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Pediatr Nephrol. 1998 May;12(4):293-4.

Successful renal transplantation in Jeune syndrome type 2.

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Service de Néphrologie, Centre Hospitalier Général, Gap, France.


Jeune syndrome (asphyxiating thoracic dystrophy) is a rare inherited disease which is fatal in early childhood in 70% of cases. Severe renal involvement may occur and lead to chronic renal insufficiency in patients who survive respiratory failure. Therefore the opportunity to perform kidney transplantation is quite rare. We report a successful cadaver renal transplantation in a 10-year-old boy with Jeune syndrome type 2.

[Indexed for MEDLINE]

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