What is the role of cystic fibrosis transmembrane conductance regulator dysfunction in primary sclerosing cholangitis?

J Pediatr. 2007 Sep;151(3):230-2. doi: 10.1016/j.jpeds.2007.05.025.
No abstract available

Publication types

  • Comment
  • Editorial

MeSH terms

  • Child
  • Cholangitis, Sclerosing / etiology
  • Cholangitis, Sclerosing / genetics*
  • Cholangitis, Sclerosing / immunology
  • Cholangitis, Sclerosing / physiopathology
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics*
  • Genetic Predisposition to Disease
  • Humans
  • Inflammatory Bowel Diseases / complications
  • Inflammatory Bowel Diseases / genetics
  • Inflammatory Bowel Diseases / immunology
  • Sweat / chemistry

Substances

  • Cystic Fibrosis Transmembrane Conductance Regulator