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Items: 20

1.

Overriding FUS autoregulation in mice triggers gain-of-toxic dysfunctions in RNA metabolism and autophagy-lysosome axis.

Ling SC, Dastidar SG, Tokunaga S, Ho WY, Lim K, Ilieva H, Parone PA, Tyan SH, Tse TM, Chang JC, Platoshyn O, Bui NB, Bui A, Vetto A, Sun S, McAlonis-Downes M, Han JS, Swing D, Kapeli K, Yeo GW, Tessarollo L, Marsala M, Shaw CE, Tucker-Kellogg G, La Spada AR, Lagier-Tourenne C, Da Cruz S, Cleveland DW.

Elife. 2019 Feb 12;8. pii: e40811. doi: 10.7554/eLife.40811.

2.

ALS/FTD-Linked Mutation in FUS Suppresses Intra-axonal Protein Synthesis and Drives Disease Without Nuclear Loss-of-Function of FUS.

López-Erauskin J, Tadokoro T, Baughn MW, Myers B, McAlonis-Downes M, Chillon-Marinas C, Asiaban JN, Artates J, Bui AT, Vetto AP, Lee SK, Le AV, Sun Y, Jambeau M, Boubaker J, Swing D, Qiu J, Hicks GG, Ouyang Z, Fu XD, Tessarollo L, Ling SC, Parone PA, Shaw CE, Marsala M, Lagier-Tourenne C, Cleveland DW, Da Cruz S.

Neuron. 2018 Nov 21;100(4):816-830.e7. doi: 10.1016/j.neuron.2018.09.044. Epub 2018 Oct 18.

3.

Misfolded SOD1 is not a primary component of sporadic ALS.

Da Cruz S, Bui A, Saberi S, Lee SK, Stauffer J, McAlonis-Downes M, Schulte D, Pizzo DP, Parone PA, Cleveland DW, Ravits J.

Acta Neuropathol. 2017 Jul;134(1):97-111. doi: 10.1007/s00401-017-1688-8. Epub 2017 Feb 28.

4.

Mitochondrial Isolation and Purification from Mouse Spinal Cord.

Parone PA, Da Cruz S, Cleveland DW.

Bio Protoc. 2013 Nov 5;3(21). pii: e961.

5.

Fused in sarcoma (FUS) protein lacking nuclear localization signal (NLS) and major RNA binding motifs triggers proteinopathy and severe motor phenotype in transgenic mice.

Shelkovnikova TA, Peters OM, Deykin AV, Connor-Robson N, Robinson H, Ustyugov AA, Bachurin SO, Ermolkevich TG, Goldman IL, Sadchikova ER, Kovrazhkina EA, Skvortsova VI, Ling SC, Da Cruz S, Parone PA, Buchman VL, Ninkina NN.

J Biol Chem. 2013 Aug 30;288(35):25266-74. doi: 10.1074/jbc.M113.492017. Epub 2013 Jul 18.

6.

Enhancing mitochondrial calcium buffering capacity reduces aggregation of misfolded SOD1 and motor neuron cell death without extending survival in mouse models of inherited amyotrophic lateral sclerosis.

Parone PA, Da Cruz S, Han JS, McAlonis-Downes M, Vetto AP, Lee SK, Tseng E, Cleveland DW.

J Neurosci. 2013 Mar 13;33(11):4657-71. doi: 10.1523/JNEUROSCI.1119-12.2013.

7.

ALS-linked TDP-43 mutations produce aberrant RNA splicing and adult-onset motor neuron disease without aggregation or loss of nuclear TDP-43.

Arnold ES, Ling SC, Huelga SC, Lagier-Tourenne C, Polymenidou M, Ditsworth D, Kordasiewicz HB, McAlonis-Downes M, Platoshyn O, Parone PA, Da Cruz S, Clutario KM, Swing D, Tessarollo L, Marsala M, Shaw CE, Yeo GW, Cleveland DW.

Proc Natl Acad Sci U S A. 2013 Feb 19;110(8):E736-45. doi: 10.1073/pnas.1222809110. Epub 2013 Feb 4.

8.

Elevated PGC-1α activity sustains mitochondrial biogenesis and muscle function without extending survival in a mouse model of inherited ALS.

Da Cruz S, Parone PA, Lopes VS, Lillo C, McAlonis-Downes M, Lee SK, Vetto AP, Petrosyan S, Marsala M, Murphy AN, Williams DS, Spiegelman BM, Cleveland DW.

Cell Metab. 2012 May 2;15(5):778-86. doi: 10.1016/j.cmet.2012.03.019.

9.

SLP-2 negatively modulates mitochondrial sodium-calcium exchange.

Da Cruz S, De Marchi U, Frieden M, Parone PA, Martinou JC, Demaurex N.

Cell Calcium. 2010 Jan;47(1):11-8. doi: 10.1016/j.ceca.2009.10.005. Epub 2009 Nov 26.

PMID:
19944461
10.

Preventing mitochondrial fission impairs mitochondrial function and leads to loss of mitochondrial DNA.

Parone PA, Da Cruz S, Tondera D, Mattenberger Y, James DI, Maechler P, Barja F, Martinou JC.

PLoS One. 2008 Sep 22;3(9):e3257. doi: 10.1371/journal.pone.0003257.

11.

SLP-2 interacts with prohibitins in the mitochondrial inner membrane and contributes to their stability.

Da Cruz S, Parone PA, Gonzalo P, Bienvenut WV, Tondera D, Jourdain A, Quadroni M, Martinou JC.

Biochim Biophys Acta. 2008 May;1783(5):904-11. doi: 10.1016/j.bbamcr.2008.02.006. Epub 2008 Feb 20.

12.

Mechanisms of mitochondrial outer membrane permeabilization.

James D, Parone PA, Terradillos O, Lucken-Ardjomande S, Montessuit S, Martinou JC.

Novartis Found Symp. 2007;287:170-6; discussion 176-82. Review.

PMID:
18074638
13.

Inhibiting the mitochondrial fission machinery does not prevent Bax/Bak-dependent apoptosis.

Parone PA, James DI, Da Cruz S, Mattenberger Y, Donzé O, Barja F, Martinou JC.

Mol Cell Biol. 2006 Oct;26(20):7397-408.

14.

Mitochondrial fission and apoptosis: an ongoing trial.

Parone PA, Martinou JC.

Biochim Biophys Acta. 2006 May-Jun;1763(5-6):522-30. Epub 2006 Apr 20. Review.

15.

Building the mitochondrial proteome.

Da Cruz S, Parone PA, Martinou JC.

Expert Rev Proteomics. 2005 Aug;2(4):541-51. Review.

PMID:
16097887
16.

Proteomic analysis of the mouse liver mitochondrial inner membrane.

Da Cruz S, Xenarios I, Langridge J, Vilbois F, Parone PA, Martinou JC.

J Biol Chem. 2003 Oct 17;278(42):41566-71. Epub 2003 Jul 15.

17.

hFis1, a novel component of the mammalian mitochondrial fission machinery.

James DI, Parone PA, Mattenberger Y, Martinou JC.

J Biol Chem. 2003 Sep 19;278(38):36373-9. Epub 2003 Jun 3. Erratum in: J Biol Chem. 2004 Aug 20;279(34):36166.

18.

Mitochondria: regulating the inevitable.

Parone PA, James D, Martinou JC.

Biochimie. 2002 Feb-Mar;84(2-3):105-11. Review.

PMID:
12022941
19.

Phosphorylation of the pro-apoptotic protein BAD on serine 155, a novel site, contributes to cell survival

Virdee K, Parone PA, Tolkovsky AM.

Curr Biol. 2000 Nov 30;10(23):R883. No abstract available.

20.

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