Format
Sort by
Items per page

Send to

Choose Destination

Search results

Items: 1 to 50 of 287

1.

Efficacy of the pharmacologic chaperone migalastat in a subset of male patients with the classic phenotype of Fabry disease and migalastat-amenable variants: data from the phase 3 randomized, multicenter, double-blind clinical trial and extension study.

Germain DP, Nicholls K, Giugliani R, Bichet DG, Hughes DA, Barisoni LM, Colvin RB, Jennette JC, Skuban N, Castelli JP, Benjamin E, Barth JA, Viereck C.

Genet Med. 2019 Feb 6. doi: 10.1038/s41436-019-0451-z. [Epub ahead of print]

PMID:
30723321
2.

Clinical Characteristics and Treatment Patterns of Children and Adults With IgA Nephropathy or IgA Vasculitis: Findings From the CureGN Study.

Selewski DT, Ambruzs JM, Appel GB, Bomback AS, Matar RB, Cai Y, Cattran DC, Chishti AS, D'Agati VD, D'Alessandri-Silva CJ, Gbadegesin RA, Hogan JJ, Iragorri S, Jennette JC, Julian BA, Khalid M, Lafayette RA, Liapis H, Lugani F, Mansfield SA, Mason S, Nachman PH, Nast CC, Nester CM, Noone DG, Novak J, O'Shaughnessy MM, Reich HN, Rheault MN, Rizk DV, Saha MK, Sanghani NS, Sperati CJ, Sreedharan R, Srivastava T, Swiatecka-Urban A, Twombley K, Vasylyeva TL, Weaver DJ, Yin H, Zee J, Falk RJ, Gharavi AG, Gillespie BW, Gipson DS, Greenbaum LA, Holzman LB, Kretzler M, Robinson BM, Smoyer WE, Flessner M, Guay-Woodford LM, Kiryluk K; CureGN Consortium.

Kidney Int Rep. 2018 Aug 3;3(6):1373-1384. doi: 10.1016/j.ekir.2018.07.021. eCollection 2018 Nov.

3.

CureGN Study Rationale, Design, and Methods: Establishing a Large Prospective Observational Study of Glomerular Disease.

Mariani LH, Bomback AS, Canetta PA, Flessner MF, Helmuth M, Hladunewich MA, Hogan JJ, Kiryluk K, Nachman PH, Nast CC, Rheault MN, Rizk DV, Trachtman H, Wenderfer SE, Bowers C, Hill-Callahan P, Marasa M, Poulton CJ, Revell A, Vento S, Barisoni L, Cattran D, D'Agati V, Jennette JC, Klein JB, Laurin LP, Twombley K, Falk RJ, Gharavi AG, Gillespie BW, Gipson DS, Greenbaum LA, Holzman LB, Kretzler M, Robinson B, Smoyer WE, Guay-Woodford LM; CureGN Consortium.

Am J Kidney Dis. 2019 Feb;73(2):218-229. doi: 10.1053/j.ajkd.2018.07.020. Epub 2018 Nov 9.

PMID:
30420158
4.

Pathogenesis of ANCA-Associated Pulmonary Vasculitis.

Alba MA, Jennette JC, Falk RJ.

Semin Respir Crit Care Med. 2018 Aug;39(4):413-424. doi: 10.1055/s-0038-1673386. Epub 2018 Nov 7.

PMID:
30404109
5.

Glomerulonephritis in Animal Models and Human Medicine: Discovery, Pathogenesis, and Diagnostics.

Cianciolo RE, Jennette JC.

Toxicol Pathol. 2018 Dec;46(8):898-903. doi: 10.1177/0192623318800714. Epub 2018 Oct 3.

PMID:
30278837
6.

Eosinophilic Granulomatosis with Polyangiitis: Clinical Pathology Conference and Review.

Wu EY, Hernandez ML, Jennette JC, Falk RJ.

J Allergy Clin Immunol Pract. 2018 Sep - Oct;6(5):1496-1504. doi: 10.1016/j.jaip.2018.07.001. Review.

PMID:
30197069
7.

Migalastat improves diarrhea in patients with Fabry disease: clinical-biomarker correlations from the phase 3 FACETS trial.

Schiffmann R, Bichet DG, Jovanovic A, Hughes DA, Giugliani R, Feldt-Rasmussen U, Shankar SP, Barisoni L, Colvin RB, Jennette JC, Holdbrook F, Mulberg A, Castelli JP, Skuban N, Barth JA, Nicholls K.

Orphanet J Rare Dis. 2018 Apr 27;13(1):68. doi: 10.1186/s13023-018-0813-7.

8.

Revision of the International Society of Nephrology/Renal Pathology Society classification for lupus nephritis: clarification of definitions, and modified National Institutes of Health activity and chronicity indices.

Bajema IM, Wilhelmus S, Alpers CE, Bruijn JA, Colvin RB, Cook HT, D'Agati VD, Ferrario F, Haas M, Jennette JC, Joh K, Nast CC, Noël LH, Rijnink EC, Roberts ISD, Seshan SV, Sethi S, Fogo AB.

Kidney Int. 2018 Apr;93(4):789-796. doi: 10.1016/j.kint.2017.11.023. Epub 2018 Feb 16.

PMID:
29459092
9.

Segmental Sclerosis and Extracapillary Hypercellularity Predict Diabetic ESRD.

Mottl AK, Gasim A, Schober FP, Hu Y, Dunnon AK, Hogan SL, Jennette JC.

J Am Soc Nephrol. 2018 Feb;29(2):694-703. doi: 10.1681/ASN.2017020192. Epub 2017 Nov 27.

10.

Predicting Outcome in Patients with Anti-GBM Glomerulonephritis.

van Daalen EE, Jennette JC, McAdoo SP, Pusey CD, Alba MA, Poulton CJ, Wolterbeek R, Nguyen TQ, Goldschmeding R, Alchi B, Griffiths M, de Zoysa JR, Vincent B, Bruijn JA, Bajema IM.

Clin J Am Soc Nephrol. 2018 Jan 6;13(1):63-72. doi: 10.2215/CJN.04290417. Epub 2017 Nov 21.

11.

Nomenclature of Cutaneous Vasculitis: Dermatologic Addendum to the 2012 Revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides.

Sunderkötter CH, Zelger B, Chen KR, Requena L, Piette W, Carlson JA, Dutz J, Lamprecht P, Mahr A, Aberer E, Werth VP, Wetter DA, Kawana S, Luqmani R, Frances C, Jorizzo J, Watts JR, Metze D, Caproni M, Alpsoy E, Callen JP, Fiorentino D, Merkel PA, Falk RJ, Jennette JC.

Arthritis Rheumatol. 2018 Feb;70(2):171-184. doi: 10.1002/art.40375. Review.

12.

Glomerular disease frequencies by race, sex and region: results from the International Kidney Biopsy Survey.

O'Shaughnessy MM, Hogan SL, Thompson BD, Coppo R, Fogo AB, Jennette JC.

Nephrol Dial Transplant. 2018 Apr 1;33(4):661-669. doi: 10.1093/ndt/gfx189.

PMID:
29106637
13.

Position paper: Revised 2017 international consensus on testing of ANCAs in granulomatosis with polyangiitis and microscopic polyangiitis.

Bossuyt X, Cohen Tervaert JW, Arimura Y, Blockmans D, Flores-Suárez LF, Guillevin L, Hellmich B, Jayne D, Jennette JC, Kallenberg CGM, Moiseev S, Novikov P, Radice A, Savige JA, Sinico RA, Specks U, van Paassen P, Zhao MH, Rasmussen N, Damoiseaux J, Csernok E.

Nat Rev Rheumatol. 2017 Nov;13(11):683-692. doi: 10.1038/nrrheum.2017.140. Epub 2017 Sep 14. Review.

PMID:
28905856
14.

ANCA Glomerulonephritis and Vasculitis.

Jennette JC, Nachman PH.

Clin J Am Soc Nephrol. 2017 Oct 6;12(10):1680-1691. doi: 10.2215/CJN.02500317. Epub 2017 Aug 25. Review.

15.

Temporal and Demographic Trends in Glomerular Disease Epidemiology in the Southeastern United States, 1986-2015.

O'Shaughnessy MM, Hogan SL, Poulton CJ, Falk RJ, Singh HK, Nickeleit V, Jennette JC.

Clin J Am Soc Nephrol. 2017 Apr 3;12(4):614-623. doi: 10.2215/CJN.10871016. Epub 2017 Mar 21.

16.

Clinical Features and Outcomes of a Racially Diverse Population with Fibrillary Glomerulonephritis.

Payan Schober F, Jobson MA, Poulton CJ, Singh HK, Nickeleit V, Falk RJ, Jennette JC, Nachman PH, Pendergraft Iii WF.

Am J Nephrol. 2017;45(3):248-256. doi: 10.1159/000455390. Epub 2017 Feb 4.

17.

Nicotinamide benefits both mothers and pups in two contrasting mouse models of preeclampsia.

Li F, Fushima T, Oyanagi G, Townley-Tilson HW, Sato E, Nakada H, Oe Y, Hagaman JR, Wilder J, Li M, Sekimoto A, Saigusa D, Sato H, Ito S, Jennette JC, Maeda N, Karumanchi SA, Smithies O, Takahashi N.

Proc Natl Acad Sci U S A. 2016 Nov 22;113(47):13450-13455. Epub 2016 Nov 7.

18.

Gene-Specific DNA Methylation Changes Predict Remission in Patients with ANCA-Associated Vasculitis.

Jones BE, Yang J, Muthigi A, Hogan SL, Hu Y, Starmer J, Henderson CD, Poulton CJ, Brant EJ, Pendergraft WF 3rd, Jennette JC, Falk RJ, Ciavatta DJ.

J Am Soc Nephrol. 2017 Apr;28(4):1175-1187. doi: 10.1681/ASN.2016050548. Epub 2016 Nov 7.

19.

Histone modification signature at myeloperoxidase and proteinase 3 in patients with anti-neutrophil cytoplasmic autoantibody-associated vasculitis.

Yang J, Ge H, Poulton CJ, Hogan SL, Hu Y, Jones BE, Henderson CD, McInnis EA, Pendergraft WF 3rd, Jennette JC, Falk RJ, Ciavatta DJ.

Clin Epigenetics. 2016 Aug 12;8:85. doi: 10.1186/s13148-016-0251-0. eCollection 2016.

20.

Overview of the Pathogenesis of ANCA-Associated Vasculitis.

Xiao H, Hu P, Falk RJ, Jennette JC.

Kidney Dis (Basel). 2016 Mar;1(4):205-15. doi: 10.1159/000442323. Epub 2015 Dec 3. Review.

21.

Renal Survival in Patients with Collapsing Compared with Not Otherwise Specified FSGS.

Laurin LP, Gasim AM, Derebail VK, McGregor JG, Kidd JM, Hogan SL, Poulton CJ, Detwiler RK, Jennette JC, Falk RJ, Nachman PH.

Clin J Am Soc Nephrol. 2016 Oct 7;11(10):1752-1759. doi: 10.2215/CJN.13091215. Epub 2016 Jul 21.

22.

Treatment with Glucocorticoids or Calcineurin Inhibitors in Primary FSGS.

Laurin LP, Gasim AM, Poulton CJ, Hogan SL, Jennette JC, Falk RJ, Foster BJ, Nachman PH.

Clin J Am Soc Nephrol. 2016 Mar 7;11(3):386-94. doi: 10.2215/CJN.07110615. Epub 2016 Feb 16.

23.

High Elmo1 expression aggravates and low Elmo1 expression prevents diabetic nephropathy.

Hathaway CK, Chang AS, Grant R, Kim HS, Madden VJ, Bagnell CR Jr, Jennette JC, Smithies O, Kakoki M.

Proc Natl Acad Sci U S A. 2016 Feb 23;113(8):2218-22. doi: 10.1073/pnas.1600511113. Epub 2016 Feb 8.

24.

Complete Remission in the Nephrotic Syndrome Study Network.

Gipson DS, Troost JP, Lafayette RA, Hladunewich MA, Trachtman H, Gadegbeku CA, Sedor JR, Holzman LB, Moxey-Mims MM, Perumal K, Kaskel FJ, Nelson PJ, Tuttle KR, Bagnasco SM, Hogan MC, Dell KM, Appel GB, Lieske JC, Ilori TO, Sethna CB, Fervenza FC, Hogan SL, Nachman PH, Rosenberg AZ, Greenbaum LA, Meyers KE, Hewitt SM, Choi MJ, Kopp JB, Zhdanova O, Hodgin JB, Johnstone DB, Adler SG, Avila-Casado C, Neu AM, Hingorani SR, Lemley KV, Nast CC, Brady TM, Barisoni-Thomas L, Fornoni A, Jennette JC, Cattran DC, Palmer MB, Gibson KL, Reich HN, Mokrzycki MH, Sambandam KK, Zilleruelo GE, Licht C, Sampson MG, Song P, Mariani LH, Kretzler M.

Clin J Am Soc Nephrol. 2016 Jan 7;11(1):81-9. doi: 10.2215/CJN.02560315. Epub 2015 Dec 10.

25.

Mayo Clinic/Renal Pathology Society Consensus Report on Pathologic Classification, Diagnosis, and Reporting of GN.

Sethi S, Haas M, Markowitz GS, D'Agati VD, Rennke HG, Jennette JC, Bajema IM, Alpers CE, Chang A, Cornell LD, Cosio FG, Fogo AB, Glassock RJ, Hariharan S, Kambham N, Lager DJ, Leung N, Mengel M, Nath KA, Roberts IS, Rovin BH, Seshan SV, Smith RJ, Walker PD, Winearls CG, Appel GB, Alexander MP, Cattran DC, Casado CA, Cook HT, De Vriese AS, Radhakrishnan J, Racusen LC, Ronco P, Fervenza FC.

J Am Soc Nephrol. 2016 May;27(5):1278-87. doi: 10.1681/ASN.2015060612. Epub 2015 Nov 13.

26.

Randomized controlled trial of mycophenolate mofetil in children, adolescents, and adults with IgA nephropathy.

Hogg RJ, Bay RC, Jennette JC, Sibley R, Kumar S, Fervenza FC, Appel G, Cattran D, Fischer D, Hurley RM, Cerda J, Carter B, Jung B, Hernandez G, Gipson D, Wyatt RJ.

Am J Kidney Dis. 2015 Nov;66(5):783-91. doi: 10.1053/j.ajkd.2015.06.013. Epub 2015 Jul 21.

PMID:
26209543
27.

Eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA) Consensus Task Force recommendations for evaluation and management.

Groh M, Pagnoux C, Baldini C, Bel E, Bottero P, Cottin V, Dalhoff K, Dunogué B, Gross W, Holle J, Humbert M, Jayne D, Jennette JC, Lazor R, Mahr A, Merkel PA, Mouthon L, Sinico RA, Specks U, Vaglio A, Wechsler ME, Cordier JF, Guillevin L.

Eur J Intern Med. 2015 Sep;26(7):545-53. doi: 10.1016/j.ejim.2015.04.022. Epub 2015 May 9.

28.

Low TGFβ1 expression prevents and high expression exacerbates diabetic nephropathy in mice.

Hathaway CK, Gasim AM, Grant R, Chang AS, Kim HS, Madden VJ, Bagnell CR Jr, Jennette JC, Smithies O, Kakoki M.

Proc Natl Acad Sci U S A. 2015 May 5;112(18):5815-20. doi: 10.1073/pnas.1504777112. Epub 2015 Apr 20.

29.

Autoimmunity to the alpha 3 chain of type IV collagen in glomerulonephritis is triggered by 'autoantigen complementarity'.

Reynolds J, Preston GA, Pressler BM, Hewins P, Brown M, Roth A, Alderman E, Bunch D, Jennette JC, Cook HT, Falk RJ, Pusey CD.

J Autoimmun. 2015 May;59:8-18. doi: 10.1016/j.jaut.2015.01.003. Epub 2015 Apr 2.

30.

Use of Activated Factor VII in Patients with Diffuse Alveolar Hemorrhage: A 10 Years Institutional Experience.

Pathak V, Kuhn J, Gabriel D, Barrow J, Jennette JC, Henke DC.

Lung. 2015 Jun;193(3):375-9. doi: 10.1007/s00408-015-9720-z. Epub 2015 Mar 24.

PMID:
25802198
31.

Palladin is upregulated in kidney disease and contributes to epithelial cell migration after injury.

Chang EH, Gasim AH, Kerber ML, Patel JB, Glaubiger SA, Falk RJ, Jennette JC, Otey CA.

Sci Rep. 2015 Jan 9;5:7695. doi: 10.1038/srep07695.

32.

ANCAs are also antimonocyte cytoplasmic autoantibodies.

Jennette JC, Falk RJ.

Clin J Am Soc Nephrol. 2015 Jan 7;10(1):4-6. doi: 10.2215/CJN.11501114. Epub 2014 Dec 16. No abstract available.

33.

Rare hereditary COL4A3/COL4A4 variants may be mistaken for familial focal segmental glomerulosclerosis.

Malone AF, Phelan PJ, Hall G, Cetincelik U, Homstad A, Alonso AS, Jiang R, Lindsey TB, Wu G, Sparks MA, Smith SR, Webb NJ, Kalra PA, Adeyemo AA, Shaw AS, Conlon PJ, Jennette JC, Howell DN, Winn MP, Gbadegesin RA.

Kidney Int. 2014 Dec;86(6):1253-9. doi: 10.1038/ki.2014.305. Epub 2014 Sep 17.

34.

Dysregulation of autoantigen genes in ANCA-associated vasculitis involves alternative transcripts and new protein synthesis.

McInnis EA, Badhwar AK, Muthigi A, Lardinois OM, Allred SC, Yang J, Free ME, Jennette JC, Preston GA, Falk RJ, Ciavatta DJ.

J Am Soc Nephrol. 2015 Feb;26(2):390-9. doi: 10.1681/ASN.2013101092. Epub 2014 Jul 24.

35.

Pathogenesis of antineutrophil cytoplasmic autoantibody-mediated disease.

Jennette JC, Falk RJ.

Nat Rev Rheumatol. 2014 Aug;10(8):463-73. doi: 10.1038/nrrheum.2014.103. Epub 2014 Jul 8. Review.

PMID:
25003769
36.

B cell-mediated pathogenesis of ANCA-mediated vasculitis.

Jennette JC, Falk RJ.

Semin Immunopathol. 2014 May;36(3):327-38. doi: 10.1007/s00281-014-0431-y. Epub 2014 Apr 29. Review.

37.

Predictors of treatment outcomes in ANCA-associated vasculitis with severe kidney failure.

Lee T, Gasim A, Derebail VK, Chung Y, McGregor JG, Lionaki S, Poulton CJ, Hogan SL, Jennette JC, Falk RJ, Nachman PH.

Clin J Am Soc Nephrol. 2014 May;9(5):905-13. doi: 10.2215/CJN.08290813. Epub 2014 Feb 27.

38.

C5a receptor (CD88) blockade protects against MPO-ANCA GN.

Xiao H, Dairaghi DJ, Powers JP, Ertl LS, Baumgart T, Wang Y, Seitz LC, Penfold ME, Gan L, Hu P, Lu B, Gerard NP, Gerard C, Schall TJ, Jaen JC, Falk RJ, Jennette JC.

J Am Soc Nephrol. 2014 Feb;25(2):225-31. doi: 10.1681/ASN.2013020143. Epub 2013 Oct 31.

39.

Overview of the 2012 revised International Chapel Hill Consensus Conference nomenclature of vasculitides.

Jennette JC.

Clin Exp Nephrol. 2013 Oct;17(5):603-606. doi: 10.1007/s10157-013-0869-6. Epub 2013 Sep 27.

40.

Patients with antineutrophil cytoplasmic antibody-associated vasculitis have defective Treg cell function exacerbated by the presence of a suppression-resistant effector cell population.

Free ME, Bunch DO, McGregor JA, Jones BE, Berg EA, Hogan SL, Hu Y, Preston GA, Jennette JC, Falk RJ, Su MA.

Arthritis Rheum. 2013 Jul;65(7):1922-33. doi: 10.1002/art.37959.

41.

Epitope specificity determines pathogenicity and detectability in ANCA-associated vasculitis.

Roth AJ, Ooi JD, Hess JJ, van Timmeren MM, Berg EA, Poulton CE, McGregor J, Burkart M, Hogan SL, Hu Y, Winnik W, Nachman PH, Stegeman CA, Niles J, Heeringa P, Kitching AR, Holdsworth S, Jennette JC, Preston GA, Falk RJ.

J Clin Invest. 2013 Apr;123(4):1773-83. doi: 10.1172/JCI65292. Epub 2013 Mar 15.

42.

L17. What can we expect from the revised Chapel Hill consensus conference nomenclature of vasculitis?

Jennette JC.

Presse Med. 2013 Apr;42(4 Pt 2):550-5. doi: 10.1016/j.lpm.2013.01.016. Epub 2013 Feb 26. Review. No abstract available.

PMID:
23453204
43.

Digital pathology evaluation in the multicenter Nephrotic Syndrome Study Network (NEPTUNE).

Barisoni L, Nast CC, Jennette JC, Hodgin JB, Herzenberg AM, Lemley KV, Conway CM, Kopp JB, Kretzler M, Lienczewski C, Avila-Casado C, Bagnasco S, Sethi S, Tomaszewski J, Gasim AH, Hewitt SM.

Clin J Am Soc Nephrol. 2013 Aug;8(8):1449-59. doi: 10.2215/CJN.08370812. Epub 2013 Feb 7.

44.

Genetically determined severity of anti-myeloperoxidase glomerulonephritis.

Xiao H, Ciavatta D, Aylor DL, Hu P, de Villena FP, Falk RJ, Jennette JC.

Am J Pathol. 2013 Apr;182(4):1219-26. doi: 10.1016/j.ajpath.2012.12.006. Epub 2013 Feb 4.

45.

Pathogenesis of antineutrophil cytoplasmic autoantibody-associated small-vessel vasculitis.

Jennette JC, Falk RJ, Hu P, Xiao H.

Annu Rev Pathol. 2013 Jan 24;8:139-60. doi: 10.1146/annurev-pathol-011811-132453. Review.

46.

Pathways to renal biopsy and diagnosis among patients with ANCA small-vessel vasculitis.

Poulton CJ, Nachman PH, Hu Y, McGregor JG, Jennette JC, Falk RJ, Hogan SL.

Clin Exp Rheumatol. 2013 Jan-Feb;31(1 Suppl 75):S32-7. Epub 2013 Jan 23.

47.

Association of histologic variants in FSGS clinical trial with presenting features and outcomes.

D'Agati VD, Alster JM, Jennette JC, Thomas DB, Pullman J, Savino DA, Cohen AH, Gipson DS, Gassman JJ, Radeva MK, Moxey-Mims MM, Friedman AL, Kaskel FJ, Trachtman H, Alpers CE, Fogo AB, Greene TH, Nast CC.

Clin J Am Soc Nephrol. 2013 Mar;8(3):399-406. doi: 10.2215/CJN.06100612. Epub 2012 Dec 6.

48.

2012 revised International Chapel Hill Consensus Conference Nomenclature of Vasculitides.

Jennette JC, Falk RJ, Bacon PA, Basu N, Cid MC, Ferrario F, Flores-Suarez LF, Gross WL, Guillevin L, Hagen EC, Hoffman GS, Jayne DR, Kallenberg CG, Lamprecht P, Langford CA, Luqmani RA, Mahr AD, Matteson EL, Merkel PA, Ozen S, Pusey CD, Rasmussen N, Rees AJ, Scott DG, Specks U, Stone JH, Takahashi K, Watts RA.

Arthritis Rheum. 2013 Jan;65(1):1-11. doi: 10.1002/art.37715. No abstract available.

49.

Classification of antineutrophil cytoplasmic autoantibody vasculitides: the role of antineutrophil cytoplasmic autoantibody specificity for myeloperoxidase or proteinase 3 in disease recognition and prognosis.

Lionaki S, Blyth ER, Hogan SL, Hu Y, Senior BA, Jennette CE, Nachman PH, Jennette JC, Falk RJ.

Arthritis Rheum. 2012 Oct;64(10):3452-62. doi: 10.1002/art.34562.

50.

High basal activity of the PTPN22 gain-of-function variant blunts leukocyte responsiveness negatively affecting IL-10 production in ANCA vasculitis.

Cao Y, Yang J, Colby K, Hogan SL, Hu Y, Jennette CE, Berg EA, Zhang Y, Jennette JC, Falk RJ, Preston GA.

PLoS One. 2012;7(8):e42783. doi: 10.1371/journal.pone.0042783. Epub 2012 Aug 3.

Supplemental Content

Loading ...
Support Center