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Items: 28

1.

Effects of Lumacaftor/Ivacaftor Therapy on CFTR Function in Phe508del Homozygous Patients with Cystic Fibrosis.

Graeber SY, Dopfer C, Naehrlich L, Gyulumyan L, Scheuermann H, Hirtz S, Wege S, Mairbäurl H, Dorda M, Hyde R, Bagheri-Hanson A, Rueckes-Nilges C, Fischer S, Mall MA, Tümmler B.

Am J Respir Crit Care Med. 2018 Jan 12. doi: 10.1164/rccm.201710-1983OC. [Epub ahead of print]

PMID:
29327948
2.

Repaglinide versus insulin for newly diagnosed diabetes in patients with cystic fibrosis: a multicentre, open-label, randomised trial.

Ballmann M, Hubert D, Assael BM, Staab D, Hebestreit A, Naehrlich L, Nickolay T, Prinz N, Holl RW; CFRD Study Group.

Lancet Diabetes Endocrinol. 2018 Feb;6(2):114-121. doi: 10.1016/S2213-8587(17)30400-X. Epub 2017 Dec 5.

PMID:
29199116
3.

Cystic Fibrosis.

Naehrig S, Chao CM, Naehrlich L.

Dtsch Arztebl Int. 2017 Aug 21;114(33-34):564-574. doi: 10.3238/arztebl.2017.0564.

4.

Three-center feasibility of lung clearance index in infants and preschool children with cystic fibrosis and other lung diseases.

Stahl M, Graeber SY, Joachim C, Barth S, Ricklefs I, Diekmann G, Kopp MV, Naehrlich L, Mall MA.

J Cyst Fibros. 2017 Aug 12. pii: S1569-1993(17)30836-6. doi: 10.1016/j.jcf.2017.08.001. [Epub ahead of print]

PMID:
28811149
5.

Assessment of pathologic increase in liver stiffness enables earlier diagnosis of CFLD: Results from a prospective longitudinal cohort study.

Klotter V, Gunchick C, Siemers E, Rath T, Hudel H, Naehrlich L, Roderfeld M, Roeb E.

PLoS One. 2017 Jun 2;12(6):e0178784. doi: 10.1371/journal.pone.0178784. eCollection 2017.

6.

Importance to question sinonasal symptoms and to perform rhinoscopy and rhinomanometry in cystic fibrosis patients.

Bock JM, Schien M, Fischer C, Naehrlich L, Kaeding M, Guntinas-Lichius O, Gerber A, Arnold C, Mainz JG.

Pediatr Pulmonol. 2017 Feb;52(2):167-174. doi: 10.1002/ppul.23613. Epub 2016 Nov 28.

PMID:
27893197
7.

Cystic fibrosis transmembrane conductance regulator biomarkers in 'real life': can we evaluate individual efficacy of cystic fibrosis transmembrane conductance regulator therapy?

van Koningsbruggen-Rietschel S, Naehrlich L.

Ther Adv Respir Dis. 2015 Aug;9(4):198-200. doi: 10.1177/1753465815579364. No abstract available.

PMID:
26175480
8.

Prevalence of meconium ileus marks the severity of mutations of the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene.

Dupuis A, Keenan K, Ooi CY, Dorfman R, Sontag MK, Naehrlich L, Castellani C, Strug LJ, Rommens JM, Gonska T.

Genet Med. 2016 Apr;18(4):333-40. doi: 10.1038/gim.2015.79. Epub 2015 Jun 18.

PMID:
26087176
9.

Identification of neutrophil activation markers as novel surrogate markers of CF lung disease.

Rath T, Zwaschka L, Hage L, Kügler M, Menendez K, Naehrlich L, Schulz R, Roderfeld M, Roeb E.

PLoS One. 2014 Dec 29;9(12):e115847. doi: 10.1371/journal.pone.0115847. eCollection 2014.

10.

High variability in oral glucose tolerance among 1,128 patients with cystic fibrosis: a multicenter screening study.

Scheuing N, Holl RW, Dockter G, Hermann JM, Junge S, Koerner-Rettberg C, Naehrlich L, Smaczny C, Staab D, Thalhammer G, van Koningsbruggen-Rietschel S, Ballmann M.

PLoS One. 2014 Nov 13;9(11):e112578. doi: 10.1371/journal.pone.0112578. eCollection 2014.

11.

Nasal potential difference: Best or average result for CFTR function as diagnostic criteria for cystic fibrosis?

Keenan K, Avolio J, Rueckes-Nilges C, Tullis E, Gonska T, Naehrlich L.

J Cyst Fibros. 2015 May;14(3):310-6. doi: 10.1016/j.jcf.2014.09.006. Epub 2014 Oct 7.

12.

Intestinal current measurement versus nasal potential difference measurements for diagnosis of cystic fibrosis: a case-control study.

Bagheri-Hanson A, Nedwed S, Rueckes-Nilges C, Naehrlich L.

BMC Pulm Med. 2014 Oct 4;14:156. doi: 10.1186/1471-2466-14-156.

13.

Diabetes in cystic fibrosis: multicenter screening results based on current guidelines.

Scheuing N, Holl RW, Dockter G, Fink K, Junge S, Naehrlich L, Smaczny C, Staab D, Thalhammer G, van Koningsbruggen-Rietschel S, Ballmann M.

PLoS One. 2013 Dec 6;8(12):e81545. doi: 10.1371/journal.pone.0081545. eCollection 2013.

14.

Is there evidence for correct diagnosis in cystic fibrosis registries?

Thomas M, Lemonnier L, Gulmans V, Naehrlich L, Vermeulen F, Cuppens H, Castellani C, Norek A, De Boeck K.

J Cyst Fibros. 2014 May;13(3):275-80. doi: 10.1016/j.jcf.2013.10.010. Epub 2013 Nov 22.

15.

Nasal potential difference measurements in diagnosis of cystic fibrosis: an international survey.

Naehrlich L, Ballmann M, Davies J, Derichs N, Gonska T, Hjelte L, van Konigsbruggen-Rietschel S, Leal T, Melotti P, Middleton P, Tümmler B, Vermeulen F, Wilschanski M; ECFS Diagnostic Network Working Group.

J Cyst Fibros. 2014 Jan;13(1):24-8. doi: 10.1016/j.jcf.2013.08.006. Epub 2013 Sep 7.

16.

Serum proteome profiling identifies novel and powerful markers of cystic fibrosis liver disease.

Rath T, Hage L, Kügler M, Menendez Menendez K, Zachoval R, Naehrlich L, Schulz R, Roderfeld M, Roeb E.

PLoS One. 2013;8(3):e58955. doi: 10.1371/journal.pone.0058955. Epub 2013 Mar 14.

17.

Individualized vitamin A supplementation for patients with cystic fibrosis.

Brei C, Simon A, Krawinkel MB, Naehrlich L.

Clin Nutr. 2013 Oct;32(5):805-10. doi: 10.1016/j.clnu.2013.01.009. Epub 2013 Jan 31.

PMID:
23395254
18.

A pilot study of the characterization of hepatic tissue strain in children with cystic-fibrosis-associated liver disease (CFLD) by acoustic radiation force impulse imaging.

Behrens CB, Langholz JH, Eiler J, Jenewein R, Naehrlich L, Fuchs K, Harth S, Krombach GA, Alzen GF.

Pediatr Radiol. 2013 Mar;43(5):552-7. doi: 10.1007/s00247-012-2560-6. Epub 2012 Nov 29.

PMID:
23192669
19.

Iodine deficiency and subclinical hypothyroidism are common in cystic fibrosis patients.

Naehrlich L, Dörr HG, Bagheri-Behrouzi A, Rauh M.

J Trace Elem Med Biol. 2013 Apr;27(2):122-5. doi: 10.1016/j.jtemb.2012.08.002. Epub 2012 Oct 26.

PMID:
23107148
20.

Misdiagnosis of cystic fibrosis: experience from Germany.

Naehrlich L, Bagheri-Behrouzi A; German CF quality assurance group.

J Cyst Fibros. 2013 Jan;12(1):68-73. doi: 10.1016/j.jcf.2012.06.008. Epub 2012 Jul 24.

21.

Serine proteases degrade airway mucins in cystic fibrosis.

Henke MO, John G, Rheineck C, Chillappagari S, Naehrlich L, Rubin BK.

Infect Immun. 2011 Aug;79(8):3438-44. doi: 10.1128/IAI.01252-10. Epub 2011 Jun 6.

22.

Concordant genotype of upper and lower airways P aeruginosa and S aureus isolates in cystic fibrosis.

Mainz JG, Naehrlich L, Schien M, Käding M, Schiller I, Mayr S, Schneider G, Wiedemann B, Wiehlmann L, Cramer N, Pfister W, Kahl BC, Beck JF, Tümmler B.

Thorax. 2009 Jun;64(6):535-40. doi: 10.1136/thx.2008.104711. Epub 2009 Mar 11.

PMID:
19282318
23.

Functional characterization of a novel CFTR mutation P67S identified in a patient with atypical cystic fibrosis.

Kraus C, Reis A, Naehrlich L, Dötsch J, Korbmacher C, Rauh R.

Cell Physiol Biochem. 2007;19(5-6):239-48.

24.

Sweat testing in CF.

Naehrlich L.

Thorax. 2007 May;62(5):462; author reply 463. No abstract available.

25.

[Sweat testing practices in German cystic fibrosis centres].

Naehrlich L.

Klin Padiatr. 2007 Mar-Apr;219(2):70-3. German.

PMID:
17405070
26.

Endoscopic cystogastrostomy of a pancreatic retention cyst in cystic fibrosis.

Naehrlich L, Zapke M, Rupprecht T, Becker D.

J Pediatr Gastroenterol Nutr. 2005 Oct;41(4):477-8. No abstract available.

PMID:
16205519
27.

[Two rare complications of percutaneous endoscopic gastrostomy: obstruction of the pylorus and gastrocolic fistula occurring in one patient].

Naehrlich L, Carbon R, Lang T, Behrens R.

Klin Padiatr. 2001 Nov-Dec;213(6):329-31. German.

PMID:
11713711
28.

Balloon dilation of an esophageal stenosis in a patient with recessive dystrophic epidermolysis bullosa.

Naehrlich L, Lang T, Schamberger U, Behrens R.

Pediatr Dermatol. 2000 Nov-Dec;17(6):477-9.

PMID:
11123785

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