Caesarean section in a parturient with Carpenter syndrome and corrected Tetralogy of Fallot

Int J Obstet Anesth. 2013 Jul;22(3):251-4. doi: 10.1016/j.ijoa.2013.04.009. Epub 2013 May 22.

Abstract

Carpenter syndrome is an extremely rare congenital disorder characterized by craniofacial malformations, syndactyly, cardiac defects and obesity. Even after surgical correction of cardiac abnormalities, intrapartum care of a parturient with this condition can be challenging because of progression of residual cardiac defects compounded by the haemodynamic changes of pregnancy. We describe the anaesthetic management for caesarean section of a parturient with Carpenter syndrome and corrected Tetralogy of Fallot. Additional complicating issues included worsening cardiac function, asthma, needle-phobia and osteoarthritis.

Publication types

  • Case Reports

MeSH terms

  • Acrocephalosyndactylia / complications*
  • Anesthesia, Inhalation
  • Anesthesia, Obstetrical
  • Apgar Score
  • Cesarean Section / methods*
  • Echocardiography
  • Female
  • Humans
  • Monitoring, Intraoperative
  • Obesity / complications
  • Pain, Postoperative / drug therapy
  • Patient Care Planning
  • Patient Care Team
  • Postoperative Care
  • Pregnancy
  • Pregnancy Outcome
  • Pulmonary Valve Insufficiency / complications
  • Pulmonary Valve Insufficiency / diagnostic imaging
  • Tetralogy of Fallot / physiopathology*
  • Tetralogy of Fallot / surgery
  • Young Adult

Supplementary concepts

  • Acrocephalopolysyndactyly Type II