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Eur Child Adolesc Psychiatry. 1997;6 Suppl 1:71-4.

Rett syndrome: analysis of deaths in the British survey.

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1
Department of Psychological Medicine, Gartnavel Royal Hospital, Glasgow, Scotland.

Abstract

The mortality rate in Rett syndrome is 1.2% per annum, 48% of deaths occurring in debilitated people, 13% from natural causes, 13% with prior severe seizures and 26% sudden and unexpected. Respiratory dysrhythmias were usually present. Neuropathology confirmed reductions in cortical dendrites and in one case immaturity of cardiac conducting tissues.

PMID:
9452925
[Indexed for MEDLINE]

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