Rhabdomyosarcoma, a common soft tissue sarcoma in children, is rarely reported. The head and neck are the most common sites of occurrence. A case of embryonal rhabdomyosarcoma of the nasopharynx is presented. The patient, a five-year-old boy, presented with a two-monthly history of epistaxis. Ear-Nose-Throat examination revealed a mass at the hard palate. Head and neck MRI showed a nasopharyngeal mass with invasion to the skull base, and intracranial extention. Histological examination of the mass revealed embryonal rhabdomyosarcoma. A combination chemotherapy and intrathecal medication was administered. This was followed by radiotherapy to the tumor site with 2 cm free margins. A good tumor response was found.