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Items: 1 to 50 of 316

1.

Acute kidney injury complicating nephrotic syndrome of minimal change disease.

Meyrier A, Niaudet P.

Kidney Int. 2018 Nov;94(5):861-869. doi: 10.1016/j.kint.2018.04.024. Epub 2018 Jul 3. Review.

PMID:
29980292
2.

Treatment and outcome of congenital nephrotic syndrome.

Bérody S, Heidet L, Gribouval O, Harambat J, Niaudet P, Baudouin V, Bacchetta J, Boudaillez B, Dehennault M, de Parscau L, Dunand O, Flodrops H, Fila M, Garnier A, Louillet F, Macher MA, May A, Merieau E, Monceaux F, Pietrement C, Rousset-Rouvière C, Roussey G, Taque S, Tenenbaum J, Ulinski T, Vieux R, Zaloszyc A, Morinière V, Salomon R, Boyer O.

Nephrol Dial Transplant. 2019 Mar 1;34(3):458-467. doi: 10.1093/ndt/gfy015.

PMID:
29474669
3.

Clinical and genetic heterogeneity in familial steroid-sensitive nephrotic syndrome.

Dorval G, Gribouval O, Martinez-Barquero V, Machuca E, Tête MJ, Baudouin V, Benoit S, Chabchoub I, Champion G, Chauveau D, Chehade H, Chouchane C, Cloarec S, Cochat P, Dahan K, Dantal J, Delmas Y, Deschênes G, Dolhem P, Durand D, Ekinci Z, El Karoui K, Fischbach M, Grunfeld JP, Guigonis V, Hachicha M, Hogan J, Hourmant M, Hummel A, Kamar N, Krummel T, Lacombe D, Llanas B, Mesnard L, Mohsin N, Niaudet P, Nivet H, Parvex P, Pietrement C, de Pontual L, Noble CP, Ribes D, Ronco P, Rondeau E, Sallee M, Tsimaratos M, Ulinski T, Salomon R, Antignac C, Boyer O.

Pediatr Nephrol. 2018 Mar;33(3):473-483. doi: 10.1007/s00467-017-3819-9. Epub 2017 Oct 23.

PMID:
29058154
4.

A randomized clinical trial indicates that levamisole increases the time to relapse in children with steroid-sensitive idiopathic nephrotic syndrome.

Gruppen MP, Bouts AH, Jansen-van der Weide MC, Merkus MP, Zurowska A, Maternik M, Massella L, Emma F, Niaudet P, Cornelissen EAM, Schurmans T, Raes A, van de Walle J, van Dyck M, Gulati A, Bagga A, Davin JC; all members of the Levamisole Study Group.

Kidney Int. 2018 Feb;93(2):510-518. doi: 10.1016/j.kint.2017.08.011. Epub 2017 Oct 18.

5.

A randomised Phase I/II trial to evaluate the efficacy and safety of orally administered Oxalobacter formigenes to treat primary hyperoxaluria.

Hoppe B, Niaudet P, Salomon R, Harambat J, Hulton SA, Van't Hoff W, Moochhala SH, Deschênes G, Lindner E, Sjögren A, Cochat P.

Pediatr Nephrol. 2017 May;32(5):781-790. doi: 10.1007/s00467-016-3553-8. Epub 2016 Dec 6.

PMID:
27924398
6.

Age-Dependent Risk of Graft Failure in Young Kidney Transplant Recipients.

Kaboré R, Couchoud C, Macher MA, Salomon R, Ranchin B, Lahoche A, Roussey-Kesler G, Garaix F, Decramer S, Pietrement C, Lassalle M, Baudouin V, Cochat P, Niaudet P, Joly P, Leffondré K, Harambat J.

Transplantation. 2017 Jun;101(6):1327-1335. doi: 10.1097/TP.0000000000001372.

PMID:
27482961
7.

Observations of a large Dent disease cohort.

Blanchard A, Curis E, Guyon-Roger T, Kahila D, Treard C, Baudouin V, Bérard E, Champion G, Cochat P, Dubourg J, de la Faille R, Devuyst O, Deschenes G, Fischbach M, Harambat J, Houillier P, Karras A, Knebelmann B, Lavocat MP, Loirat C, Merieau E, Niaudet P, Nobili F, Novo R, Salomon R, Ulinski T, Jeunemaître X, Vargas-Poussou R.

Kidney Int. 2016 Aug;90(2):430-439. doi: 10.1016/j.kint.2016.04.022. Epub 2016 Jun 22.

PMID:
27342959
8.

Excellent long-term outcome of renal transplantation in cystinosis patients.

Cohen C, Charbit M, Chadefaux-Vekemans B, Giral M, Garrigue V, Kessler M, Antoine C, Snanoudj R, Niaudet P, Kreis H, Legendre C, Servais A.

Orphanet J Rare Dis. 2015 Jul 25;10:90. doi: 10.1186/s13023-015-0307-9.

9.

Mutation Update of the CLCN5 Gene Responsible for Dent Disease 1.

Mansour-Hendili L, Blanchard A, Le Pottier N, Roncelin I, Lourdel S, Treard C, González W, Vergara-Jaque A, Morin G, Colin E, Holder-Espinasse M, Bacchetta J, Baudouin V, Benoit S, Bérard E, Bourdat-Michel G, Bouchireb K, Burtey S, Cailliez M, Cardon G, Cartery C, Champion G, Chauveau D, Cochat P, Dahan K, De la Faille R, Debray FG, Dehoux L, Deschenes G, Desport E, Devuyst O, Dieguez S, Emma F, Fischbach M, Fouque D, Fourcade J, François H, Gilbert-Dussardier B, Hannedouche T, Houillier P, Izzedine H, Janner M, Karras A, Knebelmann B, Lavocat MP, Lemoine S, Leroy V, Loirat C, Macher MA, Martin-Coignard D, Morin D, Niaudet P, Nivet H, Nobili F, Novo R, Faivre L, Rigothier C, Roussey-Kesler G, Salomon R, Schleich A, Sellier-Leclerc AL, Soulami K, Tiple A, Ulinski T, Vanhille P, Van Regemorter N, Jeunemaître X, Vargas-Poussou R.

Hum Mutat. 2015 Aug;36(8):743-52. doi: 10.1002/humu.22804. Epub 2015 Jun 11. Review.

PMID:
25907713
10.

Long-term results of combined liver-kidney transplantation for primary hyperoxaluria type 1: the French experience.

Compagnon P, Metzler P, Samuel D, Camus C, Niaudet P, Durrbach A, Lang P, Azoulay D, Duvoux C, Bayle F, Rivalan J, Merville P, Pascal G, Thervet E, Bensman A, Rostaing L, Deschenes G, Morcet J, Feray C, Boudjema K.

Liver Transpl. 2014 Dec;20(12):1475-85. doi: 10.1002/lt.24009.

11.

Nephropathic cystinosis: an international consensus document.

Emma F, Nesterova G, Langman C, Labbé A, Cherqui S, Goodyer P, Janssen MC, Greco M, Topaloglu R, Elenberg E, Dohil R, Trauner D, Antignac C, Cochat P, Kaskel F, Servais A, Wühl E, Niaudet P, Van't Hoff W, Gahl W, Levtchenko E.

Nephrol Dial Transplant. 2014 Sep;29 Suppl 4:iv87-94. doi: 10.1093/ndt/gfu090.

12.

Fanconi syndrome and severe polyuria: an uncommon clinicobiological presentation of a Gitelman syndrome.

Bouchireb K, Boyer O, Mansour-Hendili L, Garnier A, Heidet L, Niaudet P, Salomon R, Poussou RV.

BMC Pediatr. 2014 Aug 11;14:201. doi: 10.1186/1471-2431-14-201.

13.

Quality of life is improved and kidney function preserved in patients with nephropathic cystinosis treated for 2 years with delayed-release cysteamine bitartrate.

Langman CB, Greenbaum LA, Grimm P, Sarwal M, Niaudet P, Deschenes G, Cornelissen EA, Morin D, Cochat P, Elenberg E, Hanna C, Gaillard S, Bagger MJ, Rioux P.

J Pediatr. 2014 Sep;165(3):528-33.e1. doi: 10.1016/j.jpeds.2014.05.013. Epub 2014 Jun 16.

14.

A new gel formulation of topical cysteamine for the treatment of corneal cystine crystals in cystinosis: the Cystadrops OCT-1 study.

Labbé A, Baudouin C, Deschênes G, Loirat C, Charbit M, Guest G, Niaudet P.

Mol Genet Metab. 2014 Mar;111(3):314-320. doi: 10.1016/j.ymgme.2013.12.298. Epub 2014 Jan 9.

PMID:
24440466
15.

Allo-immune membranous nephropathy and recombinant aryl sulfatase replacement therapy: a need for tolerance induction therapy.

Debiec H, Valayannopoulos V, Boyer O, Nöel LH, Callard P, Sarda H, de Lonlay P, Niaudet P, Ronco P.

J Am Soc Nephrol. 2014 Apr;25(4):675-80. doi: 10.1681/ASN.2013030290. Epub 2013 Nov 21.

16.

Nephrotic syndrome: Rituximab in childhood steroid-dependent nephrotic syndrome.

Boyer O, Niaudet P.

Nat Rev Nephrol. 2013 Oct;9(10):562-3. doi: 10.1038/nrneph.2013.153. Epub 2013 Aug 13. No abstract available.

PMID:
23938594
17.

Long-term remission of atypical HUS with anti-factor H antibodies after cyclophosphamide pulses.

Sana G, Dragon-Durey MA, Charbit M, Bouchireb K, Rousset-Rouvière C, Bérard E, Salomon R, Frémeaux-Bacchi V, Niaudet P, Boyer O.

Pediatr Nephrol. 2014 Jan;29(1):75-83. doi: 10.1007/s00467-013-2558-9. Epub 2013 Jul 19.

PMID:
23868108
18.

Hydration measurement by bioimpedance spectroscopy and blood pressure management in children on hemodialysis.

Zaloszyc A, Schaefer B, Schaefer F, Krid S, Salomon R, Niaudet P, Schmitt CP, Fischbach M.

Pediatr Nephrol. 2013 Nov;28(11):2169-77. doi: 10.1007/s00467-013-2540-6. Epub 2013 Jul 7.

PMID:
23832099
19.

Renal transplantation in 4 patients with methylmalonic aciduria: a cell therapy for metabolic disease.

Brassier A, Boyer O, Valayannopoulos V, Ottolenghi C, Krug P, Cosson MA, Touati G, Arnoux JB, Barbier V, Bahi-Buisson N, Desguerre I, Charbit M, Benoist JF, Dupic L, Aigrain Y, Blanc T, Salomon R, Rabier D, Guest G, de Lonlay P, Niaudet P.

Mol Genet Metab. 2013 Sep-Oct;110(1-2):106-10. doi: 10.1016/j.ymgme.2013.05.001. Epub 2013 May 14.

PMID:
23751327
20.

Lung manifestations in MPO-ANCA associated vasculitides in children.

Ben Ameur S, Niaudet P, Baudouin V, Le Bourgeois M, Houdouin V, Delacourt C, Hadchouel A.

Pediatr Pulmonol. 2014 Mar;49(3):285-90. doi: 10.1002/ppul.22793. Epub 2013 Mar 26.

PMID:
23532899
21.

Genetics and outcome of atypical hemolytic uremic syndrome: a nationwide French series comparing children and adults.

Fremeaux-Bacchi V, Fakhouri F, Garnier A, Bienaimé F, Dragon-Durey MA, Ngo S, Moulin B, Servais A, Provot F, Rostaing L, Burtey S, Niaudet P, Deschênes G, Lebranchu Y, Zuber J, Loirat C.

Clin J Am Soc Nephrol. 2013 Apr;8(4):554-62. doi: 10.2215/CJN.04760512. Epub 2013 Jan 10.

22.

[Renal involvement in mitochondrial cytopathies].

Niaudet P.

Nephrol Ther. 2013 Apr;9(2):116-24. doi: 10.1016/j.nephro.2012.10.004. Epub 2012 Nov 26. French.

PMID:
23196040
23.

[Children and adolescents with ESRD].

Harambat J, Macher MA, Niaudet P, Couchoud C.

Nephrol Ther. 2012 Sep;8 Suppl 1:S149-59. doi: 10.1016/S1769-7255(12)70032-9. French. No abstract available.

PMID:
23121925
24.

Timing and outcome of renal replacement therapy in patients with congenital malformations of the kidney and urinary tract.

Wühl E, van Stralen KJ, Verrina E, Bjerre A, Wanner C, Heaf JG, Zurriaga O, Hoitsma A, Niaudet P, Palsson R, Ravani P, Jager KJ, Schaefer F.

Clin J Am Soc Nephrol. 2013 Jan;8(1):67-74. doi: 10.2215/CJN.03310412. Epub 2012 Oct 18.

25.

Eculizumab for atypical hemolytic uremic syndrome recurrence in renal transplantation.

Zuber J, Le Quintrec M, Krid S, Bertoye C, Gueutin V, Lahoche A, Heyne N, Ardissino G, Chatelet V, Noël LH, Hourmant M, Niaudet P, Frémeaux-Bacchi V, Rondeau E, Legendre C, Loirat C; French Study Group for Atypical HUS.

Am J Transplant. 2012 Dec;12(12):3337-54. doi: 10.1111/j.1600-6143.2012.04252.x. Epub 2012 Sep 7.

26.

Lupus anticoagulant-hypoprothrombinemia syndrome: report of 8 cases and review of the literature.

Mazodier K, Arnaud L, Mathian A, Costedoat-Chalumeau N, Haroche J, Frances C, Harlé JR, Pernod G, Lespessailles E, Gaudin P, Charlanne H, Hachulla E, Niaudet P, Piette JC, Amoura Z.

Medicine (Baltimore). 2012 Sep;91(5):251-60. Review.

27.

Overall neutralization of complement factor H by autoantibodies in the acute phase of the autoimmune form of atypical hemolytic uremic syndrome.

Blanc C, Roumenina LT, Ashraf Y, Hyvärinen S, Sethi SK, Ranchin B, Niaudet P, Loirat C, Gulati A, Bagga A, Fridman WH, Sautès-Fridman C, Jokiranta TS, Frémeaux-Bacchi V, Dragon-Durey MA.

J Immunol. 2012 Oct 1;189(7):3528-37. Epub 2012 Aug 24.

28.

Renal function and histology in children after small bowel transplantation.

Boyer O, Noto C, De Serre NP, Gubler MC, Dechaux M, Goulet O, Niaudet P, Lacaille F.

Pediatr Transplant. 2013 Feb;17(1):65-72. doi: 10.1111/j.1399-3046.2012.01767.x. Epub 2012 Aug 9.

PMID:
22882667
29.

Cystinosin is a melanosomal protein that regulates melanin synthesis.

Chiaverini C, Sillard L, Flori E, Ito S, Briganti S, Wakamatsu K, Fontas E, Berard E, Cailliez M, Cochat P, Foulard M, Guest G, Niaudet P, Picardo M, Bernard FX, Antignac C, Ortonne JP, Ballotti R.

FASEB J. 2012 Sep;26(9):3779-89. doi: 10.1096/fj.11-201376. Epub 2012 May 30.

PMID:
22649030
30.

A randomized controlled crossover trial with delayed-release cysteamine bitartrate in nephropathic cystinosis: effectiveness on white blood cell cystine levels and comparison of safety.

Langman CB, Greenbaum LA, Sarwal M, Grimm P, Niaudet P, Deschênes G, Cornelissen E, Morin D, Cochat P, Matossian D, Gaillard S, Bagger MJ, Rioux P.

Clin J Am Soc Nephrol. 2012 Jul;7(7):1112-20. doi: 10.2215/CJN.12321211. Epub 2012 May 3. Erratum in: Clin J Am Soc Nephrol. 2013 Mar 7;8(3):468.

31.

Pediatric nephrology.

Fischbach M, Niaudet P, Schaefer F, Rees L.

Int J Nephrol. 2012;2012:416749. doi: 10.1155/2012/416749. Epub 2012 Mar 22. No abstract available.

32.

Nephrotic syndrome in Kawasaki disease: a report of three cases.

Krug P, Boyer O, Balzamo E, Sidi D, Lehnert A, Niaudet P.

Pediatr Nephrol. 2012 Sep;27(9):1547-50. doi: 10.1007/s00467-012-2172-2. Epub 2012 Apr 24.

PMID:
22527534
33.

Renal transplantation under prophylactic eculizumab in atypical hemolytic uremic syndrome with CFH/CFHR1 hybrid protein.

Krid S, Roumenina LT, Beury D, Charbit M, Boyer O, Frémeaux-Bacchi V, Niaudet P.

Am J Transplant. 2012 Jul;12(7):1938-44. doi: 10.1111/j.1600-6143.2012.04051.x. Epub 2012 Apr 11.

34.

Acquired and genetic complement abnormalities play a critical role in dense deposit disease and other C3 glomerulopathies.

Servais A, Noël LH, Roumenina LT, Le Quintrec M, Ngo S, Dragon-Durey MA, Macher MA, Zuber J, Karras A, Provot F, Moulin B, Grünfeld JP, Niaudet P, Lesavre P, Frémeaux-Bacchi V.

Kidney Int. 2012 Aug;82(4):454-64. doi: 10.1038/ki.2012.63. Epub 2012 Mar 28.

35.

KLHL3 mutations cause familial hyperkalemic hypertension by impairing ion transport in the distal nephron.

Louis-Dit-Picard H, Barc J, Trujillano D, Miserey-Lenkei S, Bouatia-Naji N, Pylypenko O, Beaurain G, Bonnefond A, Sand O, Simian C, Vidal-Petiot E, Soukaseum C, Mandet C, Broux F, Chabre O, Delahousse M, Esnault V, Fiquet B, Houillier P, Bagnis CI, Koenig J, Konrad M, Landais P, Mourani C, Niaudet P, Probst V, Thauvin C, Unwin RJ, Soroka SD, Ehret G, Ossowski S, Caulfield M; International Consortium for Blood Pressure (ICBP), Bruneval P, Estivill X, Froguel P, Hadchouel J, Schott JJ, Jeunemaitre X.

Nat Genet. 2012 Mar 11;44(4):456-60, S1-3. doi: 10.1038/ng.2218. Erratum in: Nat Genet. 2012;44(5):609.

PMID:
22406640
36.

Pediatric en bloc kidney transplantation into pediatric recipients: the French experience.

Afanetti M, Niaudet P, Niel O, Saint Faust M, Cochat P, Berard E.

Pediatr Transplant. 2012 Mar;16(2):183-6. doi: 10.1111/j.1399-3046.2012.01654.x.

PMID:
22360402
37.

Population pharmacokinetics and pharmacodynamics of cysteamine in nephropathic cystinosis patients.

Bouazza N, Tréluyer JM, Ottolenghi C, Urien S, Deschenes G, Ricquier D, Niaudet P, Chadefaux-Vekemans B.

Orphanet J Rare Dis. 2011 Dec 23;6:86. doi: 10.1186/1750-1172-6-86.

38.

ANCA-associated glomerulonephritis in systemic-onset juvenile idiopathic arthritis.

Belot A, Bader-Meunier B, Niaudet P, Salomon R, Prieur AM, Noel LH, Quartier P.

Am J Kidney Dis. 2012 Mar;59(3):439-43. doi: 10.1053/j.ajkd.2011.11.002. Epub 2011 Dec 20.

PMID:
22189036
39.

Early angiotensin-converting enzyme inhibition in Alport syndrome delays renal failure and improves life expectancy.

Gross O, Licht C, Anders HJ, Hoppe B, Beck B, Tönshoff B, Höcker B, Wygoda S, Ehrich JH, Pape L, Konrad M, Rascher W, Dötsch J, Müller-Wiefel DE, Hoyer P; Study Group Members of the Gesellschaft für Pädiatrische Nephrologie, Knebelmann B, Pirson Y, Grunfeld JP, Niaudet P, Cochat P, Heidet L, Lebbah S, Torra R, Friede T, Lange K, Müller GA, Weber M.

Kidney Int. 2012 Mar;81(5):494-501. doi: 10.1038/ki.2011.407. Epub 2011 Dec 14.

40.

Intra- and postoperative adverse events in children with nephrotic syndrome requiring surgery under general anesthesia.

Greff B, Faivre J, Carli PA, Niaudet P, Orliaguet GA.

Paediatr Anaesth. 2012 Mar;22(3):244-9. doi: 10.1111/j.1460-9592.2011.03750.x. Epub 2011 Dec 6.

PMID:
22142331
41.

[Immunosuppressive treatment].

Niaudet P.

Nephrol Ther. 2011 Dec;7(7):592-8. doi: 10.1016/j.nephro.2011.11.003. French.

PMID:
22118788
42.

In vivo reflectance confocal microscopy of the skin: a noninvasive means of assessing body cystine accumulation in infantile cystinosis.

Chiavérini C, Kang HY, Sillard L, Berard E, Niaudet P, Guest G, Cailliez M, Bahadoran P, Lacour JP, Ballotti R, Ortonne JP.

J Am Acad Dermatol. 2013 Apr;68(4):e111-e116. doi: 10.1016/j.jaad.2011.08.010. Epub 2011 Oct 2.

PMID:
21963264
43.

Mycophenolate mofetil for steroid-dependent nephrotic syndrome: a phase II Bayesian trial.

Baudouin V, Alberti C, Lapeyraque AL, Bensman A, André JL, Broux F, Cailliez M, Decramer S, Niaudet P, Deschênes G, Jacqz-Aigrain E, Loirat C.

Pediatr Nephrol. 2012 Mar;27(3):389-96. doi: 10.1007/s00467-011-2006-7. Epub 2011 Sep 28.

PMID:
21947272
44.

Cysteamine therapy delays the progression of nephropathic cystinosis in late adolescents and adults.

Brodin-Sartorius A, Tête MJ, Niaudet P, Antignac C, Guest G, Ottolenghi C, Charbit M, Moyse D, Legendre C, Lesavre P, Cochat P, Servais A.

Kidney Int. 2012 Jan;81(2):179-89. doi: 10.1038/ki.2011.277. Epub 2011 Sep 7.

45.

Hemolytic uremic syndrome: new developments in pathogenesis and treatment.

Boyer O, Niaudet P.

Int J Nephrol. 2011;2011:908407. doi: 10.4061/2011/908407. Epub 2011 Aug 17.

46.

Papillary stones with Randall's plaques in children: clinicobiological features and outcome.

Bouchireb K, Boyer O, Pietrement C, Nivet H, Martelli H, Dunand O, Nobili F, Sylvie GL, Niaudet P, Salomon R, Daudon M.

Nephrol Dial Transplant. 2012 Apr;27(4):1529-34. doi: 10.1093/ndt/gfr439. Epub 2011 Aug 3. No abstract available.

PMID:
21813830
47.

Early-childhood membranous nephropathy due to cationic bovine serum albumin.

Debiec H, Lefeu F, Kemper MJ, Niaudet P, Deschênes G, Remuzzi G, Ulinski T, Ronco P.

N Engl J Med. 2011 Jun 2;364(22):2101-10. doi: 10.1056/NEJMoa1013792. Erratum in: N Engl J Med. 2014 Feb 27;370(9):886. N Engl J Med. 2011 Aug 4;365(5):477.

48.

Eculizumab in severe Shiga-toxin-associated HUS.

Lapeyraque AL, Malina M, Fremeaux-Bacchi V, Boppel T, Kirschfink M, Oualha M, Proulx F, Clermont MJ, Le Deist F, Niaudet P, Schaefer F.

N Engl J Med. 2011 Jun 30;364(26):2561-3. doi: 10.1056/NEJMc1100859. Epub 2011 May 25. No abstract available.

PMID:
21612462
49.

Efficacy and safety of Oxalobacter formigenes to reduce urinary oxalate in primary hyperoxaluria.

Hoppe B, Groothoff JW, Hulton SA, Cochat P, Niaudet P, Kemper MJ, Deschênes G, Unwin R, Milliner D.

Nephrol Dial Transplant. 2011 Nov;26(11):3609-15. doi: 10.1093/ndt/gfr107. Epub 2011 Apr 2.

PMID:
21460356
50.

Clinical features of anti-factor H autoantibody-associated hemolytic uremic syndrome.

Dragon-Durey MA, Sethi SK, Bagga A, Blanc C, Blouin J, Ranchin B, André JL, Takagi N, Cheong HI, Hari P, Le Quintrec M, Niaudet P, Loirat C, Fridman WH, Frémeaux-Bacchi V.

J Am Soc Nephrol. 2010 Dec;21(12):2180-7. doi: 10.1681/ASN.2010030315. Epub 2010 Nov 4.

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