyssinet JM, Dreyfus M.

Br J Haematol. 2005 Nov;131(4):487-9.


Identification of genes involved in Ca2+ ionophore A23187-mediated apoptosis and demonstration of a high susceptibility for transcriptional repression of cell cycle genes in B lymphoblasts from a patient with Scott syndrome.

Kozian D, Proulle V, Nitsche A, Galitzine M, Martinez MC, Schumann B, Meyer D, Herrmann M, Freyssinet JM, Kerbiriou-Nabias D.

BMC Genomics. 2005 Oct 21;6:146.


[Misdiagnosis of venous thrombosis in childhood].

Lachambre G, Proulle V, Bader-Meunier B, Dreyfus M.

Arch Pediatr. 2005 Feb;12(2):180-2. French.


Injection of recombinant activated factor VII can induce transient increase in circulating procoagulant microparticles.

Proulle V, Hugel B, Guillet B, Trichet C, Rafowicz A, Lambert T, Freyssinet JM, Dreyfus M.

Thromb Haemost. 2004 May;91(5):873-8.


Misdiagnosis of chronic thrombocytopenia in childhood.

Bader-Meunier B, Proulle V, Trichet C, Debray D, Gabolde M, Yvart J, Dreyfus M.

J Pediatr Hematol Oncol. 2003 Jul;25(7):548-52.


Two novel mutations, Q1053H and C1060R, located in the D3 domain of von Willebrand factor, are responsible for decreased FVIII-binding capacity.

Hilbert L, Jorieux S, Proulle V, Favier R, Goudemand J, Parquet A, Meyer D, Fressinaud E, Mazurier C; INSERM Network on Molecular Abnormalities in von Willebrand Disease.

Br J Haematol. 2003 Feb;120(4):627-32.


Protein A Sepharose immunoadsorption can restore the efficacy of platelet concentrates in patients with Glanzmann's thrombasthenia and anti-glycoprotein IIb-IIIa antibodies.

Martin I, Kriaa F, Proulle V, Guillet B, Kaplan C, D'Oiron R, Debré M, Fressinaud E, Laurian Y, Tchernia G, Charpentier B, Lambert T, Dreyfus M.

Br J Haematol. 2002 Dec;119(4):991-7.


Myocardial infarction occurring in a case of acquired haemophilia during the treatment course with recombinant activated factor VII.

Guillet B, Pinganaud C, Proulle V, Dreyfus M, Lambert T.

Thromb Haemost. 2002 Oct;88(4):698-9. No abstract available.


Intracerebral hemorrhage associated with a novel antithrombin gene mutation in a neonate.

Baud O, Picard V, Durand P, Duchemin J, Proulle V, Alhenc-Gelas M, Devictor D, Dreyfus M.

J Pediatr. 2001 Nov;139(5):741-3.


Protein A sepharose immunoadsorption: immunological and haemostatic effects in two cases of acquired haemophilia.

Guillet B, Kriaa F, Huysse MG, Proulle V, George C, Tchernia G, D'Oiron R, Laurian Y, Charpentier B, Lambert T, Dreyfus M.

Br J Haematol. 2001 Sep;114(4):837-44.


GPIaIIa as a candidate target for anti-platelet autoantibody occurring during valproate therapy and associated with peroperative bleeding.

Proulle V, Masnou P, Cartron J, Kaplan C, Ajzenberg N, Tchernia G, Dreyfus M.

Thromb Haemost. 2000 Jan;83(1):175-6. No abstract available.


Gene frequencies of human platelet antigens in the Tunisian population.

Mojaat N, Halle L, Proulle V, Hmida S, Ben Hamed L, Boukef K, Kaplan C.

Tissue Antigens. 1999 Aug;54(2):201-4.


A three amino acid deletion in glycoprotein IIIa is responsible for type I Glanzmann's thrombasthenia: importance of residues Ile325Pro326Gly327 for beta3 integrin subunit association.

Morel-Kopp MC, Kaplan C, Proulle V, Jallu V, Melchior C, Peyruchaud O, Aurousseau MH, Kieffer N.

Blood. 1997 Jul 15;90(2):669-77.

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