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Items: 1 to 50 of 67

1.

Laminin-111 protein therapy enhances muscle regeneration and repair in the GRMD dog model of Duchenne muscular dystrophy.

Barraza-Flores P, Fontelonga TM, Wuebbles RD, Hermann HJ, Nunes AM, Kornegay JN, Burkin DJ.

Hum Mol Genet. 2019 Aug 15;28(16):2686-2695. doi: 10.1093/hmg/ddz086.

PMID:
31179490
2.

Sunitinib promotes myogenic regeneration and mitigates disease progression in the mdx mouse model of Duchenne muscular dystrophy.

Fontelonga TM, Jordan B, Nunes AM, Barraza-Flores P, Bolden N, Wuebbles RD, Griner LM, Hu X, Ferrer M, Marugan J, Southall N, Burkin DJ.

Hum Mol Genet. 2019 Jul 1;28(13):2120-2132. doi: 10.1093/hmg/ddz044.

PMID:
30806670
3.

Human Galectin-1 Improves Sarcolemma Stability and Muscle Vascularization in the mdx Mouse Model of Duchenne Muscular Dystrophy.

Wuebbles RD, Cruz V, Van Ry P, Barraza-Flores P, Brewer PD, Jones P, Burkin DJ.

Mol Ther Methods Clin Dev. 2019 Jan 22;13:145-153. doi: 10.1016/j.omtm.2019.01.004. eCollection 2019 Jun 14.

4.

Integrin α7: a major driver and therapeutic target for glioblastoma malignancy.

Nunes AM, Barraza-Flores P, Smith CR, Burkin DJ.

Stem Cell Investig. 2017 Dec 18;4:97. doi: 10.21037/sci.2017.12.01. eCollection 2017. No abstract available.

5.

ECM-Related Myopathies and Muscular Dystrophies: Pros and Cons of Protein Therapies.

Van Ry PM, Fontelonga TM, Barraza-Flores P, Sarathy A, Nunes AM, Burkin DJ.

Compr Physiol. 2017 Sep 12;7(4):1519-1536. doi: 10.1002/cphy.c150033. Review.

PMID:
28915335
6.

Improving Reproducibility of Phenotypic Assessments in the DyW Mouse Model of Laminin-α2 Related Congenital Muscular Dystrophy.

Willmann R, Gordish-Dressman H, Meinen S, Rüegg MA, Yu Q, Nagaraju K, Kumar A, Girgenrath M, Coffey CBM, Cruz V, Van Ry PM, Bogdanik L, Lutz C, Rutkowski A, Burkin DJ.

J Neuromuscul Dis. 2017;4(2):115-126. doi: 10.3233/JND-170217. Review.

7.

Evaluation of the behavioral characteristics of the mdx mouse model of duchenne muscular dystrophy through operant conditioning procedures.

Lewon M, Peters CM, Van Ry PM, Burkin DJ, Hunter KW, Hayes LJ.

Behav Processes. 2017 Sep;142:8-20. doi: 10.1016/j.beproc.2017.05.012. Epub 2017 May 19.

PMID:
28532665
8.

SU9516 Increases α7β1 Integrin and Ameliorates Disease Progression in the mdx Mouse Model of Duchenne Muscular Dystrophy.

Sarathy A, Wuebbles RD, Fontelonga TM, Tarchione AR, Mathews Griner LA, Heredia DJ, Nunes AM, Duan S, Brewer PD, Van Ry T, Hennig GW, Gould TW, Dulcey AE, Wang A, Xu X, Chen CZ, Hu X, Zheng W, Southall N, Ferrer M, Marugan J, Burkin DJ.

Mol Ther. 2017 Jun 7;25(6):1395-1407. doi: 10.1016/j.ymthe.2017.03.022. Epub 2017 Apr 5.

9.

Impaired fetal muscle development and JAK-STAT activation mark disease onset and progression in a mouse model for merosin-deficient congenital muscular dystrophy.

Nunes AM, Wuebbles RD, Sarathy A, Fontelonga TM, Deries M, Burkin DJ, Thorsteinsdóttir S.

Hum Mol Genet. 2017 Jun 1;26(11):2018-2033. doi: 10.1093/hmg/ddx083.

10.

PTRH2 gene mutation causes progressive congenital skeletal muscle pathology.

Doe J, Kaindl AM, Jijiwa M, de la Vega M, Hu H, Griffiths GS, Fontelonga TM, Barraza P, Cruz V, Van Ry P, Ramos JW, Burkin DJ, Matter ML.

Hum Mol Genet. 2017 Apr 15;26(8):1458-1464. doi: 10.1093/hmg/ddx048.

11.

Commentary: SU9516 increases α7β1 Integrin and Ameliorates Disease Progression in the mdx Mouse Model of Duchenne Muscular Dystrophy.

Sarathy A, Nunes AM, Fontelonga TM, Ogata TY, Burkin DJ.

J Rare Dis Res Treat. 2017;2(5):1-4. Epub 2017 Aug 29. No abstract available.

12.

Heart-specific overexpression of the human short CLC-3 chloride channel isoform limits myocardial ischemia-induced ERP and QT prolongation.

Yu Y, Ye L, Li YG, Burkin DJ, Duan DD.

Int J Cardiol. 2016 Jul 1;214:218-24. doi: 10.1016/j.ijcard.2016.03.191. Epub 2016 Mar 30.

13.

Mesothelioma cells breaking bad: loss of integrin α7 promotes cell motility and poor clinical outcomes in patients.

Burkin DJ, Fontelonga TM.

J Pathol. 2015 Nov;237(3):282-4. doi: 10.1002/path.4587. Epub 2015 Aug 26.

PMID:
26174987
14.

Galectin-1 Protein Therapy Prevents Pathology and Improves Muscle Function in the mdx Mouse Model of Duchenne Muscular Dystrophy.

Van Ry PM, Wuebbles RD, Key M, Burkin DJ.

Mol Ther. 2015 Aug;23(8):1285-1297. doi: 10.1038/mt.2015.105. Epub 2015 Jun 8.

15.

Bit-1 is an essential regulator of myogenic differentiation.

Griffiths GS, Doe J, Jijiwa M, Van Ry P, Cruz V, de la Vega M, Ramos JW, Burkin DJ, Matter ML.

J Cell Sci. 2015 May 1;128(9):1707-17. doi: 10.1242/jcs.158964. Epub 2015 Mar 13.

16.

Sarcospan integration into laminin-binding adhesion complexes that ameliorate muscular dystrophy requires utrophin and α7 integrin.

Marshall JL, Oh J, Chou E, Lee JA, Holmberg J, Burkin DJ, Crosbie-Watson RH.

Hum Mol Genet. 2015 Apr 1;24(7):2011-22. doi: 10.1093/hmg/ddu615. Epub 2014 Dec 11.

17.

Laminin-111 improves muscle repair in a mouse model of merosin-deficient congenital muscular dystrophy.

Van Ry PM, Minogue P, Hodges BL, Burkin DJ.

Hum Mol Genet. 2014 Jan 15;23(2):383-96. doi: 10.1093/hmg/ddt428. Epub 2013 Sep 5.

18.

Alpha 7 integrin preserves the function of the extensor digitorum longus muscle in dystrophin-null mice.

Hakim CH, Burkin DJ, Duan D.

J Appl Physiol (1985). 2013 Nov 1;115(9):1388-92. doi: 10.1152/japplphysiol.00602.2013. Epub 2013 Aug 29.

19.

Levels of α7 integrin and laminin-α2 are increased following prednisone treatment in the mdx mouse and GRMD dog models of Duchenne muscular dystrophy.

Wuebbles RD, Sarathy A, Kornegay JN, Burkin DJ.

Dis Model Mech. 2013 Sep;6(5):1175-84. doi: 10.1242/dmm.012211. Epub 2013 Jul 11.

20.

Report on the Myomatrix Conference April 22-24, 2012, University of Nevada, Reno, Nevada, USA.

Rutkowski A, Bönnemann C, Brown S, Thorsteinsdóttir S, Dominov J, Ruegg MA, Matter ML, Guttridge D, Crosbie-Watson RH, Kardon G, Nagaraju K, Girgenrath M, Burkin DJ.

Neuromuscul Disord. 2013 Feb;23(2):188-91. doi: 10.1016/j.nmd.2012.06.353. Epub 2012 Jul 15.

21.

Dystrophin and utrophin expression require sarcospan: loss of α7 integrin exacerbates a newly discovered muscle phenotype in sarcospan-null mice.

Marshall JL, Chou E, Oh J, Kwok A, Burkin DJ, Crosbie-Watson RH.

Hum Mol Genet. 2012 Oct 15;21(20):4378-93. Epub 2012 Jul 13.

22.

A molecular bandage for diseased muscle.

Burkin DJ, Wuebbles RD.

Sci Transl Med. 2012 Jun 20;4(139):139fs19. doi: 10.1126/scitranslmed.3004082.

PMID:
22723460
23.

Laminin-111 protein therapy reduces muscle pathology and improves viability of a mouse model of merosin-deficient congenital muscular dystrophy.

Rooney JE, Knapp JR, Hodges BL, Wuebbles RD, Burkin DJ.

Am J Pathol. 2012 Apr;180(4):1593-602. doi: 10.1016/j.ajpath.2011.12.019. Epub 2012 Feb 6.

24.

Activation of volume regulated chloride channels protects myocardium from ischemia/reperfusion damage in second-window ischemic preconditioning.

Bozeat ND, Xiang SY, Ye LL, Yao TY, Duan ML, Burkin DJ, Lamb FS, Duan DD.

Cell Physiol Biochem. 2011;28(6):1265-78. doi: 10.1159/000335858. Epub 2011 Dec 16.

25.

Transgenic overexpression of the α7 integrin reduces muscle pathology and improves viability in the dy(W) mouse model of merosin-deficient congenital muscular dystrophy type 1A.

Doe JA, Wuebbles RD, Allred ET, Rooney JE, Elorza M, Burkin DJ.

J Cell Sci. 2011 Jul 1;124(Pt 13):2287-97. doi: 10.1242/jcs.083311. Epub 2011 Jun 7.

26.

Activation of AKT signaling promotes cell growth and survival in α7β1 integrin-mediated alleviation of muscular dystrophy.

Boppart MD, Burkin DJ, Kaufman SJ.

Biochim Biophys Acta. 2011 Apr;1812(4):439-46. doi: 10.1016/j.bbadis.2011.01.002. Epub 2011 Jan 7.

27.

Myotendinous junction defects and reduced force transmission in mice that lack alpha7 integrin and utrophin.

Welser JV, Rooney JE, Cohen NC, Gurpur PB, Singer CA, Evans RA, Haines BA, Burkin DJ.

Am J Pathol. 2009 Oct;175(4):1545-54. doi: 10.2353/ajpath.2009.090052. Epub 2009 Sep 3.

28.

Cardiac-specific, inducible ClC-3 gene deletion eliminates native volume-sensitive chloride channels and produces myocardial hypertrophy in adult mice.

Xiong D, Heyman NS, Airey J, Zhang M, Singer CA, Rawat S, Ye L, Evans R, Burkin DJ, Tian H, McCloskey DT, Valencik M, Britton FC, Duan D, Hume JR.

J Mol Cell Cardiol. 2010 Jan;48(1):211-9. doi: 10.1016/j.yjmcc.2009.07.003. Epub 2009 Jul 15.

29.

Laminin-111 protein therapy prevents muscle disease in the mdx mouse model for Duchenne muscular dystrophy.

Rooney JE, Gurpur PB, Burkin DJ.

Proc Natl Acad Sci U S A. 2009 May 12;106(19):7991-6. doi: 10.1073/pnas.0811599106. Epub 2009 Apr 28. Erratum in: Proc Natl Acad Sci U S A. 2009 Sep 8;106(36):15514.

30.

Valproic acid activates the PI3K/Akt/mTOR pathway in muscle and ameliorates pathology in a mouse model of Duchenne muscular dystrophy.

Gurpur PB, Liu J, Burkin DJ, Kaufman SJ.

Am J Pathol. 2009 Mar;174(3):999-1008. doi: 10.2353/ajpath.2009.080537. Epub 2009 Jan 29.

31.

Laminin-111 restores regenerative capacity in a mouse model for alpha7 integrin congenital myopathy.

Rooney JE, Gurpur PB, Yablonka-Reuveni Z, Burkin DJ.

Am J Pathol. 2009 Jan;174(1):256-64. doi: 10.2353/ajpath.2009.080522. Epub 2008 Dec 12.

32.

Cardiac-specific overexpression of the human short CLC-3 chloride channel isoform in mice.

Xiong D, Wang GX, Burkin DJ, Yamboliev IA, Singer CA, Rawat S, Scowen P, Evans R, Ye L, Hatton WJ, Tian H, Keller PS, McCloskey DT, Duan D, Hume JR.

Clin Exp Pharmacol Physiol. 2009 Apr;36(4):386-93. doi: 10.1111/j.1440-1681.2008.05069.x. Epub 2008 Oct 15.

PMID:
18986326
33.

Exercise promotes alpha7 integrin gene transcription and protection of skeletal muscle.

Boppart MD, Volker SE, Alexander N, Burkin DJ, Kaufman SJ.

Am J Physiol Regul Integr Comp Physiol. 2008 Nov;295(5):R1623-30. doi: 10.1152/ajpregu.00089.2008. Epub 2008 Sep 10.

34.

Diagnosis and etiology of congenital muscular dystrophy.

Peat RA, Smith JM, Compton AG, Baker NL, Pace RA, Burkin DJ, Kaufman SJ, Lamandé SR, North KN.

Neurology. 2008 Jul 29;71(5):312-21. Epub 2007 Dec 26.

PMID:
18160674
35.
36.

Placental defects in alpha7 integrin null mice.

Welser JV, Lange ND, Flintoff-Dye N, Burkin HR, Burkin DJ.

Placenta. 2007 Nov-Dec;28(11-12):1219-28. Epub 2007 Sep 27.

37.

Loss of the alpha7 integrin promotes extracellular signal-regulated kinase activation and altered vascular remodeling.

Welser JV, Lange N, Singer CA, Elorza M, Scowen P, Keef KD, Gerthoffer WT, Burkin DJ.

Circ Res. 2007 Sep 28;101(7):672-81. Epub 2007 Aug 17.

PMID:
17704212
38.

Severe muscular dystrophy in mice that lack dystrophin and alpha7 integrin.

Rooney JE, Welser JV, Dechert MA, Flintoff-Dye NL, Kaufman SJ, Burkin DJ.

J Cell Sci. 2006 Jun 1;119(Pt 11):2185-95. Epub 2006 May 9.

39.

Alpha7beta1-integrin regulates mechanotransduction and prevents skeletal muscle injury.

Boppart MD, Burkin DJ, Kaufman SJ.

Am J Physiol Cell Physiol. 2006 Jun;290(6):C1660-5. Epub 2006 Jan 18.

40.

Role for the alpha7beta1 integrin in vascular development and integrity.

Flintoff-Dye NL, Welser J, Rooney J, Scowen P, Tamowski S, Hatton W, Burkin DJ.

Dev Dyn. 2005 Sep;234(1):11-21.

41.
42.

Enhanced expression of the alpha 7 beta 1 integrin reduces muscular dystrophy and restores viability in dystrophic mice.

Burkin DJ, Wallace GQ, Nicol KJ, Kaufman DJ, Kaufman SJ.

J Cell Biol. 2001 Mar 19;152(6):1207-18.

43.

Laminin and alpha7beta1 integrin regulate agrin-induced clustering of acetylcholine receptors.

Burkin DJ, Kim JE, Gu M, Kaufman SJ.

J Cell Sci. 2000 Aug;113 ( Pt 16):2877-86.

44.

The alpha7beta1 integrin in muscle development and disease.

Burkin DJ, Kaufman SJ.

Cell Tissue Res. 1999 Apr;296(1):183-90. Review.

PMID:
10199978
45.

A functional role for specific spliced variants of the alpha7beta1 integrin in acetylcholine receptor clustering.

Burkin DJ, Gu M, Hodges BL, Campanelli JT, Kaufman SJ.

J Cell Biol. 1998 Nov 16;143(4):1067-75.

46.

New gene assignments using a complete, characterized sheep-hamster somatic cell hybrid panel.

Burkin DJ, Broad TE, Lambeth MR, Burkin HR, Jones C.

Anim Genet. 1998 Feb;29(1):48-54.

PMID:
9682451
47.

Localization and genomic organization of sheep antimicrobial peptide genes.

Huttner KM, Lambeth MR, Burkin HR, Burkin DJ, Broad TE.

Gene. 1998 Jan 5;206(1):85-91.

PMID:
9461419
48.

Use of the Indian muntjac idiogram to align conserved chromosomal segments in sheep and human genomes by chromosome painting.

Burkin DJ, Yang F, Broad TE, Wienberg J, Hill DF, Ferguson-Smith MA.

Genomics. 1997 Nov 15;46(1):143-7.

PMID:
9403070
49.

A fast, novel approach for DNA fibre-fluorescence in situ hybridization analysis.

Mann SM, Burkin DJ, Grin DK, Ferguson-Smith MA.

Chromosome Res. 1997 Apr;5(2):145-7. No abstract available.

PMID:
9146919
50.

Isolation of chromosome-specific paints from high-resolution flow karyotypes of the sheep (Ovis aries).

Burkin DJ, O'Brien PC, Broad TE, Hill DF, Jones CA, Wienberg J, Ferguson-Smith MA.

Chromosome Res. 1997 Apr;5(2):102-8.

PMID:
9146913

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