L'hermitte-Duclos disease in an elderly patient: A case report and review of the literature

Asian J Neurosurg. 2014 Oct-Dec;9(4):246. doi: 10.4103/1793-5482.146666.

Abstract

L'hermitte-Duclos disease (LDD) is an extremely rare cerebellar lesion of uncertain etiology. Occasionally, the patients with LDD may even have sudden neurological deterioration due to acute heniation as seen in the present case report. It is also imperative to distinguish this disease from other malignant lesion of the cerebellum and cerebellar malformations with its varied natural course of history and hence better ability to prognosticate such patients. Herein, we reported a successfully treated case of LDD following a long history of vaguely defined neurological complaints in an elderly patient and reviewed the literature.

Keywords: Dysplastic cerebellar gangliocytoma; L’hermitte–Duclos disease; elderly; magnetic resonance imaging.

Publication types

  • Case Reports