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Items: 28


Maturation of selected human mitochondrial tRNAs requires deadenylation.

Pearce SF, Rorbach J, Van Haute L, D'Souza AR, Rebelo-Guiomar P, Powell CA, Brierley I, Firth AE, Minczuk M.

Elife. 2017 Jul 26;6. pii: e27596. doi: 10.7554/eLife.27596.


Regulation of Mammalian Mitochondrial Gene Expression: Recent Advances.

Pearce SF, Rebelo-Guiomar P, D'Souza AR, Powell CA, Van Haute L, Minczuk M.

Trends Biochem Sci. 2017 Aug;42(8):625-639. doi: 10.1016/j.tibs.2017.02.003. Epub 2017 Mar 9. Review.


Deficient methylation and formylation of mt-tRNA(Met) wobble cytosine in a patient carrying mutations in NSUN3.

Van Haute L, Dietmann S, Kremer L, Hussain S, Pearce SF, Powell CA, Rorbach J, Lantaff R, Blanco S, Sauer S, Kotzaeridou U, Hoffmann GF, Memari Y, Kolb-Kokocinski A, Durbin R, Mayr JA, Frye M, Prokisch H, Minczuk M.

Nat Commun. 2016 Jun 30;7:12039. doi: 10.1038/ncomms12039.


Mitochondrial transcript maturation and its disorders.

Van Haute L, Pearce SF, Powell CA, D'Souza AR, Nicholls TJ, Minczuk M.

J Inherit Metab Dis. 2015 Jul;38(4):655-80. doi: 10.1007/s10545-015-9859-z. Epub 2015 May 28. Review.


Mutations in GTPBP3 cause a mitochondrial translation defect associated with hypertrophic cardiomyopathy, lactic acidosis, and encephalopathy.

Kopajtich R, Nicholls TJ, Rorbach J, Metodiev MD, Freisinger P, Mandel H, Vanlander A, Ghezzi D, Carrozzo R, Taylor RW, Marquard K, Murayama K, Wieland T, Schwarzmayr T, Mayr JA, Pearce SF, Powell CA, Saada A, Ohtake A, Invernizzi F, Lamantea E, Sommerville EW, Pyle A, Chinnery PF, Crushell E, Okazaki Y, Kohda M, Kishita Y, Tokuzawa Y, Assouline Z, Rio M, Feillet F, Mousson de Camaret B, Chretien D, Munnich A, Menten B, Sante T, Smet J, Régal L, Lorber A, Khoury A, Zeviani M, Strom TM, Meitinger T, Bertini ES, Van Coster R, Klopstock T, Rötig A, Haack TB, Minczuk M, Prokisch H.

Am J Hum Genet. 2014 Dec 4;95(6):708-20. doi: 10.1016/j.ajhg.2014.10.017. Epub 2014 Nov 26.


Two siblings with homozygous pathogenic splice-site variant in mitochondrial asparaginyl-tRNA synthetase (NARS2).

Vanlander AV, Menten B, Smet J, De Meirleir L, Sante T, De Paepe B, Seneca S, Pearce SF, Powell CA, Vergult S, Michotte A, De Latter E, Vantomme L, Minczuk M, Van Coster R.

Hum Mutat. 2015 Feb;36(2):222-31. doi: 10.1002/humu.22728.


MRM2 and MRM3 are involved in biogenesis of the large subunit of the mitochondrial ribosome.

Rorbach J, Boesch P, Gammage PA, Nicholls TJ, Pearce SF, Patel D, Hauser A, Perocchi F, Minczuk M.

Mol Biol Cell. 2014 Sep 1;25(17):2542-55. doi: 10.1091/mbc.E14-01-0014. Epub 2014 Jul 9.


MPV17L2 is required for ribosome assembly in mitochondria.

Dalla Rosa I, Durigon R, Pearce SF, Rorbach J, Hirst EM, Vidoni S, Reyes A, Brea-Calvo G, Minczuk M, Woellhaf MW, Herrmann JM, Huynen MA, Holt IJ, Spinazzola A.

Nucleic Acids Res. 2014 Jul;42(13):8500-15. doi: 10.1093/nar/gku513. Epub 2014 Jun 19.


Amino acid starvation has opposite effects on mitochondrial and cytosolic protein synthesis.

Johnson MA, Vidoni S, Durigon R, Pearce SF, Rorbach J, He J, Brea-Calvo G, Minczuk M, Reyes A, Holt IJ, Spinazzola A.

PLoS One. 2014 Apr 9;9(4):e93597. doi: 10.1371/journal.pone.0093597. eCollection 2014.


Hematopoietic cell transplantation in first complete remission versus early relapse.

Appelbaum FR, Pearce SF.

Best Pract Res Clin Haematol. 2006;19(2):333-9. Review.


Induction of CD36 expression by oxidized LDL and IL-4 by a common signaling pathway dependent on protein kinase C and PPAR-gamma.

Feng J, Han J, Pearce SF, Silverstein RL, Gotto AM Jr, Hajjar DP, Nicholson AC.

J Lipid Res. 2000 May;41(5):688-96.


A null mutation in murine CD36 reveals an important role in fatty acid and lipoprotein metabolism.

Febbraio M, Abumrad NA, Hajjar DP, Sharma K, Cheng W, Pearce SF, Silverstein RL.

J Biol Chem. 1999 Jul 2;274(27):19055-62.


Retinoic acid alters the mechanism of attachment of malignant astrocytoma and neuroblastoma cells to thrombospondin-1.

Pijuan-Thompson V, Grammer JR, Stewart J, Silverstein RL, Pearce SF, Tuszynski GP, Murphy-Ullrich JE, Gladson CL.

Exp Cell Res. 1999 May 25;249(1):86-101.


Three distinct D-amino acid substitutions confer potent antiangiogenic activity on an inactive peptide derived from a thrombospondin-1 type 1 repeat.

Dawson DW, Volpert OV, Pearce SF, Schneider AJ, Silverstein RL, Henkin J, Bouck NP.

Mol Pharmacol. 1999 Feb;55(2):332-8.


Recombinant glutathione S-transferase/CD36 fusion proteins define an oxidized low density lipoprotein-binding domain.

Pearce SF, Roy P, Nicholson AC, Hajjar DP, Febbraio M, Silverstein RL.

J Biol Chem. 1998 Dec 25;273(52):34875-81.


Immature dendritic cells phagocytose apoptotic cells via alphavbeta5 and CD36, and cross-present antigens to cytotoxic T lymphocytes.

Albert ML, Pearce SF, Francisco LM, Sauter B, Roy P, Silverstein RL, Bhardwaj N.

J Exp Med. 1998 Oct 5;188(7):1359-68.


CD36 mediates the In vitro inhibitory effects of thrombospondin-1 on endothelial cells.

Dawson DW, Pearce SF, Zhong R, Silverstein RL, Frazier WA, Bouck NP.

J Cell Biol. 1997 Aug 11;138(3):707-17.


Regulation of monocyte CD36 and thrombospondin-1 expression by soluble mediators.

Yesner LM, Huh HY, Pearce SF, Silverstein RL.

Arterioscler Thromb Vasc Biol. 1996 Aug;16(8):1019-25.


Regulated expression of CD36 during monocyte-to-macrophage differentiation: potential role of CD36 in foam cell formation.

Huh HY, Pearce SF, Yesner LM, Schindler JL, Silverstein RL.

Blood. 1996 Mar 1;87(5):2020-8.


Nitric oxide-stimulated guanine nucleotide exchange on p21ras.

Lander HM, Ogiste JS, Pearce SF, Levi R, Novogrodsky A.

J Biol Chem. 1995 Mar 31;270(13):7017-20.


Characterization of BADS-binding proteins in epithelial plasma membranes.

Pearce SF, Zadunaisky JA.

J Membr Biol. 1991 Sep;123(3):235-45.


The role of tyrosine at the ligand-binding site of the nicotinic acetylcholine receptor.

Pearce SF, Preston-Hurlburt P, Hawrot E.

Proc Biol Sci. 1990 Sep 22;241(1302):207-13.


Fluorescent stilbene (BADS) binding proteins in anion-transporting epithelia.

Pearce SF, Zadunaisky JA.

Am J Physiol. 1990 Sep;259(3 Pt 1):C439-49.


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