Nutritional value of essential amino acids in the treatment of adults with phenylketonuria

J Inherit Metab Dis. 1995;18(2):127-30. doi: 10.1007/BF00711746.
No abstract available

MeSH terms

  • Adolescent
  • Adult
  • Amino Acids, Essential / blood
  • Amino Acids, Essential / metabolism
  • Amino Acids, Essential / therapeutic use*
  • Blood Proteins / analysis
  • Blood Urea Nitrogen
  • Creatinine / blood
  • Feces / chemistry
  • Humans
  • Nitrogen / analysis
  • Nitrogen / metabolism
  • Nitrogen / urine
  • Phenylketonurias / diet therapy*
  • Serum Albumin / analysis
  • Transaminases / blood
  • Transferrin / analysis

Substances

  • Amino Acids, Essential
  • Blood Proteins
  • Serum Albumin
  • Transferrin
  • Creatinine
  • Transaminases
  • Nitrogen