Polyostotic fibrous dysplasia. A long-term follow up of 8 patients

Int Orthop. 1996;20(4):227-32. doi: 10.1007/s002640050069.

Abstract

Eight patients who had polyostotic fibrous dysplasia were followed up for more than 10 years. One had the Albright syndrome. Two of 3 proximal femoral lesions which were treated before puberty by either curettage and bone grafting or by osteotomy, developed progressive deformity during the growth period. One of 2 proximal femoral lesions treated by curettage and bone grafting after the age of 18 also developed a deformity. Two tibial lesions operated on at the age of one and 30 years remained stable. The histological findings showed more active lesions in young patients compared with adults.

MeSH terms

  • Adolescent
  • Adult
  • Bone Transplantation
  • Child
  • Child, Preschool
  • Disease Progression
  • Female
  • Fibrous Dysplasia, Polyostotic / diagnostic imaging
  • Fibrous Dysplasia, Polyostotic / pathology
  • Fibrous Dysplasia, Polyostotic / surgery*
  • Follow-Up Studies
  • Hip Joint / diagnostic imaging
  • Humans
  • Infant
  • Male
  • Osteotomy
  • Radiography
  • Treatment Outcome