Von Hippel-Lindau syndrome: demonstration of entire disease spectrum with (68)Ga-DOTANOC PET-CT

Korean J Radiol. 2014 Jan-Feb;15(1):169-72. doi: 10.3348/kjr.2014.15.1.169. Epub 2014 Jan 8.

Abstract

Von Hippel-Lindau (VHL) syndrome is a rare neoplastic disorder characterized by central nervous system (CNS) and visceral tumors. We here present (68)Ga-labelled [1, 4, 7, 10-tetraazacyclododecane-1, 4, 7, 10-tetraacetic acid]-1-Nal3-Octreotide positron emission tomography computed tomography findings in a 52 year old female with VHL syndrome, demonstrating both CNS and visceral tumors.

Keywords: 68Ga-DOTANOC; Hemangioblastoma; NET; PET-CT; RCC; Von Hippel-Lindau syndrome.

Publication types

  • Case Reports

MeSH terms

  • Brain Diseases / diagnostic imaging
  • Female
  • Humans
  • Kidney Diseases / diagnostic imaging
  • Liver Diseases / diagnostic imaging
  • Middle Aged
  • Multimodal Imaging / methods*
  • Organometallic Compounds
  • Pancreatic Diseases / diagnostic imaging
  • Positron-Emission Tomography / methods*
  • Tomography, X-Ray Computed / methods*
  • von Hippel-Lindau Disease / diagnostic imaging*

Substances

  • 68Ga-DOTANOC
  • Organometallic Compounds