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Eur Heart J Cardiovasc Imaging. 2017 Mar 1;18(3):237-253. doi: 10.1093/ehjci/jew229.

Comprehensive multi-modality imaging approach in arrhythmogenic cardiomyopathy-an expert consensus document of the European Association of Cardiovascular Imaging.

Author information

1
Department of Cardiology, Center for Cardiological Innovation and Institute for Surgical Research, Oslo University Hospital, Oslo and University of Oslo, Oslo, Norway.
2
Cardiovascular Pathology, Department of Cardiac, Thoracic and Vascular Sciences, University of Padua Medical School, Padua, Italy.
3
Cardiology, Department of Cardiac, Thoracic and Vascular Sciences, University of Padua Medical School, Padua, Italy.
4
Department of Cardiology, Bristol Heart Institute, University Hospitals Bristol NHS Trust and University of Bristol and Bristol NIRH Cardiovascular Biomedical Research Unit, Bristol, UK.
5
Department of Cardiology, Multimodality Cardiac Imaging Center, Sports Cardiology and Cardiomyopathies Center, Hospital da Luz, Lisbon, Portugal.
6
Interventional Cardiology and Cardiac Imaging, University Heart Center Zurich, Zurich, Switzerland.
7
Department of Advanced Biomedical Sciences, Federico II University Hospital, Naples, Italy.
8
Aix-Marseille Université, Marseille and Cardiology Department, APHM, La Timone Hospital, Marseille, France.
9
Turku PET Centre, Turku University Hospital and University of Turku, Kiinamyllynkatu, Turku, Finland.
10
GIGA Cardiovascular Sciences, Department of Cardiology, University of Liège Hospital, Heart Valve Clinic, CHU Sart Tilman, Liège, Belgium and Gruppo Villa Maria Care and Research, Anthea Hospital, Bari, Italy.
11
Heart Hospital, Hamad Medical Corporation, Doha, Qatar and Imperial College, London, UK.
12
Cardiovascular Department at Fondazione Toscana G. Monasterio, CNR Institute of Clinical Physiology and Scuola Superiore San'Anna, Pisa, Italy.
13
University of Medicine and Pharmacy "Carol Davila"-Euroecolab, Institute of Cardiovascular Diseases "Prof. Dr. C. C. Iliescu," Bucharest, Romania.

Abstract

Arrhythmogenic cardiomyopathy (AC) is a progressive disease with high risk of life-threatening ventricular arrhythmias. A genetic mutation is found in up to 50-60% of probands, mostly affecting desmosomal genes. Diagnosis of AC is made by a combination of data from different modalities including imaging, electrocardiogram, Holter monitoring, family history, genetic testing, and tissue properties. Being a progressive cardiomyopathy, repeated cardiac imaging is needed in AC patients. Repeated imaging is important also for risk assessment of ventricular arrhythmias. This expert consensus document gives clinical recommendations for how to use multi-modality imaging in the different aspects of AC disease, including diagnosis, family screening, follow-up, risk assessment, and differential diagnosis.

KEYWORDS:

arrhythmogenic cardiomyopathy; cardiac magnetic resonance; echocardiography; late gadolinium enhancement; multi-modality imaging; multidetector computed tomography; speckle tracking echocardiography

PMID:
28069601
PMCID:
PMC5837226
DOI:
10.1093/ehjci/jew229
[Indexed for MEDLINE]
Free PMC Article

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