Send to

Choose Destination
Bol Asoc Med P R. 1993 Jan-Mar;85(1-3):24-6.

Basal cell nevus syndrome and medulloblastoma: a case report.

Author information

Department of Radiology, University Pediatric Hospital-Puerto Rico Medical Center, Rio Piedras.


The basal cell nevus syndrome (BCNS) is a rare autosomal dominant disorder characterized by multiple nevoid basal-cell carcinomas of the skin, recurrent odontogenic keratocysts, skeletal anomalies, developmental malformations, and the predisposition to other neoplastic processes. Among the well known relationships of the syndrome with cancer is that of medulloblastoma. The first known case of BCNS with medulloblastoma in Puerto Rico is presented.

[Indexed for MEDLINE]

Supplemental Content

Loading ...
Support Center