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Items: 1 to 50 of 85

1.

Palatal myoclonus, abnormal eye movements, and olivary hypertrophy in GAD65-related disorder.

Macaron G, Willis MA, Ontaneda D, Fernandez H, Kim S, Jones SE, Pioro EP, Cohen JA.

Neurology. 2020 Feb 11;94(6):273-275. doi: 10.1212/WNL.0000000000008926. Epub 2019 Dec 31. No abstract available.

PMID:
31892635
2.

Primary lateral sclerosis (PLS) functional rating scale: PLS-specific clinimetric scale.

Mitsumoto H, Chiuzan C, Gilmore M, Zhang Y, Simmons Z, Paganoni S, Kisanuki YY, Zinman L, Jawdat O, Sorenson E, Floeter MK, Pioro EP, Fernandes Filho JAM, Heitzman D, Fournier CN, Oskarsson B, Heiman-Patterson T, Maragakis N, Joyce N, Hayat G, Nations S, Scelsa S, Walk D, Elman L, Hupf J, McHale B; PLSFRS study group.

Muscle Nerve. 2020 Feb;61(2):163-172. doi: 10.1002/mus.26765. Epub 2019 Dec 13.

PMID:
31758557
3.

Long-term edaravone efficacy in amyotrophic lateral sclerosis: Post-hoc analyses of Study 19 (MCI186-19).

Shefner J, Heiman-Patterson T, Pioro EP, Wiedau-Pazos M, Liu S, Zhang J, Agnese W, Apple S.

Muscle Nerve. 2020 Feb;61(2):218-221. doi: 10.1002/mus.26740. Epub 2019 Nov 11.

4.

Pattern of lung function decline in patients with amyotrophic lateral sclerosis: implications for timing of noninvasive ventilation.

Panchabhai TS, Mireles Cabodevila E, Pioro EP, Wang X, Han X, Aboussouan LS.

ERJ Open Res. 2019 Sep 25;5(3). pii: 00044-2019. doi: 10.1183/23120541.00044-2019. eCollection 2019 Jul.

5.

Stage-specific riluzole effect in amyotrophic lateral sclerosis: a retrospective study.

Thakore NJ, Lapin BR, Pioro EP; Pooled Resource Open-Access Als Clinical Trials Consortium.

Amyotroph Lateral Scler Frontotemporal Degener. 2020 Feb;21(1-2):140-143. doi: 10.1080/21678421.2019.1655060. Epub 2019 Aug 27.

PMID:
31450993
6.

Unbiased MRI Analyses Identify Micropathologic Differences Between Upper Motor Neuron-Predominant ALS Phenotypes.

Rajagopalan V, Pioro EP.

Front Neurosci. 2019 Jul 12;13:704. doi: 10.3389/fnins.2019.00704. eCollection 2019. Review.

7.

Variation in noninvasive ventilation use in amyotrophic lateral sclerosis.

Thakore NJ, Lapin BR, Pioro EP, Aboussouan LS.

Neurology. 2019 Jul 16;93(3):e306-e316. doi: 10.1212/WNL.0000000000007776. Epub 2019 Jun 10.

PMID:
31182506
8.

Longitudinal 18F-FDG PET and MRI Reveal Evolving Imaging Pathology That Corresponds to Disease Progression in a Patient With ALS-FTD.

Rajagopalan V, Pioro EP.

Front Neurol. 2019 Mar 19;10:234. doi: 10.3389/fneur.2019.00234. eCollection 2019.

9.

Revised Airlie House consensus guidelines for design and implementation of ALS clinical trials.

van den Berg LH, Sorenson E, Gronseth G, Macklin EA, Andrews J, Baloh RH, Benatar M, Berry JD, Chio A, Corcia P, Genge A, Gubitz AK, Lomen-Hoerth C, McDermott CJ, Pioro EP, Rosenfeld J, Silani V, Turner MR, Weber M, Brooks BR, Miller RG, Mitsumoto H; Airlie House ALS Clinical Trials Guidelines Group.

Neurology. 2019 Apr 2;92(14):e1610-e1623. doi: 10.1212/WNL.0000000000007242. Epub 2019 Mar 8.

10.

Provisional best practices guidelines for the evaluation of bulbar dysfunction in amyotrophic lateral sclerosis.

Pattee GL, Plowman EK, Focht Garand KL, Costello J, Brooks BR, Berry JD, Smith RA, Atassi N, Chapin JL, Yunusova Y, McIlduff CE, Young E, Macklin EA, Locatelli ER, Silani V, Heitzman D, Wymer J, Goutman SA, Gelinas DF, Perry B, Nalipinski P, Stipancic K, O'Brien M, Sullivan SL, Pioro EP, Gargiulo G, Green JR; Contributing Members of the NEALS Bulbar Subcommittee.

Muscle Nerve. 2019 May;59(5):531-536. doi: 10.1002/mus.26408. Epub 2019 Jan 22.

PMID:
30620104
11.

Additional evidence for a therapeutic effect of dextromethorphan/quinidine on bulbar motor function in patients with amyotrophic lateral sclerosis: A quantitative speech analysis.

Green JR, Allison KM, Cordella C, Richburg BD, Pattee GL, Berry JD, Macklin EA, Pioro EP, Smith RA.

Br J Clin Pharmacol. 2018 Dec;84(12):2849-2856. doi: 10.1111/bcp.13745. Epub 2018 Oct 1.

12.

Deconstructing progression of amyotrophic lateral sclerosis in stages: a Markov modeling approach.

Thakore NJ, Lapin BR, Kinzy TG, Pioro EP.

Amyotroph Lateral Scler Frontotemporal Degener. 2018 Nov;19(7-8):483-494. doi: 10.1080/21678421.2018.1484925. Epub 2018 Jul 12.

PMID:
30001159
13.

Distal Predominance of Electrodiagnostic Abnormalities in Early-Stage Amyotrophic Lateral Sclerosis.

Shayya L, Babu S, Pioro EP, Li J, Li Y.

Muscle Nerve. 2018 Sep;58(3):389-395. doi: 10.1002/mus.26158. Epub 2018 Aug 23.

PMID:
29742797
14.

Assessment of bulbar function in amyotrophic lateral sclerosis: validation of a self-report scale (Center for Neurologic Study Bulbar Function Scale).

Smith RA, Macklin EA, Myers KJ, Pattee GL, Goslin KL, Meekins GD, Green JR, Shefner JM, Pioro EP.

Eur J Neurol. 2018 Jul;25(7):907-e66. doi: 10.1111/ene.13638. Epub 2018 Apr 16. Erratum in: Eur J Neurol. 2018 Oct;25(10):1303.

15.

Genome-wide Analyses Identify KIF5A as a Novel ALS Gene.

Nicolas A, Kenna KP, Renton AE, Ticozzi N, Faghri F, Chia R, Dominov JA, Kenna BJ, Nalls MA, Keagle P, Rivera AM, van Rheenen W, Murphy NA, van Vugt JJFA, Geiger JT, Van der Spek RA, Pliner HA, Shankaracharya, Smith BN, Marangi G, Topp SD, Abramzon Y, Gkazi AS, Eicher JD, Kenna A; ITALSGEN Consortium, Mora G, Calvo A, Mazzini L, Riva N, Mandrioli J, Caponnetto C, Battistini S, Volanti P, La Bella V, Conforti FL, Borghero G, Messina S, Simone IL, Trojsi F, Salvi F, Logullo FO, D'Alfonso S, Corrado L, Capasso M, Ferrucci L; Genomic Translation for ALS Care (GTAC) Consortium, Moreno CAM, Kamalakaran S, Goldstein DB; ALS Sequencing Consortium, Gitler AD, Harris T, Myers RM; NYGC ALS Consortium, Phatnani H, Musunuri RL, Evani US, Abhyankar A, Zody MC; Answer ALS Foundation, Kaye J, Finkbeiner S, Wyman SK, LeNail A, Lima L, Fraenkel E, Svendsen CN, Thompson LM, Van Eyk JE, Berry JD, Miller TM, Kolb SJ, Cudkowicz M, Baxi E; Clinical Research in ALS and Related Disorders for Therapeutic Development (CReATe) Consortium, Benatar M, Taylor JP, Rampersaud E, Wu G, Wuu J; SLAGEN Consortium, Lauria G, Verde F, Fogh I, Tiloca C, Comi GP, Sorarù G, Cereda C; French ALS Consortium, Corcia P, Laaksovirta H, Myllykangas L, Jansson L, Valori M, Ealing J, Hamdalla H, Rollinson S, Pickering-Brown S, Orrell RW, Sidle KC, Malaspina A, Hardy J, Singleton AB, Johnson JO, Arepalli S, Sapp PC, McKenna-Yasek D, Polak M, Asress S, Al-Sarraj S, King A, Troakes C, Vance C, de Belleroche J, Baas F, Ten Asbroek ALMA, Muñoz-Blanco JL, Hernandez DG, Ding J, Gibbs JR, Scholz SW, Floeter MK, Campbell RH, Landi F, Bowser R, Pulst SM, Ravits JM, MacGowan DJL, Kirby J, Pioro EP, Pamphlett R, Broach J, Gerhard G, Dunckley TL, Brady CB, Kowall NW, Troncoso JC, Le Ber I, Mouzat K, Lumbroso S, Heiman-Patterson TD, Kamel F, Van Den Bosch L, Baloh RH, Strom TM, Meitinger T, Shatunov A, Van Eijk KR, de Carvalho M, Kooyman M, Middelkoop B, Moisse M, McLaughlin RL, Van Es MA, Weber M, Boylan KB, Van Blitterswijk M, Rademakers R, Morrison KE, Basak AN, Mora JS, Drory VE, Shaw PJ, Turner MR, Talbot K, Hardiman O, Williams KL, Fifita JA, Nicholson GA, Blair IP, Rouleau GA, Esteban-Pérez J, García-Redondo A, Al-Chalabi A; Project MinE ALS Sequencing Consortium, Rogaeva E, Zinman L, Ostrow LW, Maragakis NJ, Rothstein JD, Simmons Z, Cooper-Knock J, Brice A, Goutman SA, Feldman EL, Gibson SB, Taroni F, Ratti A, Gellera C, Van Damme P, Robberecht W, Fratta P, Sabatelli M, Lunetta C, Ludolph AC, Andersen PM, Weishaupt JH, Camu W, Trojanowski JQ, Van Deerlin VM, Brown RH Jr, van den Berg LH, Veldink JH, Harms MB, Glass JD, Stone DJ, Tienari P, Silani V, Chiò A, Shaw CE, Traynor BJ, Landers JE.

Neuron. 2018 Mar 21;97(6):1268-1283.e6. doi: 10.1016/j.neuron.2018.02.027.

16.

MR Imaging-based Estimation of Upper Motor Neuron Density in Patients with Amyotrophic Lateral Sclerosis: A Feasibility Study.

Chen J, Kostenko V, Pioro EP, Trapp BD.

Radiology. 2018 Jun;287(3):955-964. doi: 10.1148/radiol.2018162967. Epub 2018 Jan 23.

17.

Trajectories of impairment in amyotrophic lateral sclerosis: Insights from the Pooled Resource Open-Access ALS Clinical Trials cohort.

Thakore NJ, Lapin BR, Pioro EP; Pooled Resource Open-Access ALS Clinical Trials Consortium.

Muscle Nerve. 2018 Jun;57(6):937-945. doi: 10.1002/mus.26042. Epub 2018 Jan 11.

PMID:
29244213
18.

Laughter, crying and sadness in ALS.

Thakore NJ, Pioro EP.

J Neurol Neurosurg Psychiatry. 2017 Oct;88(10):825-831. doi: 10.1136/jnnp-2017-315622. Epub 2017 Jun 1.

19.

Positron emission tomography imaging in a case of E200K mutation-related spongiform encephalopathy with non-diagnostic magnetic resonance imaging and cerebrospinal fluid testing.

George P, Newey CR, Mente KP, Pioro EP.

SAGE Open Med Case Rep. 2017 Mar 29;5:2050313X17700347. doi: 10.1177/2050313X17700347. eCollection 2017.

20.

Finger extension weakness and downbeat nystagmus motor neuron disease syndrome: A novel motor neuron disorder?

Delva A, Thakore N, Pioro EP, Poesen K, Saunders-Pullman R, Meijer IA, Rucker JC, Kissel JT, Van Damme P.

Muscle Nerve. 2017 Dec;56(6):1164-1168. doi: 10.1002/mus.25669. Epub 2017 May 15.

21.
22.

Depression in ALS in a large self-reporting cohort.

Kawada T, Thakore NJ, Pioro EP.

Neurology. 2016 Oct 11;87(15):1631-1632. No abstract available.

PMID:
27765825
23.

Optimizing muscle selection for electromyography in amyotrophic lateral sclerosis.

Babu S, Pioro EP, Li J, Li Y.

Muscle Nerve. 2017 Jul;56(1):36-44. doi: 10.1002/mus.25444. Epub 2017 Feb 15.

PMID:
27759887
24.

Depression in ALS in a large self-reporting cohort.

Thakore NJ, Pioro EP.

Neurology. 2016 Mar 15;86(11):1031-8. doi: 10.1212/WNL.0000000000002465. Epub 2016 Feb 17.

PMID:
26888995
25.

Brain Parenchymal Fraction: A Relatively Simple MRI Measure to Clinically Distinguish ALS Phenotypes.

Rajagopalan V, Pioro EP.

Biomed Res Int. 2015;2015:693206. doi: 10.1155/2015/693206. Epub 2015 Dec 13.

26.

Review of Dextromethorphan 20 mg/Quinidine 10 mg (NUEDEXTA(®)) for Pseudobulbar Affect.

Pioro EP.

Neurol Ther. 2014 Jun 17;3(1):15-28. doi: 10.1007/s40120-014-0018-5. eCollection 2014 Jun. Review.

27.
28.

Comparing brain structural MRI and metabolic FDG-PET changes in patients with ALS-FTD: 'the chicken or the egg?' question.

Rajagopalan V, Pioro EP.

J Neurol Neurosurg Psychiatry. 2015 Sep;86(9):952-8. doi: 10.1136/jnnp-2014-308239. Epub 2014 Dec 17.

PMID:
25520437
29.

Mutations in the Matrin 3 gene cause familial amyotrophic lateral sclerosis.

Johnson JO, Pioro EP, Boehringer A, Chia R, Feit H, Renton AE, Pliner HA, Abramzon Y, Marangi G, Winborn BJ, Gibbs JR, Nalls MA, Morgan S, Shoai M, Hardy J, Pittman A, Orrell RW, Malaspina A, Sidle KC, Fratta P, Harms MB, Baloh RH, Pestronk A, Weihl CC, Rogaeva E, Zinman L, Drory VE, Borghero G, Mora G, Calvo A, Rothstein JD; ITALSGEN, Drepper C, Sendtner M, Singleton AB, Taylor JP, Cookson MR, Restagno G, Sabatelli M, Bowser R, Chiò A, Traynor BJ.

Nat Neurosci. 2014 May;17(5):664-666. doi: 10.1038/nn.3688. Epub 2014 Mar 30.

30.

Distinct patterns of cortical atrophy in ALS patients with or without dementia: an MRI VBM study.

Rajagopalan V, Pioro EP.

Amyotroph Lateral Scler Frontotemporal Degener. 2014 Jun;15(3-4):216-25. doi: 10.3109/21678421.2014.880179. Epub 2014 Feb 20.

PMID:
24555884
31.
32.

Brain white matter shape changes in amyotrophic lateral sclerosis (ALS): a fractal dimension study.

Rajagopalan V, Liu Z, Allexandre D, Zhang L, Wang XF, Pioro EP, Yue GH.

PLoS One. 2013 Sep 9;8(9):e73614. doi: 10.1371/journal.pone.0073614. eCollection 2013.

33.

Use of intrathecal baclofen for treatment of severe spasticity in selected patients with motor neuron disease.

Bethoux F, Boulis N, McClelland S 3rd, Willis MA, Hussain M, Machado A, Mychkovsky L, Stough D, Sutliff M, Pioro EP.

Neurorehabil Neural Repair. 2013 Nov-Dec;27(9):828-33. doi: 10.1177/1545968313496325. Epub 2013 Jul 24.

PMID:
23884016
34.

Brain white matter diffusion tensor metrics from clinical 1.5T MRI distinguish between ALS phenotypes.

Rajagopalan V, Yue GH, Pioro EP.

J Neurol. 2013 Oct;260(10):2532-40. doi: 10.1007/s00415-013-7012-1. Epub 2013 Jul 18.

PMID:
23864396
35.

T2 relaxometry measurements in low spatial frequency brain regions differ between fast spin-echo and multiple-echo spin-echo sequences.

Rajagopalan V, Lowe MJ, Beall EB, Yue GH, Pioro EP.

MAGMA. 2013 Oct;26(5):443-50. doi: 10.1007/s10334-012-0364-1. Epub 2013 Jan 26.

PMID:
23354513
36.

Amyotrophic lateral sclerosis and novel therapeutic strategies.

Morrison B, Hensley K, Pioro EP, Petri S, Kiaei M.

Neurol Res Int. 2012;2012:798028. doi: 10.1155/2012/798028. Epub 2012 Dec 19. No abstract available.

37.

Diffusion Tensor Imaging Evaluation of Corticospinal Tract Hyperintensity in Upper Motor Neuron-Predominant ALS Patients.

Rajagopalan V, Allexandre D, Yue GH, Pioro EP.

J Aging Res. 2011;2011:481745. doi: 10.4061/2011/481745. Epub 2011 Oct 26.

38.

Current concepts in the pharmacotherapy of pseudobulbar affect.

Pioro EP.

Drugs. 2011 Jun 18;71(9):1193-207. doi: 10.2165/11591450-000000000-00000. Review.

PMID:
21711063
39.

Eye movements in amyotrophic lateral sclerosis and its mimics: a review with illustrative cases.

Donaghy C, Thurtell MJ, Pioro EP, Gibson JM, Leigh RJ.

J Neurol Neurosurg Psychiatry. 2011 Jan;82(1):110-6. doi: 10.1136/jnnp.2010.212407. Epub 2010 Nov 19. Review.

PMID:
21097546
40.

Dextromethorphan plus ultra low-dose quinidine reduces pseudobulbar affect.

Pioro EP, Brooks BR, Cummings J, Schiffer R, Thisted RA, Wynn D, Hepner A, Kaye R; Safety, Tolerability, and Efficacy Results Trial of AVP-923 in PBA Investigators.

Ann Neurol. 2010 Nov;68(5):693-702. doi: 10.1002/ana.22093.

PMID:
20839238
41.

Structural basis for the wobbler mouse neurodegenerative disorder caused by mutation in the Vps54 subunit of the GARP complex.

Pérez-Victoria FJ, Abascal-Palacios G, Tascón I, Kajava A, Magadán JG, Pioro EP, Bonifacino JS, Hierro A.

Proc Natl Acad Sci U S A. 2010 Jul 20;107(29):12860-5. doi: 10.1073/pnas.1004756107. Epub 2010 Jul 6.

42.

Cervical epidural injection complicated by syrinx formation: a case report.

Khan S, Pioro EP.

Spine (Phila Pa 1976). 2010 Jun 1;35(13):E614-6. doi: 10.1097/BRS.0b013e3181cf7621.

PMID:
20461029
43.

Familial ALS with SOD1 mutation misdiagnosed with polyradiculopathy and myopathy.

Zhou L, Pioro EP.

Amyotroph Lateral Scler. 2009 Oct-Dec;10(5-6):476-8. doi: 10.3109/17482960802449278.

PMID:
19922143
44.

Phase II trial of CoQ10 for ALS finds insufficient evidence to justify phase III.

Kaufmann P, Thompson JL, Levy G, Buchsbaum R, Shefner J, Krivickas LS, Katz J, Rollins Y, Barohn RJ, Jackson CE, Tiryaki E, Lomen-Hoerth C, Armon C, Tandan R, Rudnicki SA, Rezania K, Sufit R, Pestronk A, Novella SP, Heiman-Patterson T, Kasarskis EJ, Pioro EP, Montes J, Arbing R, Vecchio D, Barsdorf A, Mitsumoto H, Levin B; QALS Study Group.

Ann Neurol. 2009 Aug;66(2):235-44. doi: 10.1002/ana.21743.

45.

Lack of evidence of monomer/misfolded superoxide dismutase-1 in sporadic amyotrophic lateral sclerosis.

Liu HN, Sanelli T, Horne P, Pioro EP, Strong MJ, Rogaeva E, Bilbao J, Zinman L, Robertson J.

Ann Neurol. 2009 Jul;66(1):75-80. doi: 10.1002/ana.21704.

PMID:
19670443
46.

Abnormal eye movements in Kennedy disease.

Thurtell MJ, Pioro EP, Leigh RJ.

Neurology. 2009 Apr 28;72(17):1528-30. doi: 10.1212/WNL.0b013e3181a2e936. No abstract available.

47.

A two-stage genome-wide association study of sporadic amyotrophic lateral sclerosis.

Chiò A, Schymick JC, Restagno G, Scholz SW, Lombardo F, Lai SL, Mora G, Fung HC, Britton A, Arepalli S, Gibbs JR, Nalls M, Berger S, Kwee LC, Oddone EZ, Ding J, Crews C, Rafferty I, Washecka N, Hernandez D, Ferrucci L, Bandinelli S, Guralnik J, Macciardi F, Torri F, Lupoli S, Chanock SJ, Thomas G, Hunter DJ, Gieger C, Wichmann HE, Calvo A, Mutani R, Battistini S, Giannini F, Caponnetto C, Mancardi GL, La Bella V, Valentino F, Monsurrò MR, Tedeschi G, Marinou K, Sabatelli M, Conte A, Mandrioli J, Sola P, Salvi F, Bartolomei I, Siciliano G, Carlesi C, Orrell RW, Talbot K, Simmons Z, Connor J, Pioro EP, Dunkley T, Stephan DA, Kasperaviciute D, Fisher EM, Jabonka S, Sendtner M, Beck M, Bruijn L, Rothstein J, Schmidt S, Singleton A, Hardy J, Traynor BJ.

Hum Mol Genet. 2009 Apr 15;18(8):1524-32. doi: 10.1093/hmg/ddp059. Epub 2009 Feb 4.

48.

Racing against the clock: recognizing, differentiating, diagnosing, and referring the amyotrophic lateral sclerosis patient.

Shook SJ, Pioro EP.

Ann Neurol. 2009 Jan;65 Suppl 1:S10-6. doi: 10.1002/ana.21545.

PMID:
19191305
49.

Intrathecal baclofen for spasticity-related pain in amyotrophic lateral sclerosis: efficacy and factors associated with pain relief.

McClelland S 3rd, Bethoux FA, Boulis NM, Sutliff MH, Stough DK, Schwetz KM, Gogol DM, Harrison M, Pioro EP.

Muscle Nerve. 2008 Mar;37(3):396-8.

PMID:
17894358
50.

A randomized controlled trial of resistance exercise in individuals with ALS.

Bello-Haas VD, Florence JM, Kloos AD, Scheirbecker J, Lopate G, Hayes SM, Pioro EP, Mitsumoto H.

Neurology. 2007 Jun 5;68(23):2003-7.

PMID:
17548549

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