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Indian J Pathol Microbiol. 2019 Jul-Sep;62(3):437-440. doi: 10.4103/IJPM.IJPM_517_18.

Kimura disease with nephrotic syndrome in a child- A rare association.

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Department of Pathology, Military Hospital Jodhpur, Jodhpur, Rajasthan, India.
Department of Radiodiagnosis and Imaging, Command Hospital, Pune, Maharashtra, India.


Lymphadenopathy along with various systemic manifestations is commonly encountered in pediatric patients, tuberculosis being the commonest etiology. Occasional patients may present a diagnostic conundrum. Here, the authors report an unusual manifestation of Kimura disease (KD) presenting as nephrotic syndrome associated with mesenteric lymphadenitis in an 11-year-old male child. KD is a chronic inflammatory disorder of unknown etiology. It typically affects young adult males in the age range of 27-40 years and usually presents as painless itchy nodular masses in the head and neck region. The involvement of mesenteric lymph nodes along with a very young age of presentation makes it a rare case, posing a diagnostic challenge for the unsuspecting physician.


Angiolymphoid hyperplasia with eosinophilia (ALHE); IgG4-related disease; Kimura disease; nephrotic syndrome

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