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Lysosomal dysfunction and early glial activation are involved in the pathogenesis of spinocerebellar ataxia type 21 caused by mutant transmembrane protein 240.
Seki T, Sato M, Kibe Y, Ohta T, Oshima M, Konno A, Hirai H, Kurauchi Y, Hisatsune A, Katsuki H.
Neurobiol Dis. 2018 Sep 2;120:34-50. doi: 10.1016/j.nbd.2018.08.022. [Epub ahead of print]
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