Format
Sort by
Items per page

Send to

Choose Destination

Links from PubMed

Items: 1 to 20 of 94

1.

Internal deletion compromises the stability of dystrophin.

Henderson DM, Belanto JJ, Li B, Heun-Johnson H, Ervasti JM.

Hum Mol Genet. 2011 Aug 1;20(15):2955-63. doi: 10.1093/hmg/ddr199. Epub 2011 May 10.

2.

Thermodynamic stability, unfolding kinetics, and aggregation of the N-terminal actin-binding domains of utrophin and dystrophin.

Singh SM, Molas JF, Kongari N, Bandi S, Armstrong GS, Winder SJ, Mallela KM.

Proteins. 2012 May;80(5):1377-92. doi: 10.1002/prot.24033. Epub 2012 Feb 17.

3.

The N- and C-Terminal Domains Differentially Contribute to the Structure and Function of Dystrophin and Utrophin Tandem Calponin-Homology Domains.

Singh SM, Bandi S, Mallela KM.

Biochemistry. 2015 Nov 24;54(46):6942-50. doi: 10.1021/acs.biochem.5b00969. Epub 2015 Nov 13.

PMID:
26516677
4.

In vitro stability of therapeutically relevant, internally truncated dystrophins.

McCourt JL, Rhett KK, Jaeger MA, Belanto JJ, Talsness DM, Ervasti JM.

Skelet Muscle. 2015 Apr 28;5:13. doi: 10.1186/s13395-015-0040-z. eCollection 2015.

5.

Functional substitution by TAT-utrophin in dystrophin-deficient mice.

Sonnemann KJ, Heun-Johnson H, Turner AJ, Baltgalvis KA, Lowe DA, Ervasti JM.

PLoS Med. 2009 May 26;6(5):e1000083. doi: 10.1371/journal.pmed.1000083. Epub 2009 May 26.

6.

The crystal structures of dystrophin and utrophin spectrin repeats: implications for domain boundaries.

Muthu M, Richardson KA, Sutherland-Smith AJ.

PLoS One. 2012;7(7):e40066. doi: 10.1371/journal.pone.0040066. Epub 2012 Jul 20.

7.

Impacts of dystrophin and utrophin domains on actin structural dynamics: implications for therapeutic design.

Lin AY, Prochniewicz E, Henderson DM, Li B, Ervasti JM, Thomas DD.

J Mol Biol. 2012 Jun 29;420(1-2):87-98. doi: 10.1016/j.jmb.2012.04.005. Epub 2012 Apr 11.

8.

Utrophin upregulation for treating Duchenne or Becker muscular dystrophy: how close are we?

Miura P, Jasmin BJ.

Trends Mol Med. 2006 Mar;12(3):122-9. Epub 2006 Jan 27. Review.

PMID:
16443393
9.

Rescue from respiratory dysfunction by transduction of full-length dystrophin to diaphragm via the peritoneal cavity in utrophin/dystrophin double knockout mice.

Ishizaki M, Maeda Y, Kawano R, Suga T, Uchida Y, Uchino K, Yamashita S, Kimura E, Uchino M.

Mol Ther. 2011 Jul;19(7):1230-5. doi: 10.1038/mt.2011.58. Epub 2011 Apr 5.

10.

Interdomain Linker Determines Primarily the Structural Stability of Dystrophin and Utrophin Tandem Calponin-Homology Domains Rather than Their Actin-Binding Affinity.

Bandi S, Singh SM, Mallela KM.

Biochemistry. 2015 Sep 8;54(35):5480-8. doi: 10.1021/acs.biochem.5b00741. Epub 2015 Aug 26.

PMID:
26288220
11.

Upregulation of brain utrophin does not rescue behavioral alterations in dystrophin-deficient mice.

Perronnet C, Chagneau C, Le Blanc P, Samson-Desvignes N, Mornet D, Laroche S, De La Porte S, Vaillend C.

Hum Mol Genet. 2012 May 15;21(10):2263-76. doi: 10.1093/hmg/dds047. Epub 2012 Feb 15.

PMID:
22343141
12.
13.

ZZ domain is essentially required for the physiological binding of dystrophin and utrophin to beta-dystroglycan.

Ishikawa-Sakurai M, Yoshida M, Imamura M, Davies KE, Ozawa E.

Hum Mol Genet. 2004 Apr 1;13(7):693-702. Epub 2004 Feb 12.

PMID:
14962982
14.

Analysis of gene expression differences between utrophin/dystrophin-deficient vs mdx skeletal muscles reveals a specific upregulation of slow muscle genes in limb muscles.

Baker PE, Kearney JA, Gong B, Merriam AP, Kuhn DE, Porter JD, Rafael-Fortney JA.

Neurogenetics. 2006 May;7(2):81-91. Epub 2006 Mar 9.

PMID:
16525850
15.

Dystrophins, utrophins, and associated scaffolding complexes: role in mammalian brain and implications for therapeutic strategies.

Perronnet C, Vaillend C.

J Biomed Biotechnol. 2010;2010:849426. doi: 10.1155/2010/849426. Epub 2010 Jun 17. Review. Erratum in: J Biomed Biotechnol. 2010;2010:970749.

16.
17.

Immunostaining of dystrophin and utrophin in skeletal muscle of dystrophinopathies.

Sahashi K, Ibi T, Suoh H, Nakao N, Tashiro M, Marui K, Arahata K, Sugita H.

Intern Med. 1994 May;33(5):277-83.

18.

The dystrophin / utrophin homologues in Drosophila and in sea urchin.

Neuman S, Kaban A, Volk T, Yaffe D, Nudel U.

Gene. 2001 Jan 24;263(1-2):17-29.

PMID:
11223239
19.

Disease-causing missense mutations in actin binding domain 1 of dystrophin induce thermodynamic instability and protein aggregation.

Henderson DM, Lee A, Ervasti JM.

Proc Natl Acad Sci U S A. 2010 May 25;107(21):9632-7. doi: 10.1073/pnas.1001517107. Epub 2010 May 10.

20.

Role of dystrophin and utrophin for assembly and function of the dystrophin glycoprotein complex in non-muscle tissue.

Haenggi T, Fritschy JM.

Cell Mol Life Sci. 2006 Jul;63(14):1614-31. Review.

PMID:
16710609

Supplemental Content

Support Center