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Items: 1 to 50 of 126

1.

TG2 regulates the heat-shock response by the post-translational modification of HSF1.

Rossin F, Villella VR, D'Eletto M, Farrace MG, Esposito S, Ferrari E, Monzani R, Occhigrossi L, Pagliarini V, Sette C, Cozza G, Barlev NA, Falasca L, Fimia GM, Kroemer G, Raia V, Maiuri L, Piacentini M.

EMBO Rep. 2018 May 11. pii: e45067. doi: 10.15252/embr.201745067. [Epub ahead of print]

PMID:
29752334
2.

IL-9 and Mast Cells Are Key Players of Candida albicans Commensalism and Pathogenesis in the Gut.

Renga G, Moretti S, Oikonomou V, Borghi M, Zelante T, Paolicelli G, Costantini C, De Zuani M, Villella VR, Raia V, Del Sordo R, Bartoli A, Baldoni M, Renauld JC, Sidoni A, Garaci E, Maiuri L, Pucillo C, Romani L.

Cell Rep. 2018 May 8;23(6):1767-1778. doi: 10.1016/j.celrep.2018.04.034.

3.

Intra-individual biological variation in sweat chloride concentrations in CF, CFTR dysfunction, and healthy pediatric subjects.

Cirilli N, Raia V, Rocco I, De Gregorio F, Tosco A, Salvadori L, Sepe AO, Buzzetti R, Minicuci N, Castaldo G.

Pediatr Pulmonol. 2018 Apr 2. doi: 10.1002/ppul.23992. [Epub ahead of print]

PMID:
29611353
4.

May the new suggested lower borderline limit of sweat chloride impact the diagnostic process for cystic fibrosis?

Cirilli N, Braggion C, Mergni G, Polizzi AM, Padoan R, Sirianni S, Seia M, Raia V, Tosco A, Pisi G, Spaggiari C, Quattromano E, Bignamini E, Brandino D, Bella S, Argentini R; ICFS Sweat Test Working Group.

J Pediatr. 2018 Mar;194:261-262. doi: 10.1016/j.jpeds.2017.11.053. Epub 2018 Jan 17. No abstract available.

PMID:
29352589
5.

S737F is a new CFTR mutation typical of patients originally from the Tuscany region in Italy.

Terlizzi V, Di Lullo AM, Comegna M, Centrone C, Pelo E, Castaldo G, Raia V, Braggion C.

Ital J Pediatr. 2018 Jan 3;44(1):2. doi: 10.1186/s13052-017-0443-z.

6.

Lack of efficacy of Lactobacillus GG in reducing pulmonary exacerbations and hospital admissions in children with cystic fibrosis: A randomised placebo controlled trial.

Bruzzese E, Raia V, Ruberto E, Scotto R, Giannattasio A, Bruzzese D, Cavicchi MC, Francalanci M, Colombo C, Faelli N, Daccò V, Magazzù G, Costa S, Lucidi V, Majo F, Guarino A.

J Cyst Fibros. 2018 May;17(3):375-382. doi: 10.1016/j.jcf.2017.10.014. Epub 2017 Nov 8.

PMID:
29128317
7.

Strategies for the etiological therapy of cystic fibrosis.

Maiuri L, Raia V, Kroemer G.

Cell Death Differ. 2017 Nov;24(11):1825-1844. doi: 10.1038/cdd.2017.126. Epub 2017 Sep 22. Review.

8.

Long-Term Follow-Up in a Girl with Cystic Fibrosis and Diabetes Since the First Year of Life.

Fattorusso V, Casale A, Raia V, Mozzillo E, Franzese A.

Diabetes Ther. 2017 Oct;8(5):1187-1190. doi: 10.1007/s13300-017-0289-9. Epub 2017 Aug 2.

9.

Lung structure and function similarities between primary ciliary dyskinesia and mild cystic fibrosis: a pilot study.

Maglione M, Montella S, Mollica C, Carnovale V, Iacotucci P, De Gregorio F, Tosco A, Cervasio M, Raia V, Santamaria F.

Ital J Pediatr. 2017 Apr 12;43(1):34. doi: 10.1186/s13052-017-0351-2.

10.

Cysteamine re-establishes the clearance of Pseudomonas aeruginosa by macrophages bearing the cystic fibrosis-relevant F508del-CFTR mutation.

Ferrari E, Monzani R, Villella VR, Esposito S, Saluzzo F, Rossin F, D'Eletto M, Tosco A, De Gregorio F, Izzo V, Maiuri MC, Kroemer G, Raia V, Maiuri L.

Cell Death Dis. 2017 Jan 12;8(1):e2544. doi: 10.1038/cddis.2016.476.

11.

Metabolic interactions between cysteamine and epigallocatechin gallate.

Izzo V, Pietrocola F, Sica V, Durand S, Lachkar S, Enot D, Bravo-San Pedro JM, Chery A, Esposito S, Raia V, Maiuri L, Maiuri MC, Kroemer G.

Cell Cycle. 2017 Feb;16(3):271-279. doi: 10.1080/15384101.2016.1249550. Epub 2017 Jan 6.

12.

An "ex vivo model" contributing to the diagnosis and evaluation of new drugs in cystic fibrosis.

Di Lullo AM, Scorza M, Amato F, Comegna M, Raia V, Maiuri L, Ilardi G, Cantone E, Castaldo G, Iengo M.

Acta Otorhinolaryngol Ital. 2017 Jun;37(3):207-213. doi: 10.14639/0392-100X-1328.

13.

Genotype-phenotype correlation and functional studies in patients with cystic fibrosis bearing CFTR complex alleles.

Terlizzi V, Castaldo G, Salvatore D, Lucarelli M, Raia V, Angioni A, Carnovale V, Cirilli N, Casciaro R, Colombo C, Di Lullo AM, Elce A, Iacotucci P, Comegna M, Scorza M, Lucidi V, Perfetti A, Cimino R, Quattrucci S, Seia M, Sofia VM, Zarrilli F, Amato F.

J Med Genet. 2017 Apr;54(4):224-235. doi: 10.1136/jmedgenet-2016-103985. Epub 2016 Oct 13.

PMID:
27738188
14.

A novel treatment of cystic fibrosis acting on-target: cysteamine plus epigallocatechin gallate for the autophagy-dependent rescue of class II-mutated CFTR.

Tosco A, De Gregorio F, Esposito S, De Stefano D, Sana I, Ferrari E, Sepe A, Salvadori L, Buonpensiero P, Di Pasqua A, Grassia R, Leone CA, Guido S, De Rosa G, Lusa S, Bona G, Stoll G, Maiuri MC, Mehta A, Kroemer G, Maiuri L, Raia V.

Cell Death Differ. 2017 Jul;24(7):1305. doi: 10.1038/cdd.2016.43. Epub 2016 Jul 22.

15.

A novel treatment of cystic fibrosis acting on-target: cysteamine plus epigallocatechin gallate for the autophagy-dependent rescue of class II-mutated CFTR.

Tosco A, De Gregorio F, Esposito S, De Stefano D, Sana I, Ferrari E, Sepe A, Salvadori L, Buonpensiero P, Di Pasqua A, Grassia R, Leone CA, Guido S, De Rosa G, Lusa S, Bona G, Stoll G, Maiuri MC, Mehta A, Kroemer G, Maiuri L, Raia V.

Cell Death Differ. 2016 Aug;23(8):1380-93. doi: 10.1038/cdd.2016.22. Epub 2016 Apr 1. Erratum in: Cell Death Differ. 2017 Jul;24(7):1305.

16.

Manipulating proteostasis to repair the F508del-CFTR defect in cystic fibrosis.

Esposito S, Tosco A, Villella VR, Raia V, Kroemer G, Maiuri L.

Mol Cell Pediatr. 2016 Dec;3(1):13. doi: 10.1186/s40348-016-0040-z. Epub 2016 Mar 14. Review.

17.

Reduced absorption and enhanced synthesis of cholesterol in patients with cystic fibrosis: a preliminary study of plasma sterols.

Gelzo M, Sica C, Elce A, Dello Russo A, Iacotucci P, Carnovale V, Raia V, Salvatore D, Corso G, Castaldo G.

Clin Chem Lab Med. 2016 Sep 1;54(9):1461-6. doi: 10.1515/cclm-2015-1151.

PMID:
26913457
18.

The Italian pilot external quality assessment program for cystic fibrosis sweat test.

Salvatore M, Floridia G, Amato A, Censi F, Carta C, de Stefano MC, Ferrari G, Tosto F, Capoluongo E, Caruso U, Castaldo G, Cirilli N, Corbetta C, Padoan R, Raia V, Taruscio D.

Clin Biochem. 2016 May;49(7-8):601-5. doi: 10.1016/j.clinbiochem.2015.12.014. Epub 2016 Feb 3.

PMID:
26851350
19.

The holy grail of cystic fibrosis research: pharmacological repair of the F508del-CFTR mutation.

Maiuri L, De Stefano D, Raia V, Kroemer G.

Ann Transl Med. 2015 May;3(Suppl 1):S24. doi: 10.3978/j.issn.2305-5839.2015.02.32. No abstract available.

20.

Screening of glucose metabolism derangements in pediatric cystic fibrosis patients: how, when, why.

Franzese A, Mozzillo E, Fattorusso V, Raia V, Valerio G.

Acta Diabetol. 2015 Aug;52(4):633-8. doi: 10.1007/s00592-015-0743-y. Epub 2015 Apr 12. Review.

PMID:
25863781
21.

Simple diagnosis of benign acute childhood myositis: Lessons from a case report.

Terlizzi V, Improta F, Raia V.

J Pediatr Neurosci. 2014 Sep-Dec;9(3):280-2. doi: 10.4103/1817-1745.147595.

22.

Clinical expression of patients with the D1152H CFTR mutation.

Terlizzi V, Carnovale V, Castaldo G, Castellani C, Cirilli N, Colombo C, Corti F, Cresta F, D'Adda A, Lucarelli M, Lucidi V, Macchiaroli A, Madarena E, Padoan R, Quattrucci S, Salvatore D, Zarrilli F, Raia V.

J Cyst Fibros. 2015 Jul;14(4):447-52. doi: 10.1016/j.jcf.2014.12.012. Epub 2015 Jan 10.

23.

Randomized, single blind, controlled trial of inhaled glutathione vs placebo in patients with cystic fibrosis.

Calabrese C, Tosco A, Abete P, Carnovale V, Basile C, Magliocca A, Quattrucci S, De Sanctis S, Alatri F, Mazzarella G, De Pietro L, Turino C, Melillo E, Buonpensiero P, Di Pasqua A, Raia V.

J Cyst Fibros. 2015 Mar;14(2):203-10. doi: 10.1016/j.jcf.2014.09.014. Epub 2014 Nov 4.

24.

Identification of Inquilinus limosus in cystic fibrosis: a first report in Italy.

Cicatiello AG, Iula DV, Pagliuca C, Pastore G, Pagliarulo C, Catania MR, Catania MR, Colicchio R, Picardi M, Raia V, Salvatore P.

New Microbiol. 2014 Oct;37(4):567-71. Epub 2014 Oct 1.

25.

Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutation.

De Stefano D, Villella VR, Esposito S, Tosco A, Sepe A, De Gregorio F, Salvadori L, Grassia R, Leone CA, De Rosa G, Maiuri MC, Pettoello-Mantovani M, Guido S, Bossi A, Zolin A, Venerando A, Pinna LA, Mehta A, Bona G, Kroemer G, Maiuri L, Raia V.

Autophagy. 2014;10(11):2053-74. doi: 10.4161/15548627.2014.973737.

26.

Can continuous subcutaneous insulin infusion improve health-related quality of life in patients with Shwachman-Bodian-Diamond syndrome and diabetes?

Terlizzi V, Zito E, Mozzillo E, Raia V, Franzese A.

Diabetes Technol Ther. 2015 Jan;17(1):64-7. doi: 10.1089/dia.2014.0184.

PMID:
25269020
27.

Shwachman-Diamond syndrome with autoimmune-like liver disease and enteropathy mimicking celiac disease.

Veropalumbo C, Campanozzi A, De Gregorio F, Correra A, Raia V, Vajro P.

Clin Res Hepatol Gastroenterol. 2015 Feb;39(1):e1-4. doi: 10.1016/j.clinre.2014.06.017. Epub 2014 Aug 14.

PMID:
25129842
28.

Primary herpes virus infection and ischemic stroke in childhood: a new association?

Terlizzi V, Improta F, Di Fraia T, Sanguigno E, D'Amico A, Buono S, Raia V, Boccia G.

J Clin Neurosci. 2014 Sep;21(9):1656-8. doi: 10.1016/j.jocn.2013.12.023. Epub 2014 Apr 13.

PMID:
24736195
29.

Disrupted intestinal microbiota and intestinal inflammation in children with cystic fibrosis and its restoration with Lactobacillus GG: a randomised clinical trial.

Bruzzese E, Callegari ML, Raia V, Viscovo S, Scotto R, Ferrari S, Morelli L, Buccigrossi V, Lo Vecchio A, Ruberto E, Guarino A.

PLoS One. 2014 Feb 19;9(2):e87796. doi: 10.1371/journal.pone.0087796. eCollection 2014.

30.

Cystic fibrosis database (CFDB): a new web-based tool for cystic fibrosis specialists.

Buzzetti R, Cirilli N, Minicucci L, Raia V, Salvatore D, Maffeis P.

Pediatr Pulmonol. 2014 Sep;49(9):938-40. doi: 10.1002/ppul.22954. Epub 2014 Feb 16.

PMID:
24532370
31.

Prediction of acute pancreatitis risk based on PIP score in children with cystic fibrosis.

Terlizzi V, Tosco A, Tomaiuolo R, Sepe A, Amato N, Casale A, Mercogliano C, De Gregorio F, Improta F, Elce A, Castaldo G, Raia V.

J Cyst Fibros. 2014 Sep;13(5):579-84. doi: 10.1016/j.jcf.2014.01.007. Epub 2014 Feb 11.

32.

Treatment of low bone density in young people with cystic fibrosis: a multicentre, prospective, open-label observational study of calcium and calcifediol followed by a randomised placebo-controlled trial of alendronate.

Bianchi ML, Colombo C, Assael BM, Dubini A, Lombardo M, Quattrucci S, Bella S, Collura M, Messore B, Raia V, Poli F, Bini R, Albanese CV, De Rose V, Costantini D, Romano G, Pustorino E, Magazzù G, Bertasi S, Lucidi V, Traverso G, Coruzzo A, Grzejdziak AD.

Lancet Respir Med. 2013 Jul;1(5):377-85. doi: 10.1016/S2213-2600(13)70064-X. Epub 2013 Jun 2.

PMID:
24429202
33.

Brand new SPINK1 and CFTR mutations in a child with acute recurrent pancreatitis: a case report.

Terlizzi V, De Gregorio F, Sepe A, Amato N, Arduino C, Casale A, Majo F, Tomaiuolo R, Castaldo G, Raia V.

Minerva Pediatr. 2013 Dec;65(6):669-72.

PMID:
24217635
34.

Towards a rational combination therapy of cystic fibrosis: How cystamine restores the stability of mutant CFTR.

Villella VR, Esposito S, Maiuri MC, Raia V, Kroemer G, Maiuri L.

Autophagy. 2013 Sep;9(9):1431-4. doi: 10.4161/auto.25517. Epub 2013 Jun 25.

PMID:
23800975
35.

Disease-relevant proteostasis regulation of cystic fibrosis transmembrane conductance regulator.

Villella VR, Esposito S, Bruscia EM, Vicinanza M, Cenci S, Guido S, Pettoello-Mantovani M, Carnuccio R, De Matteis MA, Luini A, Maiuri MC, Raia V, Kroemer G, Maiuri L.

Cell Death Differ. 2013 Aug;20(8):1101-15. doi: 10.1038/cdd.2013.46. Epub 2013 May 17.

36.

Reduced caveolin-1 promotes hyperinflammation due to abnormal heme oxygenase-1 localization in lipopolysaccharide-challenged macrophages with dysfunctional cystic fibrosis transmembrane conductance regulator.

Zhang PX, Murray TS, Villella VR, Ferrari E, Esposito S, D'Souza A, Raia V, Maiuri L, Krause DS, Egan ME, Bruscia EM.

J Immunol. 2013 May 15;190(10):5196-206. doi: 10.4049/jimmunol.1201607. Epub 2013 Apr 19.

37.

Targeting the Intracellular Environment in Cystic Fibrosis: Restoring Autophagy as a Novel Strategy to Circumvent the CFTR Defect.

Villella VR, Esposito S, Bruscia EM, Maiuri MC, Raia V, Kroemer G, Maiuri L.

Front Pharmacol. 2013 Jan 21;4:1. doi: 10.3389/fphar.2013.00001. eCollection 2013.

38.

Rapid identification of Burkholderia cepacia complex species recovered from cystic fibrosis patients using matrix-assisted laser desorption ionization time-of-flight mass spectrometry.

Lambiase A, Del Pezzo M, Cerbone D, Raia V, Rossano F, Catania MR.

J Microbiol Methods. 2013 Feb 15;92(2):145-9. doi: 10.1016/j.mimet.2012.11.010. Epub 2012 Nov 29.

PMID:
23201483
39.

Glucose derangements in very young children with cystic fibrosis and pancreatic insufficiency.

Mozzillo E, Raia V, Fattorusso V, Falco M, Sepe A, De Gregorio F, Nugnes R, Valerio G, Franzese A.

Diabetes Care. 2012 Nov;35(11):e78. doi: 10.2337/dc12-0459. No abstract available.

40.

An overview of international literature from cystic fibrosis registries. Part 4: update 2011.

Salvatore D, Buzzetti R, Baldo E, Furnari ML, Lucidi V, Manunza D, Marinelli I, Messore B, Neri AS, Raia V, Mastella G.

J Cyst Fibros. 2012 Dec;11(6):480-93. doi: 10.1016/j.jcf.2012.07.005. Epub 2012 Aug 9. Review.

41.

Targeting autophagy as a novel strategy for facilitating the therapeutic action of potentiators on ΔF508 cystic fibrosis transmembrane conductance regulator.

Luciani A, Villella VR, Esposito S, Gavina M, Russo I, Silano M, Guido S, Pettoello-Mantovani M, Carnuccio R, Scholte B, De Matteis A, Maiuri MC, Raia V, Luini A, Kroemer G, Maiuri L.

Autophagy. 2012 Nov;8(11):1657-72. doi: 10.4161/auto.21483. Epub 2012 Aug 9.

42.

Different mutations in mucA gene of Pseudomonas aeruginosa mucoid strains in cystic fibrosis patients and their effect on algU gene expression.

Pulcrano G, Iula DV, Raia V, Rossano F, Catania MR.

New Microbiol. 2012 Jul;35(3):295-305. Epub 2012 Jun 30.

43.

Nebulized hyaluronan ameliorates lung inflammation in cystic fibrosis mice.

Gavina M, Luciani A, Villella VR, Esposito S, Ferrari E, Bressani I, Casale A, Bruscia EM, Maiuri L, Raia V.

Pediatr Pulmonol. 2013 Aug;48(8):761-71. doi: 10.1002/ppul.22637. Epub 2012 Jul 23.

PMID:
22825912
44.

NMR spectroscopy metabolomic profiling of exhaled breath condensate in patients with stable and unstable cystic fibrosis.

Montuschi P, Paris D, Melck D, Lucidi V, Ciabattoni G, Raia V, Calabrese C, Bush A, Barnes PJ, Motta A.

Thorax. 2012 Mar;67(3):222-8. doi: 10.1136/thoraxjnl-2011-200072. Epub 2011 Nov 21.

PMID:
22106016
45.

Slow-release insulin in cystic fibrosis patients with glucose intolerance: a randomized clinical trial.

Minicucci L, Haupt M, Casciaro R, De Alessandri A, Bagnasco F, Lucidi V, Notarnicola S, Lorini R, Bertasi S, Raia V, Cialdella P, Haupt R.

Pediatr Diabetes. 2012 Mar;13(2):197-202. doi: 10.1111/j.1399-5448.2011.00810.x. Epub 2011 Nov 8.

PMID:
22060105
46.

Validation of a predictive survival model in Italian patients with cystic fibrosis.

Buzzetti R, Alicandro G, Minicucci L, Notarnicola S, Furnari ML, Giordano G, Lucidi V, Montemitro E, Raia V, Magazzù G, Vieni G, Quattrucci S, Ferrazza A, Gagliardini R, Cirilli N, Salvatore D, Colombo C.

J Cyst Fibros. 2012 Jan;11(1):24-9. doi: 10.1016/j.jcf.2011.08.007. Epub 2011 Sep 23.

47.

Insulin production and resistance in cystic fibrosis: effect of age, disease activity, and genotype.

Street ME, Spaggiari C, Ziveri MA, Rossi M, Volta C, Viani I, Grzincich GL, Sartori C, Zanzucchi M, Raia V, Terzi C, Pisi G, Zanetti E, Boguszewski MC, Kamoi TO, Bernasconi S.

J Endocrinol Invest. 2012 Mar;35(3):246-53. doi: 10.3275/7628. Epub 2011 Apr 6.

PMID:
21483232
48.

Measurement of nasal nitric oxide by hand-held and stationary devices.

Montella S, Alving K, Maniscalco M, Sofia M, De Stefano S, Raia V, Santamaria F.

Eur J Clin Invest. 2011 Oct;41(10):1063-70. doi: 10.1111/j.1365-2362.2011.02501.x. Epub 2011 Mar 17.

PMID:
21413977
49.

Achromobacter xylosoxidans respiratory tract infection in cystic fibrosis patients.

Lambiase A, Catania MR, Del Pezzo M, Rossano F, Terlizzi V, Sepe A, Raia V.

Eur J Clin Microbiol Infect Dis. 2011 Aug;30(8):973-80. doi: 10.1007/s10096-011-1182-5. Epub 2011 Jan 31.

50.

One-source peptide/phosphopeptide standards for accurate phosphorylation degree determination.

Hahn B, Böhm M, Raia V, Zinn N, Möller P, Klingmüller U, Lehmann WD.

Proteomics. 2011 Feb;11(3):490-4. doi: 10.1002/pmic.201000569. Epub 2011 Jan 13.

PMID:
21268278

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