Introduction: Terminal myelocystocele is a rare form of spinal dysraphism characterised by cystic dilatation of the central canal of a low-lying terminal cord. Typical presentation is a skin-covered dorsal mass; early surgical repair has been recommended.
Case report: We present the case of a 4-year-old girl with a terminal myelocystocele and syrinx, which were both observed to spontaneously regress on subsequent magnetic resonance imaging.
Conclusion: Terminal myelocystocele and its associated syrinx may resolve spontaneously. Early surgical repair may not always be necessary.