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Items: 1 to 20 of 216

1.

Serpin polymerization and its role in disease--the molecular basis of alpha1-antitrypsin deficiency.

Knaupp AS, Bottomley SP.

IUBMB Life. 2009 Jan;61(1):1-5. doi: 10.1002/iub.127. Review.

2.

Alpha(1)-antitrypsin deficiency, liver disease and emphysema.

Parfrey H, Mahadeva R, Lomas DA.

Int J Biochem Cell Biol. 2003 Jul;35(7):1009-14. Review.

PMID:
12672469
3.

New insights into the structural basis of alpha 1-antitrypsin deficiency.

Lomas DA.

QJM. 1996 Nov;89(11):807-12. Review.

PMID:
8977959
4.

Alpha1-antitrypsin deficiency. 4: Molecular pathophysiology.

Lomas DA, Parfrey H.

Thorax. 2004 Jun;59(6):529-35. Review.

5.

Hypersensitive mousetraps, alpha1-antitrypsin deficiency and dementia.

Lomas DA, Lourbakos A, Cumming SA, Belorgey D.

Biochem Soc Trans. 2002 Apr;30(2):89-92. Review.

PMID:
12023831
6.

Osmolytes as modulators of conformational changes in serpins.

Chow MK, Devlin GL, Bottomley SP.

Biol Chem. 2001 Nov;382(11):1593-9.

PMID:
11767949
7.

Probing the unfolding pathway of alpha1-antitrypsin.

James EL, Whisstock JC, Gore MG, Bottomley SP.

J Biol Chem. 1999 Apr 2;274(14):9482-8.

8.

Genetics and respiratory disease. 2. Alpha 1-antitrypsin deficiency, cirrhosis and emphysema.

Mahadeva R, Lomas DA.

Thorax. 1998 Jun;53(6):501-5. Review. No abstract available.

9.

[From gene disease; alpha1-antitrypsine deficiency].

Hiemstra PS, Stolk J.

Ned Tijdschr Geneeskd. 2003 Apr 19;147(16):758-60. Review. Dutch.

PMID:
12731467
10.

Alpha-1-antitrypsin deficiency and liver disease.

Propst T, Propst A, Dietze O, Judmaier G, Braunsteiner H, Vogel W.

Dig Dis. 1994 May-Jun;12(3):139-49. Review.

PMID:
7988061
11.

Conformational changes in serpins and the mechanism of alpha 1-antitrypsin deficiency.

Carrell RW, Whisstock J, Lomas DA.

Am J Respir Crit Care Med. 1994 Dec;150(6 Pt 2):S171-5. Review. Erratum in: Am J Respir Crit Care Med 1995 Mar;151(3 Pt 1):926.

PMID:
7952655
12.
13.

Loop-sheet polymerization: the mechanism of alpha1-antitrypsin deficiency.

Lomas DA.

Respir Med. 2000 Aug;94 Suppl C:S3-6.

PMID:
10954247
14.

Polymerisation underlies alpha1-antitrypsin deficiency, dementia and other serpinopathies.

Lomas DA, Belorgey D, Mallya M, Onda M, Kinghorn KJ, Sharp LK, Phillips RL, Page R, Crowther DC, Miranda E.

Front Biosci. 2004 Sep 1;9:2873-91. Review.

PMID:
15353322
15.

Alpha1-antitrypsin polymerization and the serpinopathies: pathobiology and prospects for therapy.

Lomas DA, Mahadeva R.

J Clin Invest. 2002 Dec;110(11):1585-90. Review. No abstract available.

16.

Clinical features and molecular characteristics of alpha 1-antitrypsin deficiency.

Blank CA, Brantly M.

Ann Allergy. 1994 Feb;72(2):105-20; quiz 120-2. Review. Erratum in: Ann Allergy 1994 Apr;72(4):305.

PMID:
8109800
17.

Molecular pathogenesis of alpha-1-antitrypsin deficiency-associated liver disease: a meeting review.

Perlmutter DH, Brodsky JL, Balistreri WF, Trapnell BC.

Hepatology. 2007 May;45(5):1313-23. Review.

PMID:
17464974
18.

Alpha1-antitrypsin deficiency--a model for conformational diseases.

Carrell RW, Lomas DA.

N Engl J Med. 2002 Jan 3;346(1):45-53. Review. No abstract available.

PMID:
11778003
19.

[Therapeutic possibilities in the management of antitrypsin-deficient pulmonary emphysema].

Tarj√°n E, Pitlik E.

Orv Hetil. 1991 Sep 8;132(36):1975-8, 1981-2. Review. Hungarian.

PMID:
1923469
20.

Kinetic instability of the serpin Z alpha1-antitrypsin promotes aggregation.

Knaupp AS, Levina V, Robertson AL, Pearce MC, Bottomley SP.

J Mol Biol. 2010 Feb 19;396(2):375-83. doi: 10.1016/j.jmb.2009.11.048. Epub 2009 Nov 26.

PMID:
19944704

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