Sort by
Items per page

Send to

Choose Destination

Links from PubMed

Items: 1 to 20 of 157


Conditional deletion of Abca3 in alveolar type II cells alters surfactant homeostasis in newborn and adult mice.

Besnard V, Matsuzaki Y, Clark J, Xu Y, Wert SE, Ikegami M, Stahlman MT, Weaver TE, Hunt AN, Postle AD, Whitsett JA.

Am J Physiol Lung Cell Mol Physiol. 2010 May;298(5):L646-59. doi: 10.1152/ajplung.00409.2009. Epub 2010 Feb 26.


ABCA3 gene mutations in newborns with fatal surfactant deficiency.

Shulenin S, Nogee LM, Annilo T, Wert SE, Whitsett JA, Dean M.

N Engl J Med. 2004 Mar 25;350(13):1296-303.


STAT3 regulates ABCA3 expression and influences lamellar body formation in alveolar type II cells.

Matsuzaki Y, Besnard V, Clark JC, Xu Y, Wert SE, Ikegami M, Whitsett JA.

Am J Respir Cell Mol Biol. 2008 May;38(5):551-8. Epub 2007 Dec 20.


Alteration of the pulmonary surfactant system in full-term infants with hereditary ABCA3 deficiency.

Brasch F, Schimanski S, Mühlfeld C, Barlage S, Langmann T, Aslanidis C, Boettcher A, Dada A, Schroten H, Mildenberger E, Prueter E, Ballmann M, Ochs M, Johnen G, Griese M, Schmitz G.

Am J Respir Crit Care Med. 2006 Sep 1;174(5):571-80. Epub 2006 May 25.


Ultrastructural and molecular analysis in fatal neonatal interstitial pneumonia caused by a novel ABCA3 mutation.

Bruder E, Hofmeister J, Aslanidis C, Hammer J, Bubendorf L, Schmitz G, Rufle A, Bührer C.

Mod Pathol. 2007 Oct;20(10):1009-18. Epub 2007 Jul 27.


Aberrant lung remodeling in a mouse model of surfactant dysregulation induced by modulation of the Abca3 gene.

Beers MF, Knudsen L, Tomer Y, Maronn J, Zhao M, Ochs M, Mulugeta S.

Ann Anat. 2017 Mar;210:135-146. doi: 10.1016/j.aanat.2016.11.015. Epub 2016 Dec 26.


Ultrastructure of lamellar bodies in congenital surfactant deficiency.

Edwards V, Cutz E, Viero S, Moore AM, Nogee L.

Ultrastruct Pathol. 2005 Nov-Dec;29(6):503-9.


C/EBP{alpha} is required for pulmonary cytoprotection during hyperoxia.

Xu Y, Saegusa C, Schehr A, Grant S, Whitsett JA, Ikegami M.

Am J Physiol Lung Cell Mol Physiol. 2009 Aug;297(2):L286-98. doi: 10.1152/ajplung.00094.2009. Epub 2009 May 22.


Sterol response element binding protein and thyroid transcription factor-1 (Nkx2.1) regulate Abca3 gene expression.

Besnard V, Xu Y, Whitsett JA.

Am J Physiol Lung Cell Mol Physiol. 2007 Dec;293(6):L1395-405. Epub 2007 Sep 21.


ABCA3 as a lipid transporter in pulmonary surfactant biogenesis.

Ban N, Matsumura Y, Sakai H, Takanezawa Y, Sasaki M, Arai H, Inagaki N.

J Biol Chem. 2007 Mar 30;282(13):9628-34. Epub 2007 Jan 30.


Identification of LBM180, a lamellar body limiting membrane protein of alveolar type II cells, as the ABC transporter protein ABCA3.

Mulugeta S, Gray JM, Notarfrancesco KL, Gonzales LW, Koval M, Feinstein SI, Ballard PL, Fisher AB, Shuman H.

J Biol Chem. 2002 Jun 21;277(25):22147-55. Epub 2002 Apr 8.


Functional and trafficking defects in ATP binding cassette A3 mutants associated with respiratory distress syndrome.

Cheong N, Madesh M, Gonzales LW, Zhao M, Yu K, Ballard PL, Shuman H.

J Biol Chem. 2006 Apr 7;281(14):9791-800. Epub 2006 Jan 16.


Characterization and classification of ATP-binding cassette transporter ABCA3 mutants in fatal surfactant deficiency.

Matsumura Y, Ban N, Ueda K, Inagaki N.

J Biol Chem. 2006 Nov 10;281(45):34503-14. Epub 2006 Sep 7.


Surfactant composition and function in patients with ABCA3 mutations.

Garmany TH, Moxley MA, White FV, Dean M, Hull WM, Whitsett JA, Nogee LM, Hamvas A.

Pediatr Res. 2006 Jun;59(6):801-5. Epub 2006 Apr 26.


Ultrastructural characterization of genetic diffuse lung diseases in infants and children: a cohort study and review.

Citti A, Peca D, Petrini S, Cutrera R, Biban P, Haass C, Boldrini R, Danhaive O.

Ultrastruct Pathol. 2013 Oct;37(5):356-65. doi: 10.3109/01913123.2013.811454.


Respiratory syncytial virus potentiates ABCA3 mutation-induced loss of lung epithelial cell differentiation.

Kaltenborn E, Kern S, Frixel S, Fragnet L, Conzelmann KK, Zarbock R, Griese M.

Hum Mol Genet. 2012 Jun 15;21(12):2793-806. doi: 10.1093/hmg/dds107. Epub 2012 Mar 20.


ABCA3 is critical for lamellar body biogenesis in vivo.

Cheong N, Zhang H, Madesh M, Zhao M, Yu K, Dodia C, Fisher AB, Savani RC, Shuman H.

J Biol Chem. 2007 Aug 17;282(33):23811-7. Epub 2007 May 31.


Expression of ABCA3 in developing lung and other tissues.

Stahlman MT, Besnard V, Wert SE, Weaver TE, Dingle S, Xu Y, von Zychlin K, Olson SJ, Whitsett JA.

J Histochem Cytochem. 2007 Jan;55(1):71-83. Epub 2006 Sep 18.


Loss of Shp2 in alveoli epithelia induces deregulated surfactant homeostasis, resulting in spontaneous pulmonary fibrosis.

Zhang X, Zhang Y, Tao B, Teng L, Li Y, Cao R, Gui Q, Ye M, Mou X, Cheng H, Hu H, Zhou R, Wu X, Xie Q, Ning W, Lai M, Shen H, Feng GS, Ke Y.

FASEB J. 2012 Jun;26(6):2338-50. doi: 10.1096/fj.11-200139. Epub 2012 Feb 23.


Supplemental Content

Support Center