Long-term survival in an infant with urethral atresia

J Urol. 1990 Feb;143(2):336-7. doi: 10.1016/s0022-5347(17)39952-4.

Abstract

Complete urethral atresia is an anomaly that previously was incompatible with life. We report on a surviving infant with this anomaly. As a fetus urinary decompression was accomplished with a vesicoamniotic shunt. Peritoneal dialysis was initiated shortly after birth and at 9 months supramembranous scrotal inlay urethroplasty was performed to provide for egress of urine from the bladder. A maternal renal allograft was performed when he was 12 months old. When the patient was 3 1/2 years old he had normal renal function and emptied the bladder to completion through the reconstructed urethra. Although mildly delayed, he continues to progress with all developmental milestones.

Publication types

  • Case Reports

MeSH terms

  • Cystostomy
  • Fetus / surgery
  • Follow-Up Studies
  • Humans
  • Infant, Newborn
  • Kidney Transplantation
  • Male
  • Peritoneal Dialysis
  • Time Factors
  • Urethra / abnormalities*
  • Urethra / surgery