Send to

Choose Destination
See comment in PubMed Commons below
Brain Dev. 1997 Jul;19(5):353-8.

Perioral myoclonia with absences? A case report with EEG and voltage mapping analysis.

Author information

County Hospital, Neurological Department, Debrecen, Hungary.


The author presents clinical and electroencephalographic data of an epileptic girl, whose absences started at the age of 2. Based on seizure semiology, serial EEG and video-EEG recording, 7 years of follow-up and other clinical data, the patient was diagnosed as having the PMA ('perioral myoclonus with absences') syndrome. There were some disagreement between clinical and EEG data, however. Finally, she became completely seizure free on valproate+lamotrigine medication. Detailed EEG and voltage mapping analysis disclosed that spike movements of ictal and interictal generalized spike-wave discharges showed always the same, very consistent, peculiar topographic pattern. This pattern was fundamentally different from spike patterns associated with typical absence seizures (recorded in other patients). Analysis of clinical, EEG and voltage mapping results-suggest that actually this case might be rather classified as myoclonic epilepsy. The conjunction of this case to the PMA syndrome has been discussed.

[Indexed for MEDLINE]
PubMed Commons home

PubMed Commons

How to join PubMed Commons

    Supplemental Content

    Full text links

    Icon for Elsevier Science
    Loading ...
    Support Center