Disturbances of valine metabolism in patients with peroxisomal biogenesis disorders

Adv Exp Med Biol. 2003:544:73-4. doi: 10.1007/978-1-4419-9072-3_11.
No abstract available

MeSH terms

  • Female
  • Humans
  • Infant
  • Male
  • Peroxisomal Disorders / cerebrospinal fluid
  • Peroxisomal Disorders / metabolism*
  • Valerates / cerebrospinal fluid
  • Valine / metabolism*

Substances

  • Valerates
  • 2-hydroxyisovaleric acid
  • Valine