Disturbances of valine metabolism in patients with peroxisomal biogenesis disorders
Adv Exp Med Biol
.
2003:544:73-4.
doi: 10.1007/978-1-4419-9072-3_11.
Authors
Francois J M Eyskens
1
,
Marc Lefevere
Affiliation
1
Provincial Centre for Metabolic Disorders (PCMA), Antwerp, Belgium. Francois.Eyskens@pcma.provant.be
PMID:
14713217
DOI:
10.1007/978-1-4419-9072-3_11
No abstract available
MeSH terms
Female
Humans
Infant
Male
Peroxisomal Disorders / cerebrospinal fluid
Peroxisomal Disorders / metabolism*
Valerates / cerebrospinal fluid
Valine / metabolism*
Substances
Valerates
2-hydroxyisovaleric acid
Valine