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J Indian Soc Pedod Prev Dent. 2019 Jul-Sep;37(3):303-307. doi: 10.4103/JISPPD.JISPPD_256_18.

Cu-sil dentures: A novel approach of Papillon-Lefèvre syndrome management.

Author information

1
Department of Pedodontics and Preventive Dentistry, Christian Dental College, Ludhiana, Punjab, India.
2
Department of Dentistry, Rajiv Gandhi Institute of Medical Sciences, Adilabad, Telangana, India.

Abstract

Papillon-Lefèvre syndrome (PLS) is a rare genetic disorder characterized by palmoplantar keratosis and premature loss of primary and permanent dentition. Its onset can be as early as 1-4 years of age. The genetic disorder is mutation in the cathepsin C gene. Hereby, we discuss the fabrication of Cu-sil dentures for the prosthetic rehabilitation of a 14-year-old girl with PLS. The case report describes the procedure and associated relevant information regarding the management protocols.

KEYWORDS:

Cu-sil dentures; Papillon–Lefèvre syndrome; palmoplantar keratosis

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