Intravascular Papillary Endothelial Hyperplasia of the Maxillary Sinus in Patient with Tricuspid Atresia

Head Neck Pathol. 2020 Sep;14(3):803-807. doi: 10.1007/s12105-019-01070-w. Epub 2019 Aug 31.

Abstract

Intravascular papillary endothelial hyperplasia (IPEH) is a benign, highly vascularized, endothelial growth that can be mischaracterized as a malignancy. While hundreds of IPEH cases are reported, only four occurred in the maxillary sinus. We present the case of a 28-year-old male who underwent surgical resection of IPEH of the right maxillary sinus. An additional consideration was the patient's condition of univentricular tricuspid atresia which contributed to chronic hypoxemia and polycythemia. After complete resection from the maxillary sinus, post-operational workup determined the lesion to be IPEH. Given the potential for misdiagnosis of IPEH, careful histopathologic evaluation is required in order to avoid improper treatment.

Keywords: Hypercoagulable; Intravascular papillary endothelial hyperplasia; Masson’s tumor; Sphenopalatine artery; Univentricular tricuspid atresia.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Endothelium, Vascular / pathology*
  • Endothelium, Vascular / surgery
  • Humans
  • Hyperplasia / pathology
  • Hyperplasia / surgery
  • Male
  • Maxillary Sinus / pathology*
  • Maxillary Sinus / surgery
  • Tricuspid Atresia / complications*