Isolated hypoglossal nerve palsy from internal carotid artery dissection related to PKD-1 gene mutation

BMC Neurol. 2019 Nov 8;19(1):276. doi: 10.1186/s12883-019-1477-1.

Abstract

Background: Internal carotid artery dissection has been well recognized as a major cause of ischaemic stroke in young and middle-aged adults. However, internal carotid artery dissection induced hypoglossal nerve palsy has been seldom reported and may be difficult to diagnose in time for treatment; even angiography sometimes misses potential dissection, especially when obvious lumen geometry changing is absent.

Case presentation: We report a 42-year-old man who presented with isolated hypoglossal nerve palsy. High-resolution MRI showed the aetiological dissected internal carotid artery. In addition, a potential genetic structural defect of the arterial wall was suggested due to an exon region mutation in the polycystic-kidney-disease type 1 gene.

Conclusions: Hypoglossal nerve palsy is a rare manifestations of carotid dissection. High-resolution MRI may provide useful information about the vascular wall to assist in the diagnosis of dissection. High-throughput sequencing might be useful to identify potential cerebrovascular-related gene mutation, especially in young individuals with an undetermined aetiology.

Keywords: High-resolution MRI; Hypoglossal nerve palsy; Internal carotid artery dissection; PKD1 gene mutation; Target genes capture and high-throughput sequencing.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Carotid Artery, Internal, Dissection / complications*
  • Carotid Artery, Internal, Dissection / genetics*
  • Humans
  • Hypoglossal Nerve Diseases / etiology*
  • Magnetic Resonance Imaging / methods
  • Male
  • Mutation
  • TRPP Cation Channels / genetics*

Substances

  • TRPP Cation Channels
  • polycystic kidney disease 1 protein