A rare childhood case of Behcet's disease and chronic thromboembolic pulmonary hypertension

J Card Surg. 2020 Jul;35(7):1669-1672. doi: 10.1111/jocs.14610. Epub 2020 May 17.

Abstract

Background: Pulmonary embolism and chronic thromboembolic pulmonary hypertension (CTEPH) are rare complications of Behcet's disease, especially in pediatric patients.

Aims/methods/results/conclusions: This case report highlights a presentation of CTEPH in an adolescent with Behcet's disease. A multidisciplinary approach was required for managing this patient's CTEPH, which successfully reversed the patient's pulmonary hypertension.

Keywords: aorta and great vessel; behcet's disease; pulmonary hypertension; pulmonary thromboendarterectomy.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Behcet Syndrome / complications*
  • Chronic Disease
  • Endarterectomy / methods*
  • Humans
  • Hypertension, Pulmonary / diagnostic imaging
  • Hypertension, Pulmonary / etiology*
  • Hypertension, Pulmonary / surgery*
  • Interdisciplinary Communication
  • Male
  • Pulmonary Embolism / diagnostic imaging
  • Pulmonary Embolism / etiology*
  • Pulmonary Embolism / surgery*
  • Rare Diseases
  • Treatment Outcome