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Items: 1 to 50 of 116

1.

Authors' response: Letter to the Editor 'Comparison of lung clearance index determined by washout of N2 and SF6 in infants and preschool children with cystic fibrosis'.

Stahl M, Joachim C, Wielpütz MO, Mall MA.

J Cyst Fibros. 2019 Feb 6. pii: S1569-1993(19)30020-7. doi: 10.1016/j.jcf.2019.01.016. [Epub ahead of print] No abstract available.

PMID:
30738803
2.

Targeting of Cathepsin S Reduces Cystic Fibrosis-like Lung Disease.

Small DM, Brown RR, Doherty DF, Abladey A, Zhou-Suckow Z, Delaney RJ, Kerrigan L, Dougan CM, Borensztajn KS, Holsinger L, Booth R, Scott CJ, López-Campos G, Elborn JS, Mall MA, Weldon S, Taggart CC.

Eur Respir J. 2019 Jan 17. pii: 1801523. doi: 10.1183/13993003.01523-2018. [Epub ahead of print]

PMID:
30655278
3.

Antisense oligonucleotide eluforsen improves CFTR function in F508del cystic fibrosis.

Sermet-Gaudelus I, Clancy JP, Nichols DP, Nick JA, De Boeck K, Solomon GM, Mall MA, Bolognese J, Bouisset F, den Hollander W, Paquette-Lamontagne N, Tomkinson N, Henig N, Elborn JS, Rowe SM.

J Cyst Fibros. 2018 Nov 19. pii: S1569-1993(18)30914-7. doi: 10.1016/j.jcf.2018.10.015. [Epub ahead of print]

4.

Emerging Concepts and Therapies for Mucoobstructive Lung Disease.

Mall MA, Danahay H, Boucher RC.

Ann Am Thorac Soc. 2018 Nov;15(Supplement_3):S216-S226. doi: 10.1513/AnnalsATS.201806-368AW.

PMID:
30431343
5.

Comparison of lung clearance index determined by washout of N2 and SF6 in infants and preschool children with cystic fibrosis.

Stahl M, Joachim C, Wielpütz MO, Mall MA.

J Cyst Fibros. 2018 Nov 9. pii: S1569-1993(18)30929-9. doi: 10.1016/j.jcf.2018.11.001. [Epub ahead of print]

PMID:
30420236
6.

Preventive Inhalation of Hypertonic Saline in Infants with Cystic Fibrosis (PRESIS): A Randomized, Double-Blind, Controlled Study.

Stahl M, Wielpütz MO, Ricklefs I, Dopfer C, Barth S, Schlegtendal A, Graeber SY, Sommerburg O, Diekmann G, Hüsing J, Koerner-Rettberg C, Nährlich L, Dittrich AM, Kopp MV, Mall MA.

Am J Respir Crit Care Med. 2018 Nov 9. doi: 10.1164/rccm.201807-1203OC. [Epub ahead of print]

PMID:
30409023
7.

VX-659-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles.

Davies JC, Moskowitz SM, Brown C, Horsley A, Mall MA, McKone EF, Plant BJ, Prais D, Ramsey BW, Taylor-Cousar JL, Tullis E, Uluer A, McKee CM, Robertson S, Shilling RA, Simard C, Van Goor F, Waltz D, Xuan F, Young T, Rowe SM; VX16-659-101 Study Group.

N Engl J Med. 2018 Oct 25;379(17):1599-1611. doi: 10.1056/NEJMoa1807119. Epub 2018 Oct 18.

PMID:
30334693
8.

VX-445-Tezacaftor-Ivacaftor in Patients with Cystic Fibrosis and One or Two Phe508del Alleles.

Keating D, Marigowda G, Burr L, Daines C, Mall MA, McKone EF, Ramsey BW, Rowe SM, Sass LA, Tullis E, McKee CM, Moskowitz SM, Robertson S, Savage J, Simard C, Van Goor F, Waltz D, Xuan F, Young T, Taylor-Cousar JL; VX16-445-001 Study Group.

N Engl J Med. 2018 Oct 25;379(17):1612-1620. doi: 10.1056/NEJMoa1807120. Epub 2018 Oct 18.

PMID:
30334692
9.

Role of the SLC26A9 Chloride Channel as Disease Modifier and Potential Therapeutic Target in Cystic Fibrosis.

Balázs A, Mall MA.

Front Pharmacol. 2018 Oct 1;9:1112. doi: 10.3389/fphar.2018.01112. eCollection 2018. Review.

10.

Assessment of Suspected Vascular Rings and Slings and/or Airway Pathologies Using Magnetic Resonance Imaging Rather Than Computed Tomography.

Sommburg O, Helling-Bakki A, Alrajab A, Schenk JP, Springer W, Mall MA, Loukanov T, Eichhorn JG.

Respiration. 2019;97(2):108-118. doi: 10.1159/000492080. Epub 2018 Oct 5.

PMID:
30293066
11.

Elastase Exocytosis by Airway Neutrophils Associates with Early Lung Damage in Cystic Fibrosis Children.

Margaroli C, Garratt LW, Horati H, Dittrich AS, Rosenow T, Montgomery ST, Frey DL, Brown MR, Schultz C, Guglani L, Kicic A, Peng L, Scholte BJ, Mall MA, Janssens HM, Stick SM, Tirouvanziam R; AREST-CF, and IMPEDE-CF.

Am J Respir Crit Care Med. 2018 Oct 3. doi: 10.1164/rccm.201803-0442OC. [Epub ahead of print]

PMID:
30281324
12.

Ductal Mucus Obstruction and Reduced Fluid Secretion Are Early Defects in Chronic Pancreatitis.

Balázs A, Balla Z, Kui B, Maléth J, Rakonczay Z Jr, Duerr J, Zhou-Suckow Z, Schatterny J, Sendler M, Mayerle J, Kühn JP, Tiszlavicz L, Mall MA, Hegyi P.

Front Physiol. 2018 May 29;9:632. doi: 10.3389/fphys.2018.00632. eCollection 2018.

13.

Interleukin-1 is associated with inflammation and structural lung disease in young children with cystic fibrosis.

Montgomery ST, Dittrich AS, Garratt LW, Turkovic L, Frey DL, Stick SM, Mall MA, Kicic A; AREST CF.

J Cyst Fibros. 2018 Nov;17(6):715-722. doi: 10.1016/j.jcf.2018.05.006. Epub 2018 Jun 6.

PMID:
29884450
14.

Expression and function of Anoctamin 1/TMEM16A calcium-activated chloride channels in airways of in vivo mouse models for cystic fibrosis research.

Hahn A, Salomon JJ, Leitz D, Feigenbutz D, Korsch L, Lisewski I, Schrimpf K, Millar-Büchner P, Mall MA, Frings S, Möhrlen F.

Pflugers Arch. 2018 Sep;470(9):1335-1348. doi: 10.1007/s00424-018-2160-x. Epub 2018 Jun 2.

PMID:
29860639
15.

Multicentre standardisation of chest MRI as radiation-free outcome measure of lung disease in young children with cystic fibrosis.

Wielpütz MO, von Stackelberg O, Stahl M, Jobst BJ, Eichinger M, Puderbach MU, Nährlich L, Barth S, Schneider C, Kopp MV, Ricklefs I, Buchholz M, Tümmler B, Dopfer C, Vogel-Claussen J, Kauczor HU, Mall MA.

J Cyst Fibros. 2018 Jul;17(4):518-527. doi: 10.1016/j.jcf.2018.05.003. Epub 2018 May 25.

PMID:
29805050
16.

Ion Channel Modulators in Cystic Fibrosis.

Gentzsch M, Mall MA.

Chest. 2018 Aug;154(2):383-393. doi: 10.1016/j.chest.2018.04.036. Epub 2018 May 8. Review.

PMID:
29750923
17.

Validation of automated lobe segmentation on paired inspiratory-expiratory chest CT in 8-14 year-old children with cystic fibrosis.

Konietzke P, Weinheimer O, Wielpütz MO, Savage D, Ziyeh T, Tu C, Newman B, Galbán CJ, Mall MA, Kauczor HU, Robinson TE.

PLoS One. 2018 Apr 9;13(4):e0194557. doi: 10.1371/journal.pone.0194557. eCollection 2018.

18.

Non-contrast enhanced magnetic resonance imaging detects mosaic signal intensity in early cystic fibrosis lung disease.

Leutz-Schmidt P, Stahl M, Sommerburg O, Eichinger M, Puderbach MU, Schenk JP, Alrajab A, Triphan SMF, Kauczor HU, Mall MA, Wielpütz MO.

Eur J Radiol. 2018 Apr;101:178-183. doi: 10.1016/j.ejrad.2018.02.023. Epub 2018 Feb 21.

PMID:
29571794
19.

Elastase activity on sputum neutrophils correlates with severity of lung disease in cystic fibrosis.

Dittrich AS, Kühbandner I, Gehrig S, Rickert-Zacharias V, Twigg M, Wege S, Taggart CC, Herth F, Schultz C, Mall MA.

Eur Respir J. 2018 Mar 29;51(3). pii: 1701910. doi: 10.1183/13993003.01910-2017. Print 2018 Mar.

PMID:
29545279
20.

One time quantitative PCR detection of Pseudomonas aeruginosa to discriminate intermittent from chronic infection in cystic fibrosis.

Boutin S, Weitnauer M, Hassel S, Graeber SY, Stahl M, Dittrich AS, Mall MA, Dalpke AH.

J Cyst Fibros. 2018 May;17(3):348-355. doi: 10.1016/j.jcf.2017.12.007. Epub 2018 Jan 12.

PMID:
29336943
21.

Effects of Lumacaftor-Ivacaftor Therapy on Cystic Fibrosis Transmembrane Conductance Regulator Function in Phe508del Homozygous Patients with Cystic Fibrosis.

Graeber SY, Dopfer C, Naehrlich L, Gyulumyan L, Scheuermann H, Hirtz S, Wege S, Mairbäurl H, Dorda M, Hyde R, Bagheri-Hanson A, Rueckes-Nilges C, Fischer S, Mall MA, Tümmler B.

Am J Respir Crit Care Med. 2018 Jun 1;197(11):1433-1442. doi: 10.1164/rccm.201710-1983OC.

PMID:
29327948
22.

Mucopurulent Triggering of the Airway Epithelium. Implications in Health and Cystic Fibrosis.

Balázs A, Mall MA.

Am J Respir Crit Care Med. 2018 Feb 15;197(4):418-420. doi: 10.1164/rccm.201712-2554ED. No abstract available.

PMID:
29298399
23.

An informative intragenic microsatellite marker suggests the IL-1 receptor as a genetic modifier in cystic fibrosis.

Stanke F, Hector A, Hedtfeld S, Hartl D, Griese M, Tümmler B, Mall MA.

Eur Respir J. 2017 Dec 28;50(6). pii: 1700426. doi: 10.1183/13993003.00426-2017. Print 2017 Dec. No abstract available.

PMID:
29284683
24.

Cystic fibrosis research topics featured at the 14th ECFS Basic Science Conference: Chairman's summary.

Mall MA, Hwang TC, Braakman I.

J Cyst Fibros. 2018 Mar;17(2S):S1-S4. doi: 10.1016/j.jcf.2017.11.008. Epub 2017 Dec 9. Review.

PMID:
29229473
25.

Lung disease phenotypes caused by overexpression of combinations of α-, β-, and γ-subunits of the epithelial sodium channel in mouse airways.

Livraghi-Butrico A, Wilkinson KJ, Volmer AS, Gilmore RC, Rogers TD, Caldwell RA, Burns KA, Esther CR Jr, Mall MA, Boucher RC, O'Neal WK, Grubb BR.

Am J Physiol Lung Cell Mol Physiol. 2018 Feb 1;314(2):L318-L331. doi: 10.1152/ajplung.00382.2017. Epub 2017 Oct 26.

26.

Bypassing CFTR dysfunction in cystic fibrosis with alternative pathways for anion transport.

Li H, Salomon JJ, Sheppard DN, Mall MA, Galietta LJ.

Curr Opin Pharmacol. 2017 Jun;34:91-97. doi: 10.1016/j.coph.2017.10.002. Epub 2017 Oct 21. Review.

PMID:
29065356
27.

Chronic but not intermittent infection with Pseudomonas aeruginosa is associated with global changes of the lung microbiome in cystic fibrosis.

Boutin S, Graeber SY, Stahl M, Dittrich AS, Mall MA, Dalpke AH.

Eur Respir J. 2017 Oct 5;50(4). pii: 1701086. doi: 10.1183/13993003.01086-2017. Print 2017 Oct. No abstract available.

PMID:
28982777
28.

Homeostatic nuclear RAGE-ATM interaction is essential for efficient DNA repair.

Kumar V, Fleming T, Terjung S, Gorzelanny C, Gebhardt C, Agrawal R, Mall MA, Ranzinger J, Zeier M, Madhusudhan T, Ranjan S, Isermann B, Liesz A, Deshpande D, Häring HU, Biswas SK, Reynolds PR, Hammes HP, Peperkok R, Angel P, Herzig S, Nawroth PP.

Nucleic Acids Res. 2017 Oct 13;45(18):10595-10613. doi: 10.1093/nar/gkx705.

29.

Three-center feasibility of lung clearance index in infants and preschool children with cystic fibrosis and other lung diseases.

Stahl M, Graeber SY, Joachim C, Barth S, Ricklefs I, Diekmann G, Kopp MV, Naehrlich L, Mall MA.

J Cyst Fibros. 2018 Mar;17(2):249-255. doi: 10.1016/j.jcf.2017.08.001. Epub 2017 Aug 12.

PMID:
28811149
30.

Reply to Verbanck and Vanderhelst: The Respective Roles of Lung Clearance Index and Magnetic Resonance Imaging in the Clinical Management of Patients with Cystic Fibrosis.

Stahl M, Wielpütz MO, Kauczor HU, Mall MA; all authors.

Am J Respir Crit Care Med. 2018 Feb 1;197(3):410-411. doi: 10.1164/rccm.201707-1367LE. No abstract available.

PMID:
28800247
31.

Cellular distribution and function of ion channels involved in transport processes in rat tracheal epithelium.

Hahn A, Faulhaber J, Srisawang L, Stortz A, Salomon JJ, Mall MA, Frings S, Möhrlen F.

Physiol Rep. 2017 Jun;5(12). pii: e13290. doi: 10.14814/phy2.13290.

32.

Disruption of the Hepcidin/Ferroportin Regulatory System Causes Pulmonary Iron Overload and Restrictive Lung Disease.

Neves J, Leitz D, Kraut S, Brandenberger C, Agrawal R, Weissmann N, Mühlfeld C, Mall MA, Altamura S, Muckenthaler MU.

EBioMedicine. 2017 Jun;20:230-239. doi: 10.1016/j.ebiom.2017.04.036. Epub 2017 Apr 29.

33.

Dephasing and diffusion on the alveolar surface.

Buschle LR, Kurz FT, Kampf T, Wagner WL, Duerr J, Stiller W, Konietzke P, Wünnemann F, Mall MA, Wielpütz MO, Schlemmer HP, Ziener CH.

Phys Rev E. 2017 Feb;95(2-1):022415. doi: 10.1103/PhysRevE.95.022415. Epub 2017 Feb 24.

PMID:
28297921
34.

Gene signature driving invasive mucinous adenocarcinoma of the lung.

Guo M, Tomoshige K, Meister M, Muley T, Fukazawa T, Tsuchiya T, Karns R, Warth A, Fink-Baldauf IM, Nagayasu T, Naomoto Y, Xu Y, Mall MA, Maeda Y.

EMBO Mol Med. 2017 Apr;9(4):462-481. doi: 10.15252/emmm.201606711.

35.

Protean proteases: at the cutting edge of lung diseases.

Taggart C, Mall MA, Lalmanach G, Cataldo D, Ludwig A, Janciauskiene S, Heath N, Meiners S, Overall CM, Schultz C, Turk B, Borensztajn KS.

Eur Respir J. 2017 Feb 8;49(2). pii: 1501200. doi: 10.1183/13993003.01200-2015. Print 2017 Feb. Review.

36.

Rare cause for hemoptysis in an adolescent: Bronchial capillary hemangioma.

Hämmerling S, Becker S, Mall MA.

Pediatr Pulmonol. 2017 Jul;52(7):E40-E42. doi: 10.1002/ppul.23673. Epub 2017 Feb 6.

PMID:
28165678
37.

Airway mucus, inflammation and remodeling: emerging links in the pathogenesis of chronic lung diseases.

Zhou-Suckow Z, Duerr J, Hagner M, Agrawal R, Mall MA.

Cell Tissue Res. 2017 Mar;367(3):537-550. doi: 10.1007/s00441-016-2562-z. Epub 2017 Jan 20. Review.

PMID:
28108847
38.

Hypoxia and sterile inflammation in cystic fibrosis airways: mechanisms and potential therapies.

Montgomery ST, Mall MA, Kicic A, Stick SM; AREST CF.

Eur Respir J. 2017 Jan 4;49(1). pii: 1600903. doi: 10.1183/13993003.00903-2016. Print 2017 Jan. Review.

39.

MRI accelerating progress in functional assessment of cystic fibrosis lung disease.

Wielpütz MO, Mall MA.

J Cyst Fibros. 2017 Mar;16(2):165-167. doi: 10.1016/j.jcf.2016.12.010. Epub 2016 Dec 20. No abstract available.

PMID:
28007460
40.

Current strategies for the long-term assessment, monitoring, and management of cystic fibrosis patients treated with CFTR modulator therapy.

Elborn JS, Davies J, Mall MA, Flume PA, Plant B.

J Cyst Fibros. 2017 Jan;16(1):163-164. doi: 10.1016/j.jcf.2016.11.009. Epub 2016 Dec 13.

41.

Impaired mucus clearance exacerbates allergen-induced type 2 airway inflammation in juvenile mice.

Fritzsching B, Hagner M, Dai L, Christochowitz S, Agrawal R, van Bodegom C, Schmidt S, Schatterny J, Hirtz S, Brown R, Goritzka M, Duerr J, Zhou-Suckow Z, Mall MA.

J Allergy Clin Immunol. 2017 Jul;140(1):190-203.e5. doi: 10.1016/j.jaci.2016.09.045. Epub 2016 Nov 16.

PMID:
27865862
42.

Early detection and sensitive monitoring of CF lung disease: Prospects of improved and safer imaging.

Mall MA, Stahl M, Graeber SY, Sommerburg O, Kauczor HU, Wielpütz MO.

Pediatr Pulmonol. 2016 Oct;51(S44):S49-S60. doi: 10.1002/ppul.23537. Review.

PMID:
27662104
43.

A Protease Inhibitor Tackles Epithelial Sodium Channels in Cystic Fibrosis.

Rickert-Zacharias V, Schultz C, Mall MA.

Am J Respir Crit Care Med. 2016 Sep 15;194(6):650-2. doi: 10.1164/rccm.201604-0781ED. No abstract available.

PMID:
27628073
44.

Comparison of Lung Clearance Index and Magnetic Resonance Imaging for Assessment of Lung Disease in Children with Cystic Fibrosis.

Stahl M, Wielpütz MO, Graeber SY, Joachim C, Sommerburg O, Kauczor HU, Puderbach M, Eichinger M, Mall MA.

Am J Respir Crit Care Med. 2017 Feb 1;195(3):349-359. doi: 10.1164/rccm.201604-0893OC.

PMID:
27575911
45.

Quantification of heterogeneity in lung disease with image-based pulmonary function testing.

Stahr CS, Samarage CR, Donnelley M, Farrow N, Morgan KS, Zosky G, Boucher RC, Siu KK, Mall MA, Parsons DW, Dubsky S, Fouras A.

Sci Rep. 2016 Jul 27;6:29438. doi: 10.1038/srep29438.

46.

A product of immunoreactive trypsinogen and pancreatitis-associated protein as second-tier strategy in cystic fibrosis newborn screening.

Weidler S, Stopsack KH, Hammermann J, Sommerburg O, Mall MA, Hoffmann GF, Kohlmüller D, Okun JG, Macek M Jr, Votava F, Krulišová V, Balaščaková M, Skalická V, Lee-Kirsch MA, Stopsack M.

J Cyst Fibros. 2016 Nov;15(6):752-758. doi: 10.1016/j.jcf.2016.07.002. Epub 2016 Jul 22.

47.

Neutrophil elastase and matrix metalloproteinase 12 in cystic fibrosis lung disease.

Wagner CJ, Schultz C, Mall MA.

Mol Cell Pediatr. 2016 Dec;3(1):25. doi: 10.1186/s40348-016-0053-7. Epub 2016 Jul 25. Review.

48.

Cigarette smoke causes acute airway disease and exacerbates chronic obstructive lung disease in neonatal mice.

Jia J, Conlon TM, Ballester Lopez C, Seimetz M, Bednorz M, Zhou-Suckow Z, Weissmann N, Eickelberg O, Mall MA, Yildirim AÖ.

Am J Physiol Lung Cell Mol Physiol. 2016 Sep 1;311(3):L602-10. doi: 10.1152/ajplung.00124.2016. Epub 2016 Jul 22.

49.

Unplugging Mucus in Cystic Fibrosis and Chronic Obstructive Pulmonary Disease.

Mall MA.

Ann Am Thorac Soc. 2016 Apr;13 Suppl 2:S177-85. doi: 10.1513/AnnalsATS.201509-641KV. Review.

PMID:
27115954
50.

Imaging of Cystic Fibrosis Lung Disease and Clinical Interpretation.

Wielpütz MO, Eichinger M, Biederer J, Wege S, Stahl M, Sommerburg O, Mall MA, Kauczor HU, Puderbach M.

Rofo. 2016 Sep;188(9):834-45. doi: 10.1055/s-0042-104936. Epub 2016 Apr 13. Review.

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