Quadricuspid aortic valve with a hidden left ostium: Case report and literature review

Filipe R Soares; Carlos Branco; Gonçalo F Coutinho; David Prieto; Manuel J Antunes

doi:10.1016/j.repc.2018.04.012

Quadricuspid aortic valve with a hidden left ostium: Case report and literature review

Rev Port Cardiol (Engl Ed). 2021 Jan;40(1):63.e1-63.e5. doi: 10.1016/j.repc.2018.04.012. Epub 2020 Dec 10.

[Article in English, Portuguese]

Authors

Filipe R Soares¹, Carlos Branco², Gonçalo F Coutinho², David Prieto², Manuel J Antunes²

Affiliations

¹ Center of Cardiothoracic Surgery, University Hospital and Medical School, Coimbra, Portugal. Electronic address: filipe_srs@hotmail.pt.
² Center of Cardiothoracic Surgery, University Hospital and Medical School, Coimbra, Portugal.

PMID: 33309128
DOI: 10.1016/j.repc.2018.04.012

Abstract

Quadricuspid aortic valve (QAV) is a rare congenital condition that frequently progresses to aortic regurgitation with clinical impact in adulthood. Surgical treatment is required in the fifth to sixth decade of life in about one fifth of patients. We describe the case of a 64-year-old woman with regular cardiological follow-up for severe aortic valve regurgitation who had suffered recent clinical and echocardiographic deterioration. Conventional open surgery was indicated. During the procedure, a QAV with leaflet retraction and central orifice was observed. The aortic valve was successfully replaced.

Keywords: Aortic valve replacement; Congenital heart disease; Doença cardíaca congénita; Quadricuspid aortic valve; Substituição valvular aórtica; Válvula aórtica quadricúspide.

Publication types

Case Reports
Review

MeSH terms

Adult
Aortic Valve / diagnostic imaging
Aortic Valve Insufficiency* / diagnostic imaging
Cardiology*
Echocardiography
Female
Humans
Middle Aged
Quadricuspid Aortic Valve*