Introduction: Arnold-Chiari malformation is a group of congenital malformations of the hindbrain. Common symptoms include cephalgia, vestibular, cerebral and cochlear disorders We present a case of pharmacoresistant tachyarrhythmia associated with Arnold-Chiari malformation.Case Description: A 49-year-old female patient had an Arnold-Chiari malformation (ACM), syringomyelia, a retrocerebellar cyst and a 6 year history of tachyarrhythmia. Heart rhythm normalized after Chiari decompression.Conclusion: ACM can lead to heart rhythm disorders.
Keywords: Arnold-Chiari malformation; cardiac arrhythmia; retrocerebellar cyst; syringomyelia.