Abstract
Linear IgA bullous dermatosis is an uncommon mucocutaneous autoimmune disorder that is distinct from dermatitis herpetiformis and bullous pemphigoid. Two patients who had significant conjunctival involvement but minimal skin disease are described. Irreversible conjunctival scarring indistinguishable from ocular pemphigoid developed in both patients.
MeSH terms
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Adult
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Aged
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Cicatrix / pathology
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Conjunctivitis / immunology*
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Conjunctivitis / pathology*
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Diagnosis, Differential
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Eyelid Diseases / immunology
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Eyelid Diseases / pathology
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Female
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Humans
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Immunoglobulin A*
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Male
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Mouth Diseases / immunology
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Mouth Diseases / pathology
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Pemphigoid, Bullous / pathology
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Skin Diseases, Vesiculobullous / immunology*
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Skin Diseases, Vesiculobullous / pathology*